Mouse MitoCarta3.0

The Mouse MitoCarta3.0 inventory is a collection of 1140 nuclear and mtDNA genes encoding proteins with strong support of mitochondrial localization. This table provides a summary of evidence supporting mitochondrial localization, the protein distribution across 14 tissues, as well as annotation of biological pathways (based on manual literature review) and sub-compartment (based on annotator's "best guess" integrating sequence features, experimental data, literature, and pathway context; note all subunits of protein complexes are assigned the same compartment). The genes are ordered by strength of mitochondrial evidence. 

When using this data, please cite:

  • Rath, S., Sharma, R., Gupta, R., ..., Calvo, S.E., Mootha, V.K. MitoCarta3.0: An updated inventory of the mitochondrial proteome, now with sub-organelle localization and pathway annotations (2020). Nucleic Acids Research [Pubmed: 33174596] 

More complete information is available for download in Mouse.MitoCarta3.0.xls and fasta and bed files.

See also MitoPathways.

SymbolDescriptionSynonymsMaestro scoreEvidenceSub-compartmentMitoPathwaysTissues
Cyc1cytochrome ­c-12610002H19Rik, AA408921, Cyct1, Q9D0M3, gene:6644544literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
Metabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits		all 14
Pdha1pyruvate ­dehydrogenase ­E1 ­alpha ­1Pdha, Pdha-1, P35486, gene:1859742literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Atp5dATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­delta ­subunit0610008F14Rik, 1500000I11Rik, AA960090, AI876556, AU020773, Atp5f1d, C85518, Q9D3D9, gene:6604342literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Isca2iron-sulfur ­cluster ­assembly ­20710001C05Rik, 5730594E03Rik, Hbld, Hbld1, Q9DCB8, gene:7431642APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Pdhbpyruvate ­dehydrogenase ­(lipoamide) ­beta2610103L06Rik, AL024199, C81408, Q9D051, gene:6826342literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Uqcrc1ubiquinol-cytochrome ­c ­reductase ­core ­protein ­11110032G10Rik, Q9CZ13, gene:2227342literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
OXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		all 14
Coq9coenzyme ­Q92310005O14Rik, C78387, Q8K1Z0, gene:6791442APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Mrpl12mitochondrial ­ribosomal ­protein ­L120610034O11Rik, 1500031N16Rik, L12mt, MRP-, MRP-L12, Rpm, Rpml12, Q9DB15, gene:5628242literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > Transcription;
Mitochondrial central dogma > Translation > Mitochondrial ribosome		all 14
Mrps35mitochondrial ­ribosomal ­protein ­S35MDSO, MDSO23, MRP, MRP-, MRP-S28, MRPS28, Q8BJZ4, gene:23253642literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Cox5acytochrome ­c ­oxidase ­subunit ­5AAA959768, CcO, CcOX, P12787, gene:1285842literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Uqcrfs1ubiquinol-cytochrome ­c ­reductase, ­Rieske ­iron-sulfur ­polypeptide ­14430402G14Rik, AI875505, Q9CR68, gene:6669441literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Coq7demethyl-Q ­7clk-, clk-1, P97478, gene:1285041literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Sdhasuccinate ­dehydrogenase ­complex, ­subunit ­A, ­flavoprotein ­(Fp)1500032O14Rik, 2310034D06Rik, 4921513A11, C81073, F, FP, SDH, SDH2, SDHF, Q8K2B3, gene:6694541literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
OXPHOS > OXPHOS subunits		all 14
Sdhbsuccinate ­dehydrogenase ­complex, ­subunit ­B, ­iron ­sulfur ­(Ip)0710008N11Rik, Q9CQA3, gene:6768041literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Atp5a1ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­alpha ­subunit ­1AI035633, AL022851, AL023067, At, Atp5f1a, Atpm, D18Ertd206, D18Ertd206e, Mom, Mom2, Q03265, gene:1194641literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Sdhaf4succinate ­dehydrogenase ­complex ­assembly ­factor ­41110058L19Rik, 1700001E18Rik, C6orf57, Q8BTE0, gene:6800241targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors		adipose, testis
Pmpcbpeptidase ­(mitochondrial ­processing) ­beta3110004O18Rik, MPP, MPP11, MPPB, MPPP52, Q9CXT8, gene:7307841literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		all 14
Sdhdsuccinate ­dehydrogenase ­complex, ­subunit ­D, ­integral ­membrane ­protein3110001M13Rik, AVLL5809, C78570, PRO19626, Q9CXV1, gene:6692541literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Heme-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Uqcrc2ubiquinol ­cytochrome ­c ­reductase ­core ­protein ­21500004O06Rik, Q9DB77, gene:6700340literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
OXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		all 14
Coq5coenzyme ­Q5 ­methyltransferase1810014G04Rik, D5Ertd33, D5Ertd33e, Q9CXI0, gene:5206440APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Ogdhoxoglutarate ­(alpha-ketoglutarate) ­dehydrogenase ­(lipoamide)2210403E04Rik, 2210412K19Rik, AA409584, d1401, mKIAA4192, Q60597, gene:1829340literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Uqcrqubiquinol-cytochrome ­c ­reductase, ­complex ­III ­subunit ­VII1100001F06Rik, 1500040F11Rik, 5830407L17Rik, 9.5kDa, AA959903, QP-, QP-C, Qp, Qpc, Uqcrb, c1502, Q9CQ69, gene:2227240literature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		all 14
Mdh2malate ­dehydrogenase ­2, ­NAD ­(mitochondrial)MDH, Mdh-2, Mo, Mor, Mor-1, Mor1, P08249, gene:1744839literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Carbohydrate metabolism > TCA cycle		all 14
Dbtdihydrolipoamide ­branched ­chain ­transacylase ­E2BCKAD-E2, D3Wsu60, D3Wsu60e, P53395, gene:1317138literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex		all 14
Dlatdihydrolipoamide ­S-acetyltransferase ­(E2 ­component ­of ­pyruvate ­dehydrogenase ­complex)6332404G05Rik, DLTA, PDC-E, PDC-E2, Q8BMF4, gene:23533938literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Lrpprcleucine-rich ­PPR-motif ­containing3110001K13Rik, C76645, Gp130, Lrp, Lrp130, Lsfc, Q6PB66, gene:7241638literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation		all 14
Mrpl53mitochondrial ­ribosomal ­protein ­L531110007K17Rik, Q9D1H8, gene:6849938literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Dlstdihydrolipoamide ­S-succinyltransferase ­(E2 ­component ­of ­2-oxo-glutarate ­complex)1600017E01Rik, 4632413C10Rik, 4930529O08Rik, DLTS, Q9D2G2, gene:7892038literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Amino acid metabolism > Lysine metabolism		all 14
Pdhxpyruvate ­dehydrogenase ­complex, ­component ­XAI481367, E3bp, Pdx, Pdx1, Q8BKZ9, gene:2740238literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Gfm1G ­elongation ­factor, ­mitochondrial ­1AW545374, D3Wsu133, D3Wsu133e, Gfm, Q8K0D5, gene:2803037literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Grpel1GrpE-like ­1, ­mitochondrialAA408748, mt-GrpE, mt-GrpE#1, mt-Grpel1, Q99LP6, gene:1771337literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Import motor;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis		all 14
Mpc2mitochondrial ­pyruvate ­carrier ­20610006C01Rik, 2010002I07Rik, 2610205H19Rik, AA108335, Brp, Brp44, ESTM4, ESTM43, Q9D023, gene:7045637literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport		all 14
Uqcr10ubiquinol-cytochrome ­c ­reductase, ­complex ­III ­subunit ­X1110020P15Rik, AA960494, Ucrc, Q8R1I1, gene:6615237literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		all 14
Coq3coenzyme ­Q3 ­methyltransferase4732433J24, C77934, Q8BMS4, gene:23002737APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atp5eATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­epsilon ­subunit2410043G19Rik, ATPE, AV000645, Atp5f1e, P56382, gene:6712637literature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Slc25a3solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­35730556H19Rik, PTP, Ph, Phc, Q8VEM8, gene:1867437literature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Copper metabolism;
Signaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > SLC25A family		all 14
Mrpl34mitochondrial ­ribosomal ­protein ­L340610007O17Rik, D8Bwg1484e, Q99N91, gene:9406537literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps15mitochondrial ­ribosomal ­protein ­S151500003E24Rik, 2410002B11Rik, Mprs15, Q9DC71, gene:6640737literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Sdhcsuccinate ­dehydrogenase ­complex, ­subunit ­C, ­integral ­membrane ­protein0610010E03Rik, AI316496, AU019277, Q9CZB0, gene:6605236literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Heme-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Atp5bATP ­synthase, ­H+ ­transporting ­mitochondrial ­F1 ­complex, ­beta ­subunitAtp5f1b, P56480, gene:1194736literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Mrps23mitochondrial ­ribosomal ­protein ­S23D11Bwg1153e, MRP-S23, Rpm, Rpms23, S23mt, Q8VE22, gene:6465636literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Etfaelectron ­transferring ­flavoprotein, ­alpha ­polypeptide2010200I21Rik, D9Ertd394, D9Ertd394e, Q99LC5, gene:11084236literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Electron carriers > Q-linked reactions, other		all 14
Fh1fumarate ­hydratase ­1Fh, Fh-1, fuma, P97807, gene:1419436literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Mrps27mitochondrial ­ribosomal ­protein ­S272610028H14Rik, Q8BK72, gene:21850636literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Isca1iron-sulfur ­cluster ­assembly ­11810010A06Rik, Hbld, Hbld2, Q9D924, gene:6904636APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Idh3aisocitrate ­dehydrogenase ­3 ­(NAD+) ­alpha1110003P10Rik, 1500012E04Rik, AA407078, AI316514, Q9D6R2, gene:6783436APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Ndufs1NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S15830412M15Rik, 9930026A05Rik, Q91VD9, gene:22719735literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
AuhAU ­RNA ­binding ­protein/enoyl-coenzyme ­A ­hydrataseC77140, W91705, Q9JLZ3, gene:1199235literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Amino acid metabolism > BCAA metabolism		all 14
Afg3l2AFG3-like ­AAA ­ATPase ­22310036I02Rik, AW260507, Emv6, Emv66, par, Q8JZQ2, gene:6959735literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Pmpcapeptidase ­(mitochondrial ­processing) ­alpha1200002L24Rik, 4933435E07Rik, Alp, Alpha-MPP, IN, P-55, Q9DC61, gene:6686535literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		all 14
Cox11cytochrome ­c ­oxidase ­assembly ­protein ­11, ­copper ­chaperone2010004I09Rik, Q6P8I6, gene:6980235literature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, spinalcord, skeletalmuscle, largeintestine, placenta
Sucla2succinate-Coenzyme ­A ­ligase, ­ADP-forming, ­beta ­subunit4930547K18Rik, A-SCS, SCS-betaA, Q9Z2I9, gene:2091635literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing		all 14
Lars2leucyl-tRNA ­synthetase, ­mitochondrialAI035546, Kiaa0028, LEURS, Q8VDC0, gene:10243635literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesall 14
Atp5oATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­O ­subunitATPO, Atp5po, D12Wsu28, D12Wsu28e, OSCP, Q9DB20, gene:2808034literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Mrpl46mitochondrial ­ribosomal ­protein ­L463110052F15Rik, C15orf4, C80107, LIEC, LIECG2, P2E, P2ECSL, Q9EQI8, gene:6730834literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
Cox15cytochrome ­c ­oxidase ­assembly ­protein ­152900026G05Rik, Q8BJ03, gene:22613934literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Heme synthesis and processing;
OXPHOS > OXPHOS assembly factors		cerebrum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Higd2aHIG1 ­domain ­family, ­member ­2A2010110M21Rik, AA690237, Q9CQJ1, gene:6704434APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly		all 14
Uqcrhubiquinol-cytochrome ­c ­reductase ­hinge ­protein2210416J04Rik, 2310021J10Rik, 2610041P16Rik, P99028, gene:6657634literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		all 14
Etfdhelectron ­transferring ­flavoprotein, ­dehydrogenase0610010I20Rik, AV001013, Q921G7, gene:6684134literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Electron carriers > Q-linked reactions, other		all 14
Timm10translocase ­of ­inner ­mitochondrial ­membrane ­10Tim1, Tim13, Timm1, Timm13a, P62073, gene:3005934literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Echs1enoyl ­Coenzyme ­A ­hydratase, ­short ­chain, ­1, ­mitochondrialC80529, SCEH, Q8BH95, gene:9374734literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism		all 14
Hadhahydroxyacyl-CoA ­dehydrogenase ­trifunctional ­multienzyme ­complex ­subunit ­alphaC77020, Mt, Mtpa, TP-alpha, Q8BMS1, gene:9721233literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Amino acid metabolism > BCAA metabolism		all 14
Bckdhabranched ­chain ­ketoacid ­dehydrogenase ­E1, ­alpha ­polypeptideQ3U3J1, gene:1203933literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex		cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Suclg1succinate-CoA ­ligase, ­GDP-forming, ­alpha ­subunit1500000I01Rik, Suc, Sucla1, Q9WUM5, gene:5645133targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing		all 14
Cscitrate ­synthase2610511A05Rik, 9030605P22Rik, Ahl4, BB234005, C, Cis, ah, Q9CZU6, gene:1297433literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Cox6a1cytochrome ­c ­oxidase ­subunit ­6A1VIaL, P43024, gene:1286133literature, targetP signal+, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Acadsacyl-Coenzyme ­A ­dehydrogenase, ­short ­chainAI196007, Bcd-1, Bcd1, Hdlq, Hdlq8, SC, SCAD, Q07417, gene:1140933literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufv2NADH:ubiquinone ­oxidoreductase ­core ­subunit ­V22900010C23Rik, Q9D6J6, gene:7290032literature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Iars2isoleucine-tRNA ­synthetase ­2, ­mitochondrial2010002H18Rik, C79125, Q8BIJ6, gene:38131432APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesall 14
Coq6coenzyme ­Q6 ­monooxygenase5930427M12Rik, AW742344, Q8R1S0, gene:21770732literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atp5kATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1F0 ­complex, ­subunit ­E2610008D24Rik, Atp5i, Atp5me, Lfm, Lfm1, Q06185, gene:1195832literature, APEX_IMS, yeast mito homolog++, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits;
Mitochondrial dynamics and surveillance > Cristae formation		all 14
Idh3bisocitrate ­dehydrogenase ­3 ­(NAD+) ­betaC78231, Q91VA7, gene:17071832literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Ndufa6NADH:ubiquinone ­oxidoreductase ­subunit ­A614kD, 14kDa, 2700038D15Rik, B230217P19Rik, Q9CQZ5, gene:6713032literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Letm1leucine ­zipper-EF-hand ­containing ­transmembrane ­protein ­1Q9Z2I0, gene:5638432literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MIMSignaling > Calcium homeostasis > Calcium cycleall 14
Atpaf2ATP ­synthase ­mitochondrial ­F1 ­complex ­assembly ­factor ­2ATP, ATP12, ATP12p, Q91YY4, gene:24678232literature, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMatrixOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Rtn4ip1reticulon ­4 ­interacting ­protein ­1D10Ertd690, D10Ertd690e, N, NIMP, Q924D0, gene:17072832literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++Matrixnoneall 14
Mrpl43mitochondrial ­ribosomal ­protein ­L434930442D21Rik, bMRP, bMRP36a, Q5RL20, gene:9406731literature, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Abhd11abhydrolase ­domain ­containing ­111110054D16Rik, A630008N09Rik, Wbscr, Wbscr21, Q8K4F5, gene:6875831literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Timm50translocase ­of ­inner ­mitochondrial ­membrane ­502810403L02Rik, AU015082, TIM5, TIM50L, Q9D880, gene:6652531literature, APEX_IMS, targetP signal+, yeast mito homolog++, mito protein domain, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Mrpl28mitochondrial ­ribosomal ­protein ­L281110015G04Rik, L28mt, MAA, MAAT1, MRP-L28, p1, p15, Q9D1B9, gene:6861131literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sdhaf2succinate ­dehydrogenase ­complex ­assembly ­factor ­20610038F07Rik, AA407634, AW049997, Q8C6I2, gene:6607231GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufb8NADH:ubiquinone ­oxidoreductase ­subunit ­B82900010I05Rik, AI987932, CI-ASHI, Q9D6J5, gene:6726431literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Dlddihydrolipoamide ­dehydrogenaseO08749, gene:1338231literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system		all 14
Ndufs2NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S2CI-49kD, Q91WD5, gene:22664631literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Ndufv1NADH:ubiquinone ­oxidoreductase ­core ­subunit ­V1CI-51kD, Q91YT0, gene:1799531literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Opa1OPA1, ­mitochondrial ­dynamin ­like ­GTPase1200011N24Rik, AI225888, AI847218, l, lilr3, mKIAA0567, P58281, gene:7414331literature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Cristae formation		all 14
Immtinner ­membrane ­protein, ­mitochondrial1700082C19Rik, D830041H16Rik, HM, HMP, Mico, Micos60, P8, P87, P87/8, P87/89, P89, mit, Q8CAQ8, gene:7661431literature, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Apoolapolipoprotein ­O-like6720473G16Rik, 9430083G14Rik, E130106L15Rik, Mico, Micos27, Q78IK4, gene:6811731literature, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Lonp1lon ­peptidase ­1, ­mitochondrial1200017E13Rik, LON, Pr, Prss15, Q8CGK3, gene:7414231literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Letmd1LETM1 ­domain ­containing ­11110019O13Rik, AI593524, BB130465, BB235638, HCCR, HCCR-, HCCR-2, HCCR1, MCC-32, Mccr, Q924L1, gene:6861431GFP, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MembraneSmall molecule transportcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Pdk4pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­4AV005916, O70571, gene:2727331literature, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
Mtif2mitochondrial ­translational ­initiation ­factor ­22310038D14Rik, 2410112O06Rik, IF-2(Mt), IF-2m, IF-2mt, IF2(mt), Q91YJ5, gene:7678431literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Translation factorsall 14
Ndufs8NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S8BC021616, CI-23kD, TYKY, Q8K3J1, gene:22588730literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Ndufs7NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S71010001M04Rik, CI-20kD, Q9DC70, gene:7540630literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Mrrfmitochondrial ­ribosome ­recycling ­factor2400002D02Rik, MRFF, MTRRF, RRF, Q9D6S7, gene:6787130literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Mrpl2mitochondrial ­ribosomal ­protein ­L2CGI-2, CGI-22, L2mt, MRP-, MRP-L14, MRP-L2, Rpm, Rpml14, Q9D773, gene:2739830literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomespinalcord, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
Gfm2G ­elongation ­factor, ­mitochondrial ­26530419G12Rik, A930009M04Rik, EF-G2mt, EFG2, MST02, MST027, RRF2mt, Q8R2Q4, gene:32080630literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Timm9translocase ­of ­inner ­mitochondrial ­membrane ­92810011L15Rik, Tim1, Tim10a, Timm1, Timm10, Q9WV98, gene:3005630literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		all 14
Pitrm1pitrilysin ­metallepetidase ­12310012C15Rik, AA410010, MP-, MP-1, MP1, Ntu, Ntup1, P, PreP, mKIAA1104, Q8K411, gene:6961730literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Acadmacyl-Coenzyme ­A ­dehydrogenase, ­medium ­chainAU018656, MCA, MCAD, P45952, gene:1136430literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Supv3l1suppressor ­of ­var1, ­3-like ­1 ­(S. ­cerevisiae)6330443E10Rik, Q80YD1, gene:33835930literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl1mitochondrial ­ribosomal ­protein ­L12410002L03Rik, 5830418D04Rik, AI462572, L1mt, Q99N96, gene:9406130literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aco2aconitase ­2, ­mitochondrialAc, Aco, Aco-2, Aco3, D10Wsu183, D10Wsu183e, Q99KI0, gene:1142930literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Coq10acoenzyme ­Q10AGm1, E9Q3H6, gene:21058230targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach
Samm50SAMM50 ­sorting ­and ­assembly ­machinery ­component1110030L07Rik, Q8BGH2, gene:6865330literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, induction, coexpression++, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		all 14
Mrps2mitochondrial ­ribosomal ­protein ­S21500019M10Rik, Q924T2, gene:11845130literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Surf1surfeit ­gene ­10610010F23Rik, Surf, Surf-1, P09925, gene:2093030literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl44mitochondrial ­ribosomal ­protein ­L441810030E18Rik, 5730593H20Rik, AI463302, Q9CY73, gene:6916330literature, APEX_matrix, targetP signal+, yeast mito homolog++, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
PhbprohibitinBap32, P67778, gene:1867330literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Guf1GUF1 ­homolog, ­GTPase4631409J12, AA407526, EF-4, Q8C3X4, gene:23127930APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MatrixMitochondrial central dogma > Translationcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Polrmtpolymerase ­(RNA) ­mitochondrial ­(DNA ­directed)1110018N15Rik, 4932416K13, Q8BKF1, gene:21615129literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression++, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription		cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Ghitmgrowth ­hormone ­inducible ­transmembrane ­protein1010001P14Rik, C77840, MICS1, PTD01, PTD010, Tmbim, Tmbim5, Q91VC9, gene:6609229literature, APEX_IMS, targetP signal+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MSMIMMitochondrial dynamics and surveillance > Apoptosisall 14
Timm13translocase ­of ­inner ­mitochondrial ­membrane ­13D10Ertd378, D10Ertd378e, Tim, Tim9, Timm, Timm9, P62075, gene:3005529literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		all 14
Cpt2carnitine ­palmitoyltransferase ­2AI323697, CP, CPTII, P52825, gene:1289629literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle		all 14
Mrpl10mitochondrial ­ribosomal ­protein ­L100610040E02Rik, C78440, L10mt, MRP, MRP-L8, Rp, Rpml8, Q3TBW2, gene:10773229literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mto1mitochondrial ­tRNA ­translation ­optimization ­12310039H01Rik, 5730419A02Rik, Q923Z3, gene:6829129literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		cerebellum, spinalcord, stomach, placenta
Prdx3peroxiredoxin ­3A, AW822249, Aop1, D0Toh, D0Tohi1, Ef2, Ef2l, Mer, Mer5, Prx3, SP, SP22, TDXM, P20108, gene:1175729literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismall 14
Cox7a2cytochrome ­c ­oxidase ­subunit ­7A2COX, COX7AL, Cox7, Cox7a3, CoxVIIa-L, P48771, gene:1286629literature, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Atp5jATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­FAtp5pf, CF6, P97450, gene:1195729literature, APEX_IMS, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Iba57IBA57 ­homolog, ­iron-sulfur ­cluster ­assembly4930543L23Rik, A230051G13Rik, C1orf69, Q8CAK1, gene:21679229APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl40mitochondrial ­ribosomal ­protein ­L40Nl, Nlvcf, Q9Z2Q5, gene:1810029literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hibch3-hydroxyisobutyryl-Coenzyme ­A ­hydrolase2610509I15Rik, HIBYL-C, HIBYL-COA-H, Q8QZS1, gene:22709529literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Ndufs6NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S6BC059730, IP, IP13, P52503, gene:40778529literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Oxct13-oxoacid ­CoA ­transferase ­12610008O03Rik, Oxct, Oxct2a, Sco, Scot-s, Q9D0K2, gene:6704129literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Gatd3aglutamine ­amidotransferase ­like ­class ­1 ­domain ­containing ­3AC21orf33, D10Jhu81e, ES1, Q9D172, gene:2829529APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++Matrixnoneall 14
Ndufb9NADH:ubiquinone ­oxidoreductase ­subunit ­B91190008J14Rik, CI-B22, Q9CQJ8, gene:6621829literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Cox6ccytochrome ­c ­oxidase ­subunit ­6CQ9CPQ1, gene:1286429literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Sod2superoxide ­dismutase ­2, ­mitochondrialMn, MnSOD, Sod, Sod-2, P09671, gene:2065629literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismall 14
Ndufb5NADH:ubiquinone ­oxidoreductase ­subunit ­B50610007D05Rik, AU015782, CI-SGDH, SGDH, Q9CQH3, gene:6604629literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Hadhhydroxyacyl-Coenzyme ­A ­dehydrogenaseAA409008, AU019341, AW742602, HCDH, Hadhsc, Sch, Schad, Q61425, gene:1510728literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > Lysine metabolism		all 14
FechferrochelataseAI894116, Fc, Fcl, fch, Q544X6, gene:1415128literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Liaslipoic ­acid ­synthetase2900022L22Rik, 4933425M12Rik, 7a5e, 7a5ex, C77512, LS, lip-syn, mL, Q99M04, gene:7946428literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion;
Metabolism > Metals and cofactors > Fe-S-containing proteins		brainstem, skeletalmuscle, adipose, largeintestine, placenta
Nfs1nitrogen ­fixation ­gene ­1 ­(S. ­cerevisiae)AA987187, m-Nf, m-Nfs1, m-Nfsl, Q9Z1J3, gene:1804128literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Fdx1ferredoxin ­1ADRE, P46656, gene:1414828literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
Metabolism > Vitamin metabolism > Vitamin D metabolism		all 14
Mrm1mitochondrial ­rRNA ­methyltransferase ­1A530065E19Rik, Q99J25, gene:21703828APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications		spinalcord, placenta, testis
Mrps18amitochondrial ­ribosomal ­protein ­S18A1110004O20Rik, C79712, Q99N85, gene:6856528literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Malsu1mitochondrial ­assembly ­of ­ribosomal ­large ­subunit ­12410003K15Rik, Matsu1, Q9CWV0, gene:7559328literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblycerebrum, cerebellum, liver, smallintestine, largeintestine, placenta
Gatbglutamyl-tRNA(Gln) ­amidotransferase, ­subunit ­B9430026F02Rik, Pet11, Pet112, Pet112l, Q99JT1, gene:22948728literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, skeletalmuscle, adipose, stomach, testis
Yars2tyrosyl-tRNA ­synthetase ­2 ­(mitochondrial)2210023C10Rik, tyrRS, Q8BYL4, gene:7012028literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesbrainstem, spinalcord, kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
FxnfrataxinFA, FARR, Fr, Frda, X25, O35943, gene:1429728literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesisall 14
Idh3gisocitrate ­dehydrogenase ­3 ­(NAD+), ­gammaP70404, gene:1592928literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Mrps28mitochondrial ­ribosomal ­protein ­S281500012D08Rik, AW061224, Q9CY16, gene:6623028literature, targetP signal+, mito protein domain+, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Timm44translocase ­of ­inner ­mitochondrial ­membrane ­440710005E20Rik, D8Ertd118, D8Ertd118e, Mimt4, Mimt44, Tim4, Tim44, O35857, gene:2185628literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorall 14
Clpxcaseinolytic ­mitochondrial ­matrix ­peptidase ­chaperone ­subunitAU014732, E330029I21, Q9JHS4, gene:27016628literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Mrpl3mitochondrial ­ribosomal ­protein ­L32010320L16Rik, 5930422H18Rik, AA407889, L3mt, dc, dcr, Q99N95, gene:9406228literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Mecrmitochondrial ­trans-2-enoyl-CoA ­reductaseAI195831, NRBF-1, Nrb, Nrbf1, Q9DCS3, gene:2692228literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisall 14
Slc25a20solute ­carrier ­family ­25 ­(mitochondrial ­carnitine/acylcarnitine ­translocase), ­member ­201110007P09Rik, C78826, CAC, Cact, mCA, mCAC, Q9Z2Z6, gene:5727928literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle;
Small molecule transport > SLC25A family		all 14
Slc25a4solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­adenine ­nucleotide ­translocator), ­member ­4AU019225, An, Ant1, mANC1, P48962, gene:1173928literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport > SLC25A family		all 14
Mtch2mitochondrial ­carrier ­22310034D24Rik, 4930539J07Rik, HSPC0, HSPC032, Q791V5, gene:5642828literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MS++MOMSmall molecule transport > SLC25A family;
Mitochondrial dynamics and surveillance > Fusion		all 14
Pdk2pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­2Q9JK42, gene:1860428literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Cox6b1cytochrome ­c ­oxidase, ­subunit ­6B12010000G05Rik, COX VIb-1, Cox6b, P56391, gene:11032328literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Vdac1voltage-dependent ­anion ­channel ­1AL033343, Vda, Vdac5, mVDAC1, mVDAC5, Q60932, gene:2233328literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MOMSignaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Mitochondrial dynamics and surveillance > Organelle contact sites;
Small molecule transport		all 14
Mrpl4mitochondrial ­ribosomal ­protein ­L41110017G11Rik, Q9DCU6, gene:6616328literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Mrps14mitochondrial ­ribosomal ­protein ­S141810032L21Rik, AL022847, Rpm, Rpms14, Q9CR88, gene:6465928literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hspa9heat ­shock ­protein ­974kDa, C, Csa, GRP, Grp75, Hs, Hsc7, Hsc74, Hsp, Hsp74, Hsp74a, Hspa9a, Mortalin, Mot-2, Mot2, Mthsp70, PBP, Pbp74, mo, mot-, mthsp, P38647, gene:1552628APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesisall 14
Ndufa9NADH:ubiquinone ­oxidoreductase ­subunit ­A91010001N11Rik, Q9DC69, gene:6610827literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ndufa2NADH:ubiquinone ­oxidoreductase ­subunit ­A2AV000592, B8, C1-B8, CI-B8, Q9CQ75, gene:1799127literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Iscuiron-sulfur ­cluster ­assembly ­enzyme2310020H20Rik, AA407971, ISCU2, Ni, Nifu, Nifun, Q9D7P6, gene:6638327literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
C1qbpcomplement ­component ­1, ­q ­subcomponent ­binding ­proteinAA407365, AA986492, D11Wsu182, D11Wsu182e, HAB, HABP1, P3, P32, gC1qBP, Q8R5L1, gene:1226127literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixSignaling > Immune responseall 14
Afg1lAFG1 ­like ­ATPaseCG8520, Lac, Lace1, Q3V384, gene:21595127APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, spinalcord, heart, adipose, smallintestine, largeintestine, stomach, placenta
Micos10mitochondrial ­contact ­site ­and ­cristae ­organizing ­system ­subunit ­102310028O11Rik, Mi, Minos1, Q7TNS2, gene:43377127literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Cox17cytochrome ­c ­oxidase ­assembly ­protein ­17, ­copper ­chaperoneAI037035, COX1, P56394, gene:1285627literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++IMSOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors		heart, adipose, smallintestine, placenta, testis
Uqcc1ubiquinol-cytochrome ­c ­reductase ­complex ­assembly ­factor ­12310079L17Rik, 2410003P15Rik, 3110038N19Rik, Bfz, Bfzb, Bfzp, Cbp, Cbp3, Uqcc, Q9CWU6, gene:5604627literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl33mitochondrial ­ribosomal ­protein ­L330610009M10Rik, L33mt, MRP-L33, Q9CQP0, gene:6684527literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, stomach, placenta, testis
Acadlacyl-Coenzyme ­A ­dehydrogenase, ­long-chainAA960361, AU018452, C79855, LC, LCAD, P51174, gene:1136327literature, targetP signal+, mito protein domain+, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufs4NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S46720411N02Rik, C1-18k, Q9CXZ1, gene:1799327literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Phb2prohibitin ­2AU044498, BAP, Bap37, Bcap, Bcap37, R, REA, O35129, gene:1203427literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Bckdhbbranched ­chain ­ketoacid ­dehydrogenase ­E1, ­beta ­polypeptideBCKDE1B, BCKDH E1-beta, Q6P3A8, gene:1204027literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrps12mitochondrial ­ribosomal ­protein ­S12AI327385, Rpm, Rpms12, rp, rps12, O35680, gene:2403027literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mcatmalonyl ­CoA:ACP ­acyltransferase ­(mitochondrial)AI225907, BC025519, Q8R3F5, gene:22372227literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisspinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl24mitochondrial ­ribosomal ­protein ­L242010005E08Rik, 2810470K06Rik, 6720473G22Rik, AA407670, Q9CQ06, gene:6770727literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl13mitochondrial ­ribosomal ­protein ­L131110002D09Rik, Q9D1P0, gene:6853727literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Pccapropionyl-Coenzyme ­A ­carboxylase, ­alpha ­polypeptideC79630, Q91ZA3, gene:11082127literature, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Vitamin metabolism > Biotin utilizing proteins		all 14
Mrpl17mitochondrial ­ribosomal ­protein ­L17MRP-, MRP-L26, Rpm, Rpml26, Q9D8P4, gene:2739727literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Aifm1apoptosis-inducing ­factor, ­mitochondrion-associated ­1A, AIF, AIFsh2, Hq, Pdcd, Pdcd8, Q9Z0X1, gene:2692627literature, APEX_IMS, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > MIA40;
OXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors;
Mitochondrial dynamics and surveillance > Apoptosis		all 14
Cox4i1cytochrome ­c ­oxidase ­subunit ­4I1AL024441, CO, COX, COX IV-1, COXIV, Cox4, Cox4a, IV-1, P19783, gene:1285727literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Ndufaf4NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­41110007M04Rik, 3000003G13Rik, AW214064, Q9D1H6, gene:6849327APEX_matrix, GFP, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Slc25a35solute ­carrier ­family ­25, ­member ­351810012H11Rik, Q5SWT3, gene:7199827APEX_matrix, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMSmall molecule transport > SLC25A familycerebrum, cerebellum, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dap3death ­associated ­protein ­34921514D13Rik, DAP, DAP-3, MRP-S29, S29mt, Q9ER88, gene:6511127literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Atp5c1ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­gamma ­polypeptide ­11700094F02Rik, Atp5f1c, Q91VR2, gene:1194927literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Slc25a11solute ­carrier ­family ­25 ­(mitochondrial ­carrier ­oxoglutarate ­carrier), ­member ­112310022P18Rik, 2ox, 2oxoc, Q9CR62, gene:6786327literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport > SLC25A family		all 14
Timm8btranslocase ­of ­inner ­mitochondrial ­membrane ­8BTim8, Tim8b, P62077, gene:3005727literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sdhaf1succinate ­dehydrogenase ­complex ­assembly ­factor ­10610010E21Rik, AI430885, AW490662, Lyr, Lyrm8, Q3U276, gene:6833226literature, targetP signal+, yeast mito homolog, mito protein domain+, induction, coexpression+, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl15mitochondrial ­ribosomal ­protein ­L15HSPC1, HSPC145, MRP, MRP-L7, Rp, Rpml7, Q9CPR5, gene:2739526literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Alas1aminolevulinic ­acid ­synthase ­1A, ALAS, ALAS-N, Al, Alas-1, Alas-h, Q8VC19, gene:1165526literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Heme synthesis and processingliver, heart, adipose, largeintestine, placenta
Cmc2COX ­assembly ­mitochondrial ­protein ­21110046L09Rik, 2310061C15Rik, DC13, Q8K199, gene:6653126APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+IMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, spinalcord, liver, heart, adipose, largeintestine, stomach, placenta, testis
Pptc7PTC7 ­protein ­phosphatase ­homolog9130017A15Rik, AA672638, AI848390, TA-PP2C, Q6NVE9, gene:32071726APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixSignalingcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, largeintestine, placenta, testis
Bckdkbranched ­chain ­ketoacid ­dehydrogenase ­kinaseAI327402, BCKD-ki, O55028, gene:1204126literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex		cerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Txn2thioredoxin ­22510006J11Rik, AI788873, Trx, Trx2, P97493, gene:5655126literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MatrixMetabolism > Vitamin metabolism > Vitamin C metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism		all 14
Suclg2succinate-Coenzyme ­A ­ligase, ­GDP-forming, ­beta ­subunitAF171077, AW556404, D6Wsu120, D6Wsu120e, G-SCS, GTPSCS, SCS-betaG, Q9Z2I8, gene:2091726literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing		all 14
Mfn1mitofusin ­12310002F04Rik, 6330416C07Rik, D3Ertd265, D3Ertd265e, HR, HR2, mKIAA4032, Q811U4, gene:6741426literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Organelle contact sites		cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Ndufb6NADH:ubiquinone ­oxidoreductase ­subunit ­B6CI-B17, Gm137, Q3UIU2, gene:23007526literature, APEX_IMS, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ndufa5NADH:ubiquinone ­oxidoreductase ­subunit ­A52900002J19Rik, CI-13kD-B, Q9CPP6, gene:6820226literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Mtx2metaxin ­21500012G02Rik, O88441, gene:5337526literature, mito protein domain+, induction, coexpression++, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		all 14
Ogdhloxoglutarate ­dehydrogenase-likeE9Q7L0, gene:23901726APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Acat1acetyl-Coenzyme ­A ­acetyltransferase ­16330585C21Rik, Ac, Acat, Q8QZT1, gene:11044626literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism		all 14
Echdc3enoyl ­Coenzyme ­A ­hydratase ­domain ­containing ­32310005D12Rik, AI662097, Q9D7J9, gene:6785626targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++Matrixnonespinalcord, kidney, liver, heart, adipose, largeintestine, stomach, placenta, testis
Mrpl21mitochondrial ­ribosomal ­protein ­L21BC028768, L21mt, MRP-L21, Q9D1N9, gene:35324226literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Nfu1NFU1 ­iron-sulfur ­cluster ­scaffold0610006G17Rik, CGI-3, CGI-33, Hi, Hirip5, Q9QZ23, gene:5674826APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Mrpl55mitochondrial ­ribosomal ­protein ­L552810038N09Rik, L55mt, MRP-L55, Q9CZ83, gene:6721226literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Taco1translational ­activator ­of ­mitochondrially ­encoded ­cytochrome ­c ­oxidase ­I2310066I18Rik, Ccdc44, Q8K0Z7, gene:7020726literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Sdhaf3succinate ­dehydrogenase ­complex ­assembly ­factor ­30610005M07Rik, 4933430A16Rik, Ac, Acn9, Q8BQU3, gene:7123826targetP signal, yeast mito homolog++, mito protein domain+, coexpression+, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors		adipose, testis
Mrpl11mitochondrial ­ribosomal ­protein ­L112410001P07Rik, L11mt, Q9CQF0, gene:6641926literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Echdc2enoyl ­Coenzyme ­A ­hydratase ­domain ­containing ­21300017C12Rik, 2610009M20Rik, D4Ertd765e, Q3TLP5, gene:5243026targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++Matrixnoneall 14
Cox5bcytochrome ­c ­oxidase ­subunit ­5BQ9D881, gene:1285926literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Acadsbacyl-Coenzyme ­A ­dehydrogenase, ­short/branched ­chain1300003O09Rik, 2-MEBCAD, BB066609, SBCAD, Q9DBL1, gene:6688525literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism		all 14
Eral1Era ­(G-protein)-like ­1 ­(E. ­coli)2610524P08Rik, 9130407C09Rik, AU019798, Era, M-ERA, MER, MERA, MERA-S, MERA-W, Q9CZU4, gene:5783725APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		none
Abcb10ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­10ABC-m, Abc-me, Abcb12, Q9JI39, gene:5619925literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MIMMetabolism > Metals and cofactors > Heme synthesis and processing;
Small molecule transport > ABC transporters		cerebellum, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bcs1lBCS1-like ­(yeast)9130022O19Rik, Q9CZP5, gene:6682125literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS+MIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hsdl2hydroxysteroid ­dehydrogenase ­like ­22610207I16Rik, Q2TPA8, gene:7247925APEX_matrix, GFP, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++Matrixnoneall 14
Cmc1COX ­assembly ­mitochondrial ­protein ­12010110K16Rik, 2010312P05Rik, AI596001, Q9CPZ8, gene:6789925APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+IMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Me3malic ­enzyme ­3, ­NADP(+)-dependent, ­mitochondrial1700020C08Rik, B230207H15Rik, Q8BMF3, gene:10926425literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hspd1heat ­shock ­protein ­1 ­(chaperonin)60kDa, CPN60, HSP-60, HSP-65, Hsp, Hsp60, P63038, gene:1551025literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Lyrm7LYR ­motif ­containing ­71700024C24Rik, 9330147L21Rik, Q9DA03, gene:7553025literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MatrixOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
TsfmTs ­translation ­elongation ­factor, ­mitochondrial2310050B20Rik, 9430024O13Rik, EF-T, EF-TS, EF-Tsm, EF-Tsmt, Q9CZR8, gene:6639925literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorscerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ethe1ethylmalonic ­encephalopathy ­10610025L15Rik, Hsco, Q9DCM0, gene:6607125literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixMetabolism > Sulfur metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Aldh4a1aldehyde ­dehydrogenase ­4 ­family, ­member ­A1A930035F14Rik, ALD, Ahd, Ahd-, Ahd-1, Ahd1, Aldh4, Aldh5a1, E330022C09, P5cd, P5cdh, P5cdhl, P5cdhs, Ssd, Ssdh1, Q8CHT0, gene:21264725literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolism;
Metabolism > Amino acid metabolism > Glyoxylate metabolism		all 14
Vdac2voltage-dependent ­anion ­channel ­2Vda, Vdac6, mVDAC2, mVDAC6, Q60930, gene:2233425literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MOMSmall molecule transportall 14
Coa6cytochrome ­c ­oxidase ­assembly ­factor ­61810063B05Rik, AI447995, Q8BGD8, gene:6789225APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Coq4coenzyme ­Q4D2Ertd97, D2Ertd97e, Q8BGB8, gene:22768325literature, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Ivdisovaleryl ­coenzyme ­A ­dehydrogenase1300016K07Rik, 6720455E18Rik, AI463340, Q9JHI5, gene:5635725literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Acadvlacyl-Coenzyme ­A ­dehydrogenase, ­very ­long ­chainVL, vlcad, P50544, gene:1137025literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Slc25a1solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­citrate ­transporter), ­member ­11300019P08Rik, 2610100G11Rik, AI194714, Ctp, Dgs, Dgsj, Slc2, Slc20a3, Q8JZU2, gene:1335825literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > TCA-associated;
Metabolism > Lipid metabolism;
Small molecule transport > SLC25A family		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a42solute ­carrier ­family ­25, ­member ­422900084M01Rik, Q8R0Y8, gene:7309525literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme A metabolism;
Small molecule transport > SLC25A family		all 14
Abcb8ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­84833412N02Rik, AA409895, MITOSUR, Q9CXJ4, gene:7461025literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMSmall molecule transport > ABC transportersall 14
Ndufs5NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S5AI256693, Q99LY9, gene:59513625literature, APEX_IMS, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Mrps7mitchondrial ­ribosomal ­protein ­S7MRP, MRP-S7, Rp, Rpms7, S7mt, Q80X85, gene:5052925literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome		all 14
Mccc1methylcrotonoyl-Coenzyme ­A ­carboxylase ­1 ­(alpha)1810045E08Rik, 2310058B18Rik, MCC, MCCalpha, Mcca, R75106, Q99MR8, gene:7203925literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Vitamin metabolism > Biotin utilizing proteins		all 14
Mrpl49mitochondrial ­ribosomal ­protein ­L49L49mt, MRP-L49, No, Nof1, Q9CQ40, gene:1812025literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufaf5NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­52310003L22Rik, A2APY7, gene:6948725literature, APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebellum, brainstem, skeletalmuscle, largeintestine, stomach, placenta
Mrps9mitochondrial ­ribosomal ­protein ­S92310002A08Rik, AW322516, Mrp-S9, S9mt, mg637, Q9D7N3, gene:6952725literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome		all 14
Ndufb10NADH:ubiquinone ­oxidoreductase ­subunit ­B100610011B04Rik, 22kD, 22kDa, PDSW, Q9DCS9, gene:6834224literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Dnaja3DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­A31200003J13Rik, 1810053A11Rik, C81173, Tid-, Tid-1, Tid1l, Q99M87, gene:8394524literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Mrpl19mitochondrial ­ribosomal ­protein ­L199030416F12Rik, 9130412E02Rik, D6Ertd157, D6Ertd157e, MRP-, MRP-L15, RL, RLX1, Rpm, Rpml15, Q9D338, gene:5628424literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mipepmitochondrial ­intermediate ­peptidase5730405E07Rik, MIP, A6H611, gene:7047824literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm40ltranslocase ­of ­outer ­mitochondrial ­membrane ­40-likeQ9CZR3, gene:64137624targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MSMOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, testis
Adhfe1alcohol ­dehydrogenase, ­iron ­containing, ­16330565B14Rik, AI043035, Adh8, HOT, Q8R0N6, gene:7618724targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolismkidney, liver, heart, adipose, stomach, placenta
Coq8acoenzyme ­Q8A4632432J16Rik, AI462003, Adck, Adck3, Cabc, Cabc1, mKIAA0451, Q60936, gene:6742624literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Bdh13-hydroxybutyrate ­dehydrogenase, ­type ­12310032J20Rik, AI327223, Bdh, Q80XN0, gene:7191124literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Ketone metabolismall 14
Tomm7translocase ­of ­outer ­mitochondrial ­membrane ­71110020J08Rik, AW047273, TOM, Tom7, Q9D173, gene:6616924literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
Hccsholocytochrome ­c ­synthetaseP53702, gene:1515924literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSIMSMetabolism > Metals and cofactors > Heme synthesis and processing;
OXPHOS > OXPHOS subunits;
OXPHOS > Cytochrome C		cerebrum, spinalcord, heart, adipose, smallintestine, largeintestine, placenta, testis
Mrpl16mitochondrial ­ribosomal ­protein ­L162310039D06Rik, Q99N93, gene:9406324literature, targetP signal, yeast mito homolog++, mito protein domain, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Prodhproline ­dehydrogenaseP, Pr, Pro-1, Pro1, Ym24d07, Q9WU79, gene:1912524literature, targetP signal, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Proline metabolism;
Metabolism > Electron carriers > Q-linked reactions, other		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl30mitochondrial ­ribosomal ­protein ­L302310001L22Rik, L30mt, MRP-, MRP-L28, MRP-L30, Rpm, Rpml28, Q9D7N6, gene:10773424literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufa10NADH:ubiquinone ­oxidoreductase ­subunit ­A102900053E13Rik, Q99LC3, gene:6727324literature, targetP signal+, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Mars2methionine-tRNA ­synthetase ­2 ­(mitochondrial)C730026E21Rik, MetRS, Q499X9, gene:21267924literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Clppcaseinolytic ­mitochondrial ­matrix ­peptidase ­proteolytic ­subunitAU019820, D17Wsu160, D17Wsu160e, O88696, gene:5389524literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Ak3adenylate ­kinase ­3AA407498, AI506714, AK-, AK-3, Ak3l, Ak3l1, Akl3l, Q9WTP7, gene:5624824literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
Spg7SPG7, ­paraplegin ­matrix ­AAA ­peptidase ­subunitAI452278, AU015315, Cm, Cmar, PGN, pa, Q3ULF4, gene:23484723literature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MSMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sco1SCO1 ­cytochrome ­c ­oxidase ­assembly ­protein2610001C07Rik, D11Bwg1310e, Q5SUC9, gene:5289223literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atpif1ATPase ­inhibitory ­factor ­1ATP5IF1, Atpi, IF(1), If, If1, O35143, gene:1198323literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MatrixOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Chchd3coiled-coil-helix-coiled-coil-helix ­domain ­containing ­30610041L09Rik, 1700039J09Rik, AW558177, Mico, Micos19, Q9CRB9, gene:6607523literature, APEX_IMS, APEX_matrix, GFP, Rickettsial homolog, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		all 14
Acad12acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­129330129D05Rik, D3Z7X0, gene:33835023targetP signal+, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hibadh3-hydroxyisobutyrate ­dehydrogenase6430402H10Rik, AI265272, Q99L13, gene:5887523literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Gatcglutamyl-tRNA(Gln) ­amidotransferase, ­subunit ­C2010003O18Rik, Q8CBY0, gene:38428123literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, spinalcord, kidney, largeintestine, testis
Cox8bcytochrome ­c ­oxidase ­subunit ­8BCOX8, Cox8h, CoxVIII-H, P48772, gene:1286923literature, targetP signal, mito protein domain+, induction, coexpression+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		skeletalmuscle
ClpbClpB ­caseinolytic ­peptidase ­BAL118244, Skd, Skd3, Q60649, gene:2048023APEX_IMS, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++IMSProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tmem126atransmembrane ­protein ­126A1810020E01Rik, Q9D8Y1, gene:6627123literature, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Aldh6a1aldehyde ­dehydrogenase ­family ­6, ­subfamily ­A11110038I05Rik, Mmsd, Mmsdh, Q9EQ20, gene:10477623literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > BCAA metabolismall 14
Mrps18cmitochondrial ­ribosomal ­protein ­S18C1110037D14Rik, Q8R2L5, gene:6873523literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pdk1pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­1B830012B01, D530020C15Rik, Q8BFP9, gene:22802623literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Ppifpeptidylprolyl ­isomerase ­F ­(cyclophilin ­F)AW457192, CyP-, CyP-D, CyP-F, Cyp, CypD, PPIase, Q99KR7, gene:10567523literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS++MatrixSignaling > Calcium homeostasis > Mitochondrial permeability transition poreall 14
Lyrm4LYR ­motif ­containing ­4BC034664, Gm903, Q8K215, gene:38084023literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesisall 14
Ech1enoyl ­coenzyme ­A ­hydratase ­1, ­peroxisomalAA617331, O35459, gene:5179823APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolismall 14
Acaa2acetyl-Coenzyme ­A ­acyltransferase ­2 ­(mitochondrial ­3-oxoacyl-Coenzyme ­A ­thiolase)0610011L04Rik, AI255831, AI265397, D18Ertd240, D18Ertd240e, Q8BWT1, gene:5253823literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > Lysine metabolism		all 14
Ndufa7NADH:ubiquinone ­oxidoreductase ­subunit ­A714.5kD, 14.5kDa, 2400007M02Rik, CI-B14.5a, Q9Z1P6, gene:6641623literature, APEX_matrix, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Mrpl35mitochondrial ­ribosomal ­protein ­L351110066C01Rik, Q9CQL6, gene:6622323literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomelargeintestine, testis
Pccbpropionyl ­Coenzyme ­A ­carboxylase, ­beta ­polypeptide1300012P06Rik, AI314687, R74805, Q99MN9, gene:6690423literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation		all 14
Coq2coenzyme ­Q2 ­4-hydroxybenzoate ­polyprenyltransferase2310002F18Rik, PHB:PPT, Q66JT7, gene:7188323literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismnone
Mrpl20mitochondrial ­ribosomal ­protein ­L202610008D01Rik, 4930425I20Rik, Q9CQL4, gene:6644823literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Timm17atranslocase ­of ­inner ­mitochondrial ­membrane ­17a17kD, Tim17a, mTim1, mTim17a, Q9Z0V8, gene:2185423literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Timm22translocase ­of ­inner ­mitochondrial ­membrane ­22Tim22, Q9CQ85, gene:5632223literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathwayall 14
Mrpl54mitochondrial ­ribosomal ­protein ­L540610008M19Rik, D10Sut1, D10Sut1e, Q9CPW3, gene:6604723literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm22translocase ­of ­outer ­mitochondrial ­membrane ­222310047D01, Tom2, Tom22, Q9CPQ3, gene:22369622literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMall 14
Cratcarnitine ­acetyltransferaseAW107812, CA, CARAT, P47934, gene:1290822literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Mrps5mitochondrial ­ribosomal ­protein ­S51620401I16Rik, AI850294, Q99N87, gene:7772122literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dhtkd1dehydrogenase ­E1 ­and ­transketolase ­domain ­containing ­1C330018I04Rik, A2ATU0, gene:20969222APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MSMatrixMetabolism > Amino acid metabolism > Lysine metabolismcerebrum, kidney, liver, adipose, placenta, testis
Tmem70transmembrane ­protein ­701110020A09Rik, 2210416J16Rik, Q921N7, gene:7039722literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Alkbh7alkB ­homolog ­72310045B01Rik, 2510008E23Rik, Abh, Abh7, Spa, Spata11, Q9D6Z0, gene:6640022APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MSMatrixnonecerebellum, brainstem, largeintestine, testis
Mrps22mitochondrial ­ribosomal ­protein ­S223100002P07Rik, Rpm, Rpms22, Q9CXW2, gene:6465522literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Uqcrbubiquinol-cytochrome ­c ­reductase ­binding ­protein2210415M14Rik, QP-, QP-C, QPC, UQBC, UQBP, UQPC, Q9CQB4, gene:6753022literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		all 14
Cox7ccytochrome ­c ­oxidase ­subunit ­7CCOX, COXVIIc, Cox7c1, P17665, gene:1286722literature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Ndufaf1NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­12410001M24Rik, CGI-6, CGI-65, CIA, CIA30, Q9CWX2, gene:6970222literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebellum, brainstem, spinalcord, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acad8acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­82310016C19Rik, AI786953, Q9D7B6, gene:6694822literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Wars2tryptophanyl ­tRNA ­synthetase ­2 ­(mitochondrial)5730427B17Rik, 9430020O07Rik, AI413375, T, TrpRS, Q9CYK1, gene:7056022literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, kidney, skeletalmuscle, adipose, largeintestine, placenta, testis
Mrps34mitochondrial ­ribosomal ­protein ­S340610007F04Rik, 5330430D13Rik, AV001970, Tce2, Q9JIK9, gene:7904422literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufv3NADH:ubiquinone ­oxidoreductase ­core ­subunit ­V31500032D16Rik, Q8BK30, gene:7833022literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ndufb2NADH:ubiquinone ­oxidoreductase ­subunit ­B21810011O01Rik, 8kD, 8kDa, AGGG, AI325567, CI-AGGG, Q9CPU2, gene:6819822literature, targetP signal, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Slc25a12solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­Aralar), ­member ­122610002D09Rik, AI839531, B230107K20Rik, BB129864, Q8BH59, gene:7883022literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Amino acid metabolism > Glutamate metabolism;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family		all 14
Slc25a5solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­adenine ­nucleotide ­translocator), ­member ­5An, Ant2, P51881, gene:1174022literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport > SLC25A family		all 14
Mrps21mitochondrial ­ribosomal ­protein ­S211810031B19Rik, S21mt, P58059, gene:6629222literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Msrb2methionine ­sulfoxide ­reductase ­B22310050L06Rik, Mrsb, Ms, Msrb, Pilb, Q78J03, gene:7646722APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Sulfur metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Glrx5glutaredoxin ­5Q80Y14, gene:7304622literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Chchd10coiled-coil-helix-coiled-coil-helix ­domain ­containing ­101620401E04Rik, AI267078, Ndg, Ndg2, Q7TNL9, gene:10317222literature, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression++IMSnonenone
Coq10bcoenzyme ­Q10B1500041J02Rik, 1700030I21Rik, 9530077A17Rik, AV002237, AW742641, Q3THF9, gene:6787622GFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
Slc25a30solute ­carrier ­family ­25, ­member ­304933433D23Rik, AV025504, AV221431, AW319655, KMCP, KMCP1, Q9CR58, gene:6755421literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Sulfur metabolism;
Small molecule transport > SLC25A family		cerebrum, cerebellum, liver, placenta, testis
Slc25a13solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­adenine ­nucleotide ­translocator), ­member ­13AI785475, Ct, Ctrn, ci, Q9QXX4, gene:5079921literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Amino acid metabolism > Urea cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family		all 14
Slc25a10solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­dicarboxylate ­transporter), ­member ­10Di, Dic, Q9QZD8, gene:2737621literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Small molecule transport > SLC25A family		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox7a1cytochrome ­c ­oxidase ­subunit ­7A1COX, COX7, COX7A, COX7AH, COX7AM, P56392, gene:1286521literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a19solute ­carrier ­family ­25 ­(mitochondrial ­thiamine ­pyrophosphate ­carrier), ­member ­192900089E13Rik, DN, DNC, MUP, MUP1, TP, TPC, Q9DAM5, gene:6728321literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin B1 metabolism;
Small molecule transport > SLC25A family		cerebellum, spinalcord, adipose, testis
Smdt1single-pass ­membrane ­protein ­with ­aspartate ­rich ­tail ­11500032L24Rik, Emr, Emre, Q9DB10, gene:6902921literature, targetP signal, mito protein domain+, induction, coexpression+, MS/MSMIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > Calcium uniporter		cerebrum, cerebellum, brainstem, spinalcord, kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl22mitochondrial ­ribosomal ­protein ­L22E030011D16Rik, HSPC1, HSPC158, L22mt, MRP-, MRP-L22, MRP-L25, Rpm, Rpml25, Q8BU88, gene:21676721literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrps10mitochondrial ­ribosomal ­protein ­S101110038B19Rik, AW743084, Rpm, Rpms10, G5E8U5, gene:6465721literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Afg3l1AFG3-like ­AAA ­ATPase ­11700047G05Rik, 3110061K15Rik, Q920A7, gene:11489621literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Fdxrferredoxin ­reductaseAR, Q61578, gene:1414921literature, APEX_matrix, targetP signal, yeast mito homolog++, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Vitamin metabolism > Vitamin D metabolism		spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
SlirpSRA ­stem-loop ­interacting ­RNA ­binding ­protein1810035L17Rik, Q9D8T7, gene:38077321literature, APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation		all 14
Poldip2polymerase ­(DNA-directed), ­delta ­interacting ­protein ­21300003F06Rik, Pdip38, Q91VA6, gene:6781121literature, APEX_matrix, targetP signal+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoidall 14
Acsf3acyl-CoA ­synthetase ­family ­member ­3BB101783, Q3URE1, gene:25763321APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisall 14
Oxa1loxidase ­assembly ­1-like1810020M02Rik, AI894287, Q8BGA9, gene:6908921literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMIMProtein import, sorting and homeostasis > Protein import and sorting > OXA;
Mitochondrial central dogma > Translation		cerebrum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, placenta, testis
Idh2isocitrate ­dehydrogenase ­2 ­(NADP+), ­mitochondrialE430004F23, ID, IDPm, Idh-, Idh-2, P54071, gene:26995121literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Atp5lATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­G4933437C06Rik, Atp5mg, Q9CPQ8, gene:2742521literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits;
Mitochondrial dynamics and surveillance > Cristae formation		all 14
Bola1bolA-like ­1 ­(E. ­coli)1810037G04Rik, Q9D8S9, gene:6916821GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Fahd2afumarylacetoacetate ­hydrolase ­domain ­containing ­2A1500003K14Rik, B430104H02Rik, Cgi-105, Fahd2, Q3TC72, gene:6812621APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS++Matrixnoneall 14
Etfrf1electron ­transfer ­flavoprotein ­regulatory ­factor ­14930469P12Rik, AL022899, Gh, Ghiso, Lyr, Lyrm5, Q91V16, gene:6763621mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Electron carriers > Q-linked reactions, othercerebrum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
Ndufc2NADH:ubiquinone ­oxidoreductase ­subunit ­C21810004I06Rik, 2010300P09Rik, G1, R75094, Q9CQ54, gene:6819721literature, APEX_IMS, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ndufa8NADH:ubiquinone ­oxidoreductase ­subunit ­A80610033L03Rik, AW261656, CI-19kD, CI-PGIV, Q9DCJ5, gene:6837521literature, APEX_IMS, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Mthfd1lmethylenetetrahydrofolate ­dehydrogenase ­(NADP+ ­dependent) ­1-like2410004L15Rik, AI647056, Fthfsdc, Fthfsdc1, Q3V3R1, gene:27068521literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pdk3pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­32610001M10Rik, AI035637, Q922H2, gene:23690021literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox14cytochrome ­c ­oxidase ­assembly ­protein ­142310016M24Rik, AA959804, Q8BH51, gene:6637921literature, GFP, mito protein domain+, induction, coexpression++, MS/MS+MIMMitochondrial central dogma > Translation > Translation factors;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, smallintestine, testis
Gcdhglutaryl-Coenzyme ­A ­dehydrogenase9030411L18, AI266902, D17825, GCD, Q60759, gene:27007621literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolismall 14
Mrpl51mitochondrial ­ribosomal ­protein ­L512610511M02Rik, CDA0, CDA09, HSPC2, HSPC241, Mrp, Mrp64, Q9CPY1, gene:6649321literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Haghhydroxyacyl ­glutathione ­hydrolaseBC019817, Gl, Glo, Glo-2, Glo2, Rs, Rsp29, Q99KB8, gene:1465121literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtx1metaxin ­1Gca, Gcap6, Mtx, F7C846, gene:1782721literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		all 14
Fars2phenylalanine-tRNA ­synthetase ­2 ­(mitochondrial)Fa, Fars1, pheRS, Q99M01, gene:6995521literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesadipose, largeintestine, stomach, placenta, testis
Cbr4carbonyl ­reductase ­4A730083J17Rik, BC009118, Q91VT4, gene:23430921literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisall 14
Mrpl32mitochondrial ­ribosomal ­protein ­L320610033O15Rik, Q9DCI9, gene:7539821literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
2310061I04RikRIKEN ­cDNA ­2310061I04 ­geneB8JJ69, gene:6966221targetP signal, induction, coexpression++, MS/MS+Matrixnoneall 14
Fdx2ferredoxin ­2B230118G17Rik, Fdx1, Fdx1l, Q9CPW2, gene:6816521APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
mt-Co2cytochrome ­c ­oxidase ­subunit ­IIP00405, gene:1770921literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
mt-Atp6ATP ­synthase ­F0 ­subunit ­6P00848, gene:1770521literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Trap1TNF ­receptor-associated ­protein ­12410002K23Rik, HSP, HSP75, Q9CQN1, gene:6801521APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression++, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Gpd2glycerol ­phosphate ­dehydrogenase ­2, ­mitochondrialAA408484, AI448216, AU021455, AW494132, GPDH, Gdm1, Gpd-m, Gpdh-m, TISP38, Q64521, gene:1457121literature, APEX_IMS, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Glycerol phosphate shuttle;
Metabolism > Electron carriers > Q-linked reactions, other		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Abcb7ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­7AA517758, AU019072, Abc, Abc7, Q61102, gene:1130621literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Small molecule transport > ABC transporters		all 14
Hsd17b10hydroxysteroid ­(17-beta) ­dehydrogenase ­1017bHSD10, Ad, Ads9, ER, ERAB, Hadh, Hadh2, Q99N15, gene:1510821literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Amino acid metabolism > BCAA metabolism		all 14
Glud1glutamate ­dehydrogenase ­1AI118167, Gdh-X, Glu, Glud, Gludl, P26443, gene:1466121literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolism;
Metabolism > Amino acid metabolism > GABA metabolism		all 14
Aldh2aldehyde ­dehydrogenase ­2, ­mitochondrialAHD-M1, ALDH-E2, ALDHI, Ahd, Ahd-, Ahd-5, Ahd5, P47738, gene:1166921literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
TufmTu ­translation ­elongation ­factor, ­mitochondrial2300002G02Rik, C76308, C76389, EF-TuMT, EFTU, Q8BFR5, gene:23387020literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Stoml2stomatin ­(Epb7.2)-like ­20610038F01Rik, MSLP2, SL, SLP-2, Q99JB2, gene:6659220literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasisall 14
Dhrs4dehydrogenase/reductase ­(SDR ­family) ­member ­4AI043103, AI790593, CR, D14Ucl, D14Ucla2, NDRD, PHCR, PSCD, R, RRD, mouNRDR, Q99LB2, gene:2820020targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin A metabolismall 14
Aldh9a1aldehyde ­dehydrogenase ­9, ­subfamily ­A1AA139417, Abaldh, ESTM4, ESTM40, TMABA-, TMABA-DH, Tmabadh, Q9JLJ2, gene:5675220APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism		brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nars2asparaginyl-tRNA ­synthetase ­2 ­(mitochondrial)(putative)AI875199, Q8BGV0, gene:24414120GFP, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesspinalcord, adipose, largeintestine, stomach, placenta
Vwa8von ­Willebrand ­factor ­A ­domain ­containing ­81300010F03Rik, 4932416F07Rik, AI957255, Kiaa0564, mKIAA0564, Q8CC88, gene:21918920APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression+, MS/MS++Matrixnoneall 14
Mrps26mitochondrial ­ribosomal ­protein ­S26AI648866, GI00, GI008, MRP-, MRP-S13, MRP-S26, Rpm, Rpms13, Q80ZS3, gene:9904520literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Adck5aarF ­domain ­containing ­kinase ­5A230108P17, Q80V03, gene:26882220targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSunknownnonecerebrum, largeintestine, testis
Cars2cysteinyl-tRNA ­synthetase ­2 ­(mitochondrial)(putative)2310051N18Rik, 2410044A07Rik, D530030H10Rik, cysRS, Q8BYM8, gene:7194120APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox10heme ­A:farnesyltransferase ­cytochrome ­c ­oxidase ­assembly ­factor ­102410004F01Rik, AU042636, Q8CFY5, gene:7038320literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++MIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Heme synthesis and processing;
OXPHOS > OXPHOS assembly factors		none
Ndufb11NADH:ubiquinone ­oxidoreductase ­subunit ­B11CI-ESSS, D5Bwg0566e, D5Bwg0577e, NP15.6, Np, Np15, p15.6, O09111, gene:10413020literature, APEX_IMS, APEX_matrix, targetP signal+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Pdha2pyruvate ­dehydrogenase ­E1 ­alpha ­2Pd, Pdhal, P35487, gene:1859820literature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ssbp1single-stranded ­DNA ­binding ­protein ­12810480P10Rik, G630031O20Rik, MtSSB, mtDB, mtDBP, Q9CYR0, gene:38176020literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid		all 14
HscbHscB ­iron-sulfur ­cluster ­co-chaperoneAI325508, AW049829, Hsc20, Q8K3A0, gene:10090020APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesiscerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl27mitochondrial ­ribosomal ­protein ­L27A630055F16Rik, D11Moh4, D11Moh47, D18Ertd643, D18Ertd643e, Q99N92, gene:9406420literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Hint2histidine ­triad ­nucleotide ­binding ­protein ­21190005L05Rik, Q9D0S9, gene:6891720APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisall 14
Etfbelectron ­transferring ­flavoprotein, ­beta ­polypeptide0610009I16Rik, 2810441H06Rik, Q9DCW4, gene:11082620literature, APEX_matrix, yeast mito homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Electron carriers > Q-linked reactions, other		all 14
Slc25a15solute ­carrier ­family ­25 ­(mitochondrial ­carrier ­ornithine ­transporter), ­member ­15D630044L02Rik, Or, Ornt1, Q9WVD5, gene:1840820literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Urea cycle;
Small molecule transport > SLC25A family		spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta
Oxnad1oxidoreductase ­NAD-binding ­domain ­containing ­12410002F01Rik, AW492292, BC019806, Q8VE38, gene:21888520APEX_matrix, GFP, targetP signal, yeast mito homolog, mito protein domain, coexpression++, MS/MS++Matrixnonecerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cyctcytochrome ­c, ­testisT-Cc, P00015, gene:1306720literature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++IMSMetabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits;
OXPHOS > Cytochrome C		all 14
Cycscytochrome ­c, ­somaticP62897, gene:1306320literature, APEX_IMS, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++IMSMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits;
OXPHOS > Cytochrome C;
Mitochondrial dynamics and surveillance > Apoptosis		all 14
Mrpl23mitochondrial ­ribosomal ­protein ­L23L23, L23mrp, Rp, Rpl23, Rpl23l, O35972, gene:1993520literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrpl9mitochondrial ­ribosomal ­protein ­L98030480E20Rik, AA409733, C330013D18Rik, L9mt, Q99N94, gene:7852320literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Chchd1coiled-coil-helix-coiled-coil-helix ­domain ­containing ­11110001O19Rik, 2400010G13Rik, MRP-S37, Q9CQA6, gene:6612120GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression+, MS/MSMIMMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atad3aATPase ­family, ­AAA ­domain ­containing ­3A2400004H09Rik, Atad3, Tob, Tob3, mKIAA1273, Q925I1, gene:10888820APEX_IMS, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++MIMMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial dynamics and surveillance > Organelle contact sites;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		all 14
Mmutmethylmalonyl-Coenzyme ­A ­mutaseD230010K02Rik, Mcm, Mut, P16332, gene:1785020literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Vitamin metabolism > Vitamin B12 metabolism		all 14
Cisd1CDGSH ­iron ­sulfur ­domain ­1AU043990, AW743335, D10Ertd214, D10Ertd214e, Zcd1, mitoN, mitoNEET, Q91WS0, gene:5263720literature, mito protein domain, induction, coexpression++, MS/MS++MOMMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Dars2aspartyl-tRNA ­synthetase ­2 ­(mitochondrial)5830468K18Rik, aspRS, Q8BIP0, gene:22653920APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aldh18a1aldehyde ­dehydrogenase ­18 ­family, ­member ­A12810433K04Rik, AI429789, Py, Pycs, Q9Z110, gene:5645420literature, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolismcerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl50mitochondrial ­ribosomal ­protein ­L50AA408971, AI317351, D4Wsu125, D4Wsu125e, Q8VDT9, gene:2802820literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox8acytochrome ­c ­oxidase ­subunit ­8ACOX, COX8L, Q64445, gene:1286820literature, targetP signal+, mito protein domain+, coexpression+, MS/MSMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		stomach, placenta, testis
Mrps6mitochondrial ­ribosomal ­protein ­S6AW046321, P58064, gene:12102220literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Hspe1heat ­shock ­protein ­1 ­(chaperonin ­10)10kDa, Hsp, Hsp10, mt-cpn10, Q64433, gene:1552820literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Ppa2pyrophosphatase ­(inorganic) ­21110013G13Rik, Sid63, Sid6306, Q91VM9, gene:7477620literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance;
Mitochondrial central dogma > mtRNA metabolism;
Mitochondrial central dogma > Translation;
Metabolism > Nucleotide metabolism		all 14
Pcxpyruvate ­carboxylaseP, Pc, Pcb, E9QPD7, gene:1856320literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > TCA-associated;
Metabolism > Vitamin metabolism > Biotin utilizing proteins		all 14
Gldcglycine ­decarboxylaseD030049L12Rik, D19Wsu57, D19Wsu57e, b2b2679C, b2b2679Clo, Q91W43, gene:10417420literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system		cerebrum, cerebellum, kidney, liver, adipose, placenta
Tamm41TAM41 ­mitochondrial ­translocator ­assembly ­and ­maintenance ­homolog1500001M20Rik, TAM41, G5E881, gene:6897120GFP, yeast mito homolog++, mito protein domain+, MS/MS++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Atp5g3ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­C3 ­(subunit ­9)6030447M23, Atp5mc3, P56384, gene:22803319literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		none
Mrpl38mitochondrial ­ribosomal ­protein ­L381110036N21Rik, 4733401F03Rik, MRP, MRP-L3, R75240, Rp, Rpml3, Q8K2M0, gene:6044119APEX_matrix, targetP signal+, mito protein domain, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, heart, smallintestine, largeintestine, stomach, placenta, testis
Ndufa12NADH:ubiquinone ­oxidoreductase ­subunit ­A122410011G03Rik, AW112974, CI-B17.2, CIB17.2, Q7TMF3, gene:6641419literature, APEX_matrix, Rickettsial homolog, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Pdfpeptide ­deformylase ­(mitochondrial)2610019N19Rik, S4R2K0, gene:6802319APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > fMet processing;
Protein import, sorting and homeostasis > Protein homeostasis		cerebrum, heart, skeletalmuscle, adipose, largeintestine, placenta, testis
Acad10acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­102410021P16Rik, Q8K370, gene:7198519APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ptges2prostaglandin ­E ­synthase ­20610038H10Rik, C79137, Gbf1, Mpges2, Pges2, Q8BWM0, gene:9697919literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Eicosanoid metabolismall 14
Ccdc58coiled-coil ­domain ­containing ­58A930007B11Rik, AI413631, Q8R3Q6, gene:38104519APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++IMSnoneall 14
Slc25a31solute ­carrier ­family ­25 ­(mitochondrial ­carrier; ­adenine ­nucleotide ­translocator), ­member ­311700034J06Rik, Ant4, Sfec, Q3V132, gene:7333319literature, yeast mito homolog++, mito protein domain+, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport > SLC25A family		all 14
Atp5hATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­D0610009D10Rik, Atp5pd, Q9DCX2, gene:7167919literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Atp5pbATP ­synthase ­peripheral ­stalk-membrane ­subunit ­bAtp5, Atp5f1, C76477, Q9CQQ7, gene:1195019literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Mrpl41mitochondrial ­ribosomal ­protein ­L41MRP-, MRP-L27, Rpm, Rpml27, Q9CQN7, gene:10773319literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Txnrd2thioredoxin ­reductase ­2AA118373, ESTM57301, ESTM573010, TG, TGR, TR, Tr3, Trxr2, Trxrd2, Q9JLT4, gene:2646219literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins		cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mceemethylmalonyl ­CoA ­epimerase1110007A04Rik, Q9D1I5, gene:7372419targetP signal, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation		all 14
Mccc2methylcrotonoyl-Coenzyme ­A ­carboxylase ­2 ­(beta)4930552N12Rik, MCCB, Q3ULD5, gene:7803819literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Ptcd2pentatricopeptide ­repeat ­domain ­21190005P08Rik, Q8R3K3, gene:6892719literature, targetP signal, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing		smallintestine, largeintestine, placenta
Ak4adenylate ­kinase ­4AK 4, Ak-, Ak-3, Ak-4, Ak3, Ak3l1, D4Ertd274, D4Ertd274e, Q9WUR9, gene:1163919APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
Slc25a25solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­251110030N17Rik, MCSC, mKIAA1896, A2ASZ8, gene:22773119literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family		cerebrum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, placenta
Tomm40translocase ­of ­outer ­mitochondrial ­membrane ­40AW539759, Mom35, Tom4, Tom40, Q9QYA2, gene:5333319literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Clyblcitrate ­lyase ­beta ­like0610033J05Rik, 2310014M14Rik, AI256068, Cl, Clb, Q8R4N0, gene:6963419APEX_matrix, targetP signal+, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolismall 14
Mterf2mitochondrial ­transcription ­termination ­factor ­21700007D05Rik, Mterfd, Mterfd3, Q8BKY8, gene:7423819literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoidcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, testis
Dnajc11DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C11E030019A03Rik, Q5U458, gene:23093519GFP, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		all 14
Decr12,4-dienoyl ­CoA ­reductase ­1, ­mitochondrial1200012F07Rik, Dec, Decr, Na, Nadph, Q9CQ62, gene:6746019literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufaf6NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­62310030N02Rik, A2AIL4, gene:7694719literature, targetP signal, mito protein domain, induction, coexpression++, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		adipose, smallintestine, largeintestine, placenta, testis
Ptrh1peptidyl-tRNA ­hydrolase ­1 ­homolog2210013M04Rik, AW046744, Q8BW00, gene:32938419APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixnonecerebrum, cerebellum, brainstem, largeintestine, placenta
Rmnd1required ­for ­meiotic ­nuclear ­division ­1 ­homolog0610042C05Rik, AA408137, AI462664, AW536662, Q8CI78, gene:6608419literature, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation		cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Gcatglycine ­C-acetyltransferase ­(2-amino-3-ketobutyrate-coenzyme ­A ­ligase)AI526977, Kb, Kbl, O88986, gene:2691219literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++unknownMetabolism > Amino acid metabolism > Glycine metabolismbrainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
PyurfPigy ­upstream ­reading ­frame2610022G08Rik, AI847956, Pi, Prey, Q9D1C3, gene:6645919targetP signal+, induction, coexpression++, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
Acsm1acyl-CoA ­synthetase ­medium-chain ­family ­member ­1Acas3, Bucs, Bucs1, Ma, Macs, Q91VA0, gene:11714719literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationspinalcord, kidney, liver, smallintestine
Atad1ATPase ­family, ­AAA ­domain ­containing ­14921525H23Rik, AW107648, Tho, Thorase, Q9D5T0, gene:6797919yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Tmem14ctransmembrane ­protein ­14C1110021D01Rik, AU020193, HSPC1, HSPC194, Q9CQN6, gene:6615419literature, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS+MIMnoneall 14
C030006K11RikRIKEN ­cDNA ­C030006K11 ­gene1110033I13Rik, Q8VE95, gene:22366519APEX_matrix, targetP signal+, coexpression+, MS/MS++Matrixnoneall 14
Nit2nitrilase ­family, ­member ­21190017B19Rik, D16Ertd502, D16Ertd502e, Q9JHW2, gene:5263319yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++unknownMetabolism > Detoxificationcerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a26solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­264930433D19Rik, 4933433F13Rik, AW557176, D6Bwg0781e, Slc25a6, Q5U680, gene:6758219literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, cerebellum, adipose, largeintestine, placenta, testis
Timm21translocase ­of ­inner ­mitochondrial ­membrane ­211700034H14Rik, 2700002I20Rik, Q8CCM6, gene:6710519APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMMitochondrial central dogma > Translation > Translation factors;
Protein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Ndufa4Ndufa4, ­mitochondrial ­complex ­associatedML, MLRQ, Q62425, gene:1799219literature, targetP signal, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Rexo2RNA ­exonuclease ­21810038D15Rik, AW107347, Rex, Rex2, S, Sfn, Sm, Smfn, Q9D8S4, gene:10444419APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decayall 14
Me2malic ­enzyme ­2, ­NAD(+)-dependent, ­mitochondrialAW120568, D030040L20Rik, NAD-ME, Q99KE1, gene:10702919literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sars2seryl-aminoacyl-tRNA ­synthetase ­22410015F05Rik, D7Ertd353, D7Ertd353e, SerRS, SerRSmt, Q9JJL8, gene:7198419literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesskeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
DnlzDNL-type ­zinc ­finger1110034G11Rik, D2Bwg1335e, HEP1, Q9D113, gene:5283819APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MSMatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonescerebrum, cerebellum, brainstem, heart, adipose, smallintestine, largeintestine, stomach, placenta
Ckmt2creatine ­kinase, ­mitochondrial ­22300008A19Rik, ScCKm, ScCKmit, Q6P8J7, gene:7672219literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Creatine metabolismcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Spryd4SPRY ­domain ­containing ­44633402N23Rik, AA114801, Q91WK1, gene:6670118APEX_matrix, GFP, targetP signal, mito protein domain, coexpression+, MS/MS++Matrixnoneall 14
Bphlbiphenyl ­hydrolase-like ­(serine ­hydrolase, ­breast ­epithelial ­mucin-associated ­antigen)2010012D11Rik, 5730533B08Rik, AI115341, Q8R164, gene:6802118targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Chchd4coiled-coil-helix-coiled-coil-helix ­domain ­containing ­42410012P20Rik, 2810014D17Rik, AI838740, Q8VEA4, gene:7217018literature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS+IMSProtein import, sorting and homeostasis > Protein import and sorting > MIA40cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl37mitochondrial ­ribosomal ­protein ­L372300004O14Rik, AI132596, MRP, MRP-L2, Rp, Rpml2, Q921S7, gene:5628018literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomekidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a51solute ­carrier ­family ­25, ­member ­519130208E07Rik, D130005A03Rik, Gm138, Mcar, Mcart1, Q5HZI9, gene:23012518GFP, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolism;
Small molecule transport > SLC25A family		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtarc2mitochondrial ­amidoxime ­reducing ­component ­22810484M10Rik, Mar, Marc2, Mos, Mosc2, mARC1, Q922Q1, gene:6724718literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS++MOMMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Metabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex		all 14
Immp1lIMP1 ­inner ­mitochondrial ­membrane ­peptidase-like ­(S. ­cerevisiae)1500034J20Rik, 2610528O17Rik, AU042386, Q9CQU8, gene:6654118literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		testis
Fam210afamily ­with ­sequence ­similarity ­210, ­member ­A4933403F05Rik, AA987140, AV134576, AW491926, Q8BGY7, gene:10865418GFP, targetP signal, induction, coexpression++, MS/MSMIMnoneall 14
Mrps24mitochondrial ­ribosomal ­protein ­S243110030K20Rik, AI414579, MRP-S24, Rpm, Rpms24, S24mt, Q9CQV5, gene:6466018literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Timm17btranslocase ­of ­inner ­mitochondrial ­membrane ­17b17kD, 17kDa, Sfc, Sfc3, mTim17, mTim17b, Q9Z0V7, gene:2185518literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Hars2histidyl-tRNA ­synthetase ­24631412B19Rik, H, HARSR, HO, HO3, Harsl, Q99KK9, gene:7079118literature, APEX_matrix, GFP, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebellum, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox16cytochrome ­c ­oxidase ­assembly ­protein ­161810020G14Rik, 1810055I05Rik, BB388670, Q9CR63, gene:6627218APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		kidney, liver, adipose, largeintestine, placenta, testis
Pdss2prenyl ­(solanesyl) ­diphosphate ­synthase, ­subunit ­25430420P03Rik, Gm60, P, Plmp, kd, mDL, mDLP1, Q33DR3, gene:7136518literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismsmallintestine, largeintestine
Eci1enoyl-Coenzyme ­A ­delta ­isomerase ­1Dc, Dci, ec, eci, P42125, gene:1317718literature, APEX_matrix, targetP signal+, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufs3NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S30610010M09Rik, CI-30kD, Q9DCT2, gene:6834918literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Hmgcs23-hydroxy-3-methylglutaryl-Coenzyme ­A ­synthase ­21300002P16, mH, mHS, P54869, gene:1536018literature, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolismcerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
L2hgdhL-2-hydroxyglutarate ­dehydrogenaseBC016226, Q91YP0, gene:21766618literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
Zadh2zinc ­binding ­alcohol ­dehydrogenase, ­domain ­containing ­2C530046K17Rik, PTGR-3, Pth, Pthr3, Q8BGC4, gene:22579118targetP signal, mito protein domain, induction, coexpression+, MS/MS++unknownMetabolism > Lipid metabolism > Eicosanoid metabolismall 14
Aurkaip1aurora ­kinase ­A ­interacting ­protein ­10610033H09Rik, Aip, Akip, MRP-S38, Q9DCJ7, gene:6607718GFP, targetP signal+, yeast mito homolog++, mito protein domain, coexpression+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomenone
Coa5cytochrome ­C ­oxidase ­assembly ­factor ­51700001A24Rik, 6330578E17Rik, Pet19, Pet191, Q99M07, gene:7617818literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		adipose, placenta, testis
H2-Ke6H2-K ­region ­expressed ­gene ­6D17H6S112E, H-2Ke6, Hsd17b8, Ke-6, Ke6, Ri, Ring2, P50171, gene:1497918APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis;
Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis		all 14
Micos13mitochondrial ­contact ­site ­and ­cristae ­organizing ­system ­subunit ­132410015M20Rik, Mic13, QI, QIL1, sr104, Q8R404, gene:22490418induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Ndufb7NADH:ubiquinone ­oxidoreductase ­subunit ­B71110002H15Rik, Q9CR61, gene:6691618literature, APEX_IMS, APEX_matrix, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Nipsnap2nipsnap ­homolog ­2AV006093, Gb, Gbas, N, Q7TMG8, gene:1446718literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MS++MatrixMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		all 14
Mrpl47mitochondrial ­ribosomal ­protein ­L474833424P18Rik, CGI-20, CGI-204, Gm9859, L47mt, MRP-L47, MTF/L47, NCM, NCM1, Q8K2Y7, gene:7460018literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome		all 14
Mtres1mitochondrial ­transcription ­rescue ­factor ­11700021F05Rik, Q9CQF4, gene:6785118GFP, targetP signal, induction, coexpression++, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > Transcription;
Mitochondrial central dogma > Translation		all 14
Ndufaf7NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­72410091C18Rik, AL033374, PRO1853, Q9CWG8, gene:7369418APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, brainstem, spinalcord, kidney, adipose, largeintestine, stomach, placenta, testis
Acad9acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­92600017P15Rik, 4732402K02, C630012L17Rik, NPD0, NPD002, Q8JZN5, gene:22921118literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
NagsN-acetylglutamate ­synthase1700120E20Rik, argA, Q8R4H7, gene:21721418literature, targetP signal, yeast mito homolog++, mito protein domain+, MS/MSMatrixMetabolism > Amino acid metabolism > Urea cycleliver
Ldhdlactate ­dehydrogenase ­D4733401P21Rik, D8Bwg1320e, DLD, Q7TNG8, gene:5281518literature, targetP signal+, yeast mito homolog+, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolismkidney, liver, heart, adipose, stomach, placenta, testis
Sardhsarcosine ­dehydrogenaseQ99LB7, gene:19216618literature, targetP signal+, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sprsepiapterin ­reductaseAA409688, Gm10328, Q91XH5, gene:2075118targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++unknownMetabolism > Metals and cofactors > Tetrahydrobiopterin synthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach
NaxeNAD(P)HX ­epimeraseAA087124, AI, AI-BP, AIBP, AP, Apoa1bp, Apoa1ip, ESTM3, ESTM37, Q8K4Z3, gene:24670318APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismall 14
Timm23translocase ­of ­inner ­mitochondrial ­membrane ­23Tim2, Tim23, Q9CXU4, gene:5360018literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Mpv17MpV17 ­mitochondrial ­inner ­membrane ­proteinTg.Mpv, Tg.Mpv17, P19258, gene:1752718literature, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MIMSmall molecule transportall 14
Mtg1mitochondrial ­ribosome-associated ­GTPase ­1Gm169, Gtpb, Gtpbp7, Q8R2R6, gene:21250818literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, testis
Ideinsulin ­degrading ­enzyme1300012G03Rik, 4833415K22Rik, AA675336, AI507533, AI507533, gene:1592518literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Trnt1tRNA ­nucleotidyl ­transferase, ­CCA-adding, ­12410043H24Rik, 2610044E04Rik, 9830143O18Rik, AA408384, C76540, CGI-4, CGI-47, mt-Trat, Q8K1J6, gene:7004718literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsspinalcord, adipose, placenta, testis
Mrps25mitochondrial ­ribosomal ­protein ­S252810429N01Rik, Rpm, Rpms25, Q9D125, gene:6465818literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrpl14mitochondrial ­ribosomal ­protein ­L141110006I11Rik, AI846816, MRP-, MRP-L32, Rpm, Rpml32, Q9D1I6, gene:6846318literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrps30mitochondrial ­ribosomal ­protein ­S302610020A16Rik, AA968347, PAP, Pdcd, Pdcd9, Q9D0G0, gene:5905418literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps16mitochondrial ­ribosomal ­protein ­S161500011E11Rik, Mprs16, S16mt, Q9CPX7, gene:6624217literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Prelid2PRELI ­domain ­containing ­21700003A01Rik, C330008K14Rik, Q0VBB0, gene:7761917yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MSIMSnonelargeintestine, stomach
Shmt2serine ­hydroxymethyltransferase ­2 ­(mitochondrial)2700043D08Rik, AA408223, AA986903, SHMT, Q9CZN7, gene:10803717literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Suoxsulfite ­oxidaseSO, Q8R086, gene:21138917APEX_IMS, targetP signal, mito protein domain+, coexpression, MS/MS++IMSMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Metabolism > Sulfur metabolism		cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ccdc90bcoiled-coil ­domain ­containing ­90B2310015N07Rik, C86558, Q8C3X2, gene:6636517literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MSMIMnoneall 14
Rmdn1regulator ­of ­microtubule ­dynamics ­1Fam82, Fam82b, RMD-1, Q9DCV4, gene:6630217APEX_IMS, targetP signal+, mito protein domain, induction, coexpression, MS/MSMOMnoneall 14
Acsm5acyl-CoA ­synthetase ­medium-chain ­family ­member ­5C730019D22, C730027J19Rik, Q8BGA8, gene:27242817literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Detoxification > Xenobiotic metabolism		kidney, liver, adipose, smallintestine, largeintestine
Mrpl36mitochondrial ­ribosomal ­protein ­L36AI646041, Q99N90, gene:9406617literature, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomenone
Gstk1glutathione ­S-transferase ­kappa ­10610025I19Rik, AW260476, Dsb, DsbA-L, Q9DCM2, gene:7626317literature, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Fmc1formation ­of ­mitochondrial ­complex ­V ­assembly ­factor ­11110001J03Rik, Q9CR13, gene:6611717literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl58mitochondrial ­ribosomal ­protein ­L581110001A02Rik, 1110002E03Rik, Ict, Ict1, MRP-L58, Q8R035, gene:6857217APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome;
Mitochondrial central dogma > Translation > Translation factors		all 14
Cpt1acarnitine ­palmitoyltransferase ­1a, ­liverC730027G07, CP, CPTI, Cpt, Cpt1, P97742, gene:1289417literature, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle		all 14
Ak2adenylate ­kinase ­2Ak-, Ak-2, D4Ertd220, D4Ertd220e, Q9WTP6, gene:1163717literature, APEX_IMS, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++IMSMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
2810006K23RikRIKEN ­cDNA ­2810006K23 ­geneQ80VP5, gene:7265017literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Translation factorscerebrum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta
Glsglutaminase6330442B14, AI314027, B230365M23Rik, D3Z7P3, gene:1466017literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Glutamate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Them4thioesterase ­superfamily ­member ­42700077M13Rik, 4921507I02Rik, Q3UUI3, gene:7577817literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, MS/MS++MIMMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Pdss1prenyl ­(solanesyl) ­diphosphate ­synthase, ­subunit ­12610203G20Rik, 2700031G06Rik, TPT, TPT 1, Tp, Tprt, mDLP1, mS, mSPS1, Q33DR2, gene:5607517APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Metals and cofactors > Coenzyme Q metabolismskeletalmuscle, largeintestine, placenta, testis
Mtg2mitochondrial ­ribosome ­associated ­GTPase ­21810011P19Rik, 2900056P18Rik, D2Bwg0647e, Gtpb, Gtpbp5, A2AFK4, gene:5285617literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, placenta
Mrps11mitochondrial ­ribosomal ­protein ­S110710005I03Rik, C79873, MRP-S11, S11mt, Q3U8Y1, gene:6799417literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mlycdmalonyl-CoA ­decarboxylaseAI324784, Mcd, Q99J39, gene:5669017literature, APEX_matrix, targetP signal, mito protein domain, coexpression++, MS/MSMatrixMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
TcaimT ­cell ­activation ­inhibitor, ­mitochondrialD9Ertd402, D9Ertd402e, Gm1129, TOAG-1, Q66JZ4, gene:38211717literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++Matrixnonenone
Ndufc1NADH:ubiquinone ­oxidoreductase ­subunit ­C12310016K22Rik, KFYI, Q9CQY9, gene:6637717literature, targetP signal+, mito protein domain+, coexpression++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		none
Gsrglutathione ­reductaseAI325518, D8Ertd238, D8Ertd238e, Gr-, Gr-1, Gr1, P47791, gene:1478217literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismspinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Rars2arginyl-tRNA ­synthetase ­2, ­mitochondrial1500002I10Rik, PRO1, PRO1992, Rarsl, Q3U186, gene:10909317literature, APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesall 14
Slc25a24solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­242610016M12Rik, Q8BMD8, gene:22973117literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family		adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a18solute ­carrier ­family ­25 ­(mitochondrial ­carrier), ­member ­181500015I14Rik, AW125787, Q9DB41, gene:7180317literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a22solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­glutamate), ­member ­221300006L01Rik, AI060884, Gc1, Q9D6M3, gene:6826717literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mpc1mitochondrial ­pyruvate ­carrier ­10610006G08Rik, 3830411I18Rik, Brp, Brp44l, P63030, gene:5595117GFP, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport		all 14
Timm8a1translocase ­of ­inner ­mitochondrial ­membrane ­8A1DXHXS1274, DXHXS1274E, Ddp, Ddp1, Fci-1, Fci-12, Tim, Tim8a, Timm8a, Q9WVA2, gene:3005817literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		all 14
Vdac3voltage-dependent ­anion ­channel ­3Q60931, gene:2233517literature, yeast mito homolog+, mito protein domain+, MS/MS++MOMSignaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport		all 14
Akap1A ­kinase ­(PRKA) ­anchor ­protein ­1AKA, AKAP121, AKAP84, Akap, C76494, C81186, DAK, DAKAP1, S-AK, S-AKAP84, O08715, gene:1164017literature, mito protein domain, induction, coexpression++, MS/MS+MOMSignaling > cAMP-PKA signalingcerebellum, skeletalmuscle, testis
Eci2enoyl-Coenzyme ­A ­delta ­isomerase ­2ACBD, Acbd2, DR, Drs1, HCA8, Hca88, Pe, Peci, Q9WUR2, gene:2398617literature, APEX_matrix, targetP signal, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Mrm2mitochondrial ­rRNA ­methyltransferase ­22310037B18Rik, Ftsj, Ftsj2, Q9CPY0, gene:6801717literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		cerebrum
Lipt2lipoyl(octanoyl) ­transferase ­2 ­(putative)2610209A20Rik, Q9D009, gene:6716417yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertioncerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
Nubplnucleotide ­binding ­protein-like2410170E07Rik, Q9CWD8, gene:7682617literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MatrixOXPHOS > Complex I > CI assembly factors;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS assembly factors		spinalcord, adipose, largeintestine, stomach, placenta, testis
Sfxn1sideroflexin ­12810002O05Rik, A930015P12Rik, f, Q99JR1, gene:1405717literature, yeast mito homolog, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > Sideroflexins		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc30a9solute ­carrier ­family ­30 ­(zinc ­transporter), ­member ­92310024J23Rik, AL024256, GAC6, GAC63, HUEL, znT-9, Q5IRJ6, gene:10910817APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MSMIMSmall molecule transportcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Gatmglycine ­amidinotransferase ­(L-arginine:glycine ­amidinotransferase)1810003P21Rik, AI314789, AT, Q9D964, gene:6709217literature, targetP signal, mito protein domain+, MS/MS++MatrixMetabolism > Nucleotide metabolism > Creatine metabolismspinalcord, kidney, liver, stomach, placenta, testis
Triap1TP53 ­regulated ­inhibitor ­of ­apoptosis ­11810015M01Rik, AU020874, AU043831, P53csv, Wf-1, Q9D8Z2, gene:6907616literature, yeast mito homolog++, mito protein domain, induction, MS/MS++IMSMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		adipose, stomach, placenta
Cpoxcoproporphyrinogen ­oxidaseC, CPX, Cpo, HCP, ca, cac, nc, nct, P36552, gene:1289216literature, APEX_IMS, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Heme synthesis and processingcerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Xpnpep3X-prolyl ­aminopeptidase ­3, ­mitochondrialAPP3, E430012M05Rik, B7ZMP1, gene:32100316literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		cerebrum, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pnpla8patatin-like ­phospholipase ­domain ­containing ­81200006O19Rik, AI467579, Ipla2(gamma), Q8K1N1, gene:6745216APEX_matrix, Rickettsial homolog, induction, coexpression++, MS/MS+MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, testis
Gadd45gip1growth ­arrest ­and ­DNA-damage-inducible, ­gamma ­interacting ­protein ­12310040G17Rik, AI425883, Cri, Crif1, MRP-L59, Plinp1, Q9CR59, gene:10206016APEX_matrix, GFP, targetP signal+, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Gfergrowth ­factor, ­augmenter ­of ­liver ­regenerationAlr, ER, ERV1, P56213, gene:1169216literature, GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MSIMSProtein import, sorting and homeostasis > Protein import and sorting > MIA40cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ngrnneugrin, ­neurite ­outgrowth ­associatedAW552001, Q99KS2, gene:8348516APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		none
Mrpl57mitochondrial ­ribosomal ­protein ­L572610025P17Rik, AV005697, Mrp, Mrp63, Q9CQF8, gene:6784016literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Ndufa3NADH:ubiquinone ­oxidoreductase ­subunit ­A31010001M12Rik, 1700022J01Rik, Q9CQ91, gene:6609116literature, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ptcd3pentatricopeptide ­repeat ­domain ­32610034F17Rik, 2810422B04Rik, AA589622, AU045708, MRP-S39, Q14C51, gene:6995616literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		all 14
Mrpl45mitochondrial ­ribosomal ­protein ­L452600005P05Rik, AU043542, R75241, Q9D0Q7, gene:6703616literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a16solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­Graves ­disease ­autoantigen), ­member ­163110021G18Rik, GDA, GDC, HGT.1, ML, ML7, Q8C0K5, gene:7313216literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Ucp1uncoupling ­protein ­1 ­(mitochondrial, ­proton ­carrier)AI385626, Slc2, Slc25a7, Ucp, P12242, gene:2222716literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A familyadipose
Tars2threonyl-tRNA ­synthetase ­2, ­mitochondrial ­(putative)2610024N01Rik, AI429208, Ta, Tarsl1, thrRS, Q3UQ84, gene:7180716APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Trit1tRNA ­isopentenyltransferase ­12310075G14Rik, AI314189, AI314635, AV099619, IPPT, IPT, MOD, MOD5, Q80UN9, gene:6696616literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications		cerebellum
Ndufab1NADH:ubiquinone ­oxidoreductase ­subunit ­AB12210401F17Rik, 2310039H15Rik, 2610003B19Rik, 8kD, 8kDa, 9130423F15Rik, ACP, CI-SDAP, SDAP, Q9CR21, gene:7031616literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+MIMOXPHOS > Complex I > CI subunits;
Metabolism > Lipid metabolism > Type II fatty acid synthesis;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
OXPHOS > OXPHOS subunits		all 14
Cslcitrate ­synthase ­like1700007H16Rik, Q80X68, gene:7183216targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++Matrixnoneall 14
Slc25a39solute ­carrier ­family ­25, ­member ­393010027G13Rik, D11Ertd333, D11Ertd333e, Q9D8K8, gene:6806616literature, yeast mito homolog+, mito protein domain+, induction, coexpressionMIMSmall molecule transport > SLC25A familynone
Prelid3bPRELI ­domain ­containing ­3B2310042G06Rik, AA407013, Sl, Slmo2, Q9CYY7, gene:6639016GFP, yeast mito homolog+, mito protein domain+, induction, coexpressionIMSMetabolism > Lipid metabolism > Phospholipid metabolismnone
Mtch1mitochondrial ­carrier ­12310034O17Rik, AI255158, AU018396, C77849, PSAP, Q791T5, gene:5646216literature, yeast mito homolog+, mito protein domain+, MS/MS++MOMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dele1DAP3 ­binding ­cell ­death ­enhancer ­10610009O20Rik, 2700004E22Rik, DELE1(L), Dele, Kiaa0141, Q9DCV6, gene:6683916targetP signal+, yeast mito homolog, mito protein domain, induction, coexpressionMIMSignalingnone
Acaa1aacetyl-Coenzyme ­A ­acyltransferase ­1AAc, Acaa, Acaa1, D9Ertd25, D9Ertd25e, P, PTL, Q921H8, gene:11386816targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Fatty acid oxidationspinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acot13acyl-CoA ­thioesterase ­130610006O17Rik, Them2, Q9CQR4, gene:6683416mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolismall 14
Ndufa13NADH:ubiquinone ­oxidoreductase ­subunit ­A132700054G14Rik, AU022060, CDA01, CDA016, CGI-3, CGI-39, CI-B16.6, GRIM-, GRIM-19, Grim, Grim19, F6W8I0, gene:6718416literature, APEX_IMS, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Agxt2alanine-glyoxylate ­aminotransferase ­2AI303810, AI663818, Q3UEG6, gene:26878216literature, targetP signal, yeast mito homolog++, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism > Glyoxylate metabolismkidney, liver
Selenooselenoprotein ­O1300018J18Rik, S, Selo, Q9DBC0, gene:22377616targetP signal+, yeast mito homolog, mito protein domain+, coexpressionMatrixMetabolism > Detoxification > Selenoproteinsspinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Oxld1oxidoreductase ­like ­domain ­containing ­11810049H13Rik, Q9CR10, gene:6643116targetP signal, yeast mito homolog, mito protein domain+, coexpression+unknownnoneadipose, largeintestine, stomach
Mfn2mitofusin ­2D630023P19Rik, Fz, Fzo, Q80U63, gene:17073116literature, mito protein domain+, induction, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Organelle contact sites		cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Chdhcholine ­dehydrogenaseAU041472, D630034H06Rik, Q8BJ64, gene:21886516APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Metabolism > Electron carriers > Q-linked reactions, other		spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Msramethionine ­sulfoxide ­reductase ­A2310045J23Rik, 6530413P12Rik, MS, MSR-A, Q9D6Y7, gene:11026516targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Sulfur metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Nit1nitrilase ­1AI255805, ESTM3, ESTM30, W57327, Q8VDK1, gene:2704516APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox4i2cytochrome ­c ­oxidase ­subunit ­4I2Cox4, Cox4b, CoxIV-2, Q91W29, gene:8468216literature, targetP signal, yeast mito homolog++, mito protein domain+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		cerebrum, spinalcord, heart, adipose, largeintestine, stomach, placenta
Lactblactamase, ­betaLACT-1, Lact1, Mrp, Mrpl56, Q9EP89, gene:8090716literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++IMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Metabolism > Lipid metabolism > Phospholipid metabolism		all 14
Tstthiosulfate ­sulfurtransferase, ­mitochondrialRhod, rhodanese, P52196, gene:2211716literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Sulfur metabolism		all 14
Coa8cytochrome ­c ­oxidase ­assembly ­factor ­81700081D05Rik, 2810002N01Rik, Ap, Apop-1, Apop1, Apopt1, Q9CQW7, gene:6802016literature, targetP signal+, mito protein domain+, coexpression+MIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		largeintestine, placenta
Prodh2proline ­dehydrogenase ­(oxidase) ­22510028N04Rik, 2510038B11Rik, HYPDH, MmPO, MmPOX, MmPOX1, POX1, Q8VCZ9, gene:5618916targetP signal, yeast mito homolog+, mito protein domain+, MS/MS+MIMMetabolism > Amino acid metabolism > Glyoxylate metabolism;
Metabolism > Electron carriers > Q-linked reactions, other		kidney, liver
Cox7bcytochrome ­c ­oxidase ­subunit ­7B1110004F07Rik, C80563, P56393, gene:6614216literature, targetP signal, mito protein domain+, induction, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
Glrx2glutaredoxin ­2 ­(thioltransferase)1700010P22Rik, AI645710, Grx, Grx2, Q923X4, gene:6936716literature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S-containing proteins;
Metabolism > Vitamin metabolism > Vitamin C metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism		cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, largeintestine, placenta, testis
Aldh1b1aldehyde ­dehydrogenase ­1 ­family, ­member ­B12700007F14Rik, Q9CZS1, gene:7253516literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Ndufb3NADH:ubiquinone ­oxidoreductase ­subunit ­B32700033I16Rik, CI-B12, Q9CQZ6, gene:6649516literature, APEX_IMS, APEX_matrix, mito protein domain+, coexpression+, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ehhadhenoyl-Coenzyme ­A, ­hydratase/3-hydroxyacyl ­Coenzyme ­A ­dehydrogenase1300002P22Rik, HD, L-P, L-PBE, LBFP, LBP, MF, MFE1, MFP, MFP-1, MFP1, PBFE, Q9DBM2, gene:7414715yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+unknownMetabolism > Lipid metabolismspinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta
Echdc1enoyl ­Coenzyme ­A ­hydratase ­domain ­containing ­11700028A24Rik, AI314462, AI930038, D10Ertd667e, MMCD, Q9D9V3, gene:5266515yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+unknownMetabolism > Lipid metabolismbrainstem, spinalcord, liver, adipose, largeintestine, placenta, testis
TrmutRNA ­5-methylaminomethyl-2-thiouridylate ­methyltransferase1110005N20Rik, 1600025P05Rik, AI314320, Trmt, Trmt1, Q9DAT5, gene:7202615literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsadipose, largeintestine, placenta
Vars2valyl-tRNA ­synthetase ­2, ­mitochondrial1190004I24Rik, V, Vars2l, mKIAA1885, Q3U2A8, gene:6891515APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mettl17methyltransferase ­like ­172310032K15Rik, D14Ertd209, D14Ertd209e, Mett11d1, Q3U2U7, gene:5253515GFP, targetP signal+, yeast mito homolog++, mito protein domain+MatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		none
Aassaminoadipate-semialdehyde ­synthaseLKR, LKR/SDH, LOR, LOR/SDH, Lo, Lorsdh, SDH, Q99K67, gene:3095615APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Aadataminoadipate ­aminotransferaseAI875679, Aadt, KA, KATII, Kat, Kat2, Kyat, Kyat2, mKat-, mKat-2, Q9WVM8, gene:2392315targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolismkidney, liver
Ndufa11NADH:ubiquinone ­oxidoreductase ­subunit ­A112010012C24Rik, AV006275, B14.7, G5E814, gene:6987515literature, APEX_IMS, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Gm4984predicted ­pseudogene ­4984AI428901, EG245347, EG245347, gene:24534715yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport		testis
Slc25a21solute ­carrier ­family ­25 ­(mitochondrial ­oxodicarboxylate ­carrier), ­member ­219930033G19Rik, A630030I10, BB158148, Q8BZ09, gene:21759315literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism;
Small molecule transport > SLC25A family		spinalcord, kidney, liver, testis
Slc25a29solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­palmitoylcarnitine ­transporter), ­member ­29C030003J19Rik, CA, CACL, mCA, mCACL, Q8BL03, gene:21466315literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Lysine metabolism;
Small molecule transport > SLC25A family		placenta, testis
Mthfd2methylenetetrahydrofolate ­dehydrogenase ­(NAD+ ­dependent), ­methenyltetrahydrofolate ­cyclohydrolaseAW558851, NMDM, NMDMC, P18155, gene:1776815literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismspinalcord, placenta, testis
Mmabmethylmalonic ­aciduria ­(cobalamin ­deficiency) ­cblB ­type ­homolog ­(human)9130222L19Rik, ATR, Q9D273, gene:7769715APEX_matrix, GFP, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Hsd17b4hydroxysteroid ­(17-beta) ­dehydrogenase ­417-beta-HSD, 17[b]-HS, 17[b]-HSD, DBP, MFE-2, MFP, MFP2, MPF-2, Mfp-, Mfp-2, perMFE, perMFE-2, P51660, gene:1548815Rickettsial homolog, mito protein domain+, induction, coexpressionunknownMetabolism > Lipid metabolismkidney, liver, adipose, largeintestine, stomach, testis
Nntnicotinamide ­nucleotide ­transhydrogenase4930423F13Rik, AI323702, BB168308, Q8C1W8, gene:1811515literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, spinalcord, skeletalmuscle, adipose, placenta
Tmem11transmembrane ­protein ­115730466P16Rik, AA409091, Q8BK08, gene:21682115GFP, targetP signal, mito protein domain+, induction, coexpression, MS/MSMIMMitochondrial dynamics and surveillanceall 14
Mrm3mitochondrial ­rRNA ­methyltransferase ­34833420N02Rik, AI255153, HC90, Rnm, Rnmtl1, Q5ND52, gene:6739015APEX_matrix, GFP, targetP signal, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		none
Ridareactive ­intermediate ­imine ­deaminase ­A ­homologHR1, HR12, HRP, HRP12, Hrs, Hrsp12, P52760, gene:1547315APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MS+Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox6a2cytochrome ­c ­oxidase ­subunit ­6A2COX, CoxVIaH, V, VIaH, P43023, gene:1286215literature, yeast mito homolog+, mito protein domain+, induction, coexpressionMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		heart, skeletalmuscle
Sco2SCO2 ­cytochrome ­c ­oxidase ­assembly ­proteinQ8VCL2, gene:10012682415literature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors		all 14
Cox18cytochrome ­c ­oxidase ­assembly ­protein ­18BC038311, Q8VC74, gene:23143015literature, targetP signal+, yeast mito homolog++, mito protein domain, coexpressionMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		none
Gcshglycine ­cleavage ­system ­protein ­H ­(aminomethyl ­carrier)1100001L02Rik, 5730591C18Rik, Q91WK5, gene:6813315literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain+, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system		spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Dmgdhdimethylglycine ­dehydrogenase ­precursor1200014D15Rik, AI787269, Q9DBT9, gene:7412915literature, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		spinalcord, kidney, liver, smallintestine, stomach, placenta
Rdh13retinol ­dehydrogenase ­13 ­(all-trans ­and ­9-cis)8430425D21Rik, Q8CEE7, gene:10884115yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin A metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Lyrm2LYR ­motif ­containing ­22610208E05Rik, Q8R033, gene:10875515APEX_matrix, GFP, targetP signal+, mito protein domain+, coexpression, MS/MSMatrixOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		heart, adipose, largeintestine, placenta
Prdx5peroxiredoxin ­5AOEB1, AOEB166, AOPP, P, PLP, PMP, Pmp20, Prd, Prdx6, PrxV, P99029, gene:5468314literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismall 14
Maip1matrix ­AAA ­peptidase ­interacting ­protein ­19430016H08Rik, AA409999, C78988, Q8BHE8, gene:6811514GFP, targetP signal, induction, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Gstz1glutathione ­transferase ­zeta ­1 ­(maleylacetoacetate ­isomerase)GSTZ1-1, MAAI, Q9WVL0, gene:1487414APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Twnktwinkle ­mtDNA ­helicaseD19Ertd626, D19Ertd626e, PEO, Pe, Peo1, Tw, Twinl, twin, Q8CIW5, gene:22615314literature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid		none
Tefmtranscription ­elongation ­factor, ­mitochondrial1110002N22Rik, Q5SSK3, gene:6855014APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Transcriptionliver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Coa3cytochrome ­C ­oxidase ­assembly ­factor ­31810033A19Rik, Ccdc56, D11Ertd99, D11Ertd99e, HSPC009, Q9D2R6, gene:5246914APEX_IMS, APEX_matrix, mito protein domain+, coexpression, MS/MS++MIMMitochondrial central dogma > Translation > Translation factors;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Mcur1mitochondrial ­calcium ­uniporter ­regulator ­16230416A05Rik, AU015498, AV136929, AW554392, C88263, Ccdc90, Ccdc90a, Q9CXD6, gene:7613714APEX_matrix, yeast mito homolog+, mito protein domain+, induction, MS/MSMIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Pck2phosphoenolpyruvate ­carboxykinase ­2 ­(mitochondrial)1810010O14Rik, 9130022B02Rik, PEPCK-M, Q8BH04, gene:7455114literature, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > TCA-associated		cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hmgcl3-hydroxy-3-methylglutaryl-Coenzyme ­A ­lyaseAW476067, HL, P38060, gene:1535614literature, APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Amino acid metabolism > BCAA metabolism		all 14
Abhd10abhydrolase ­domain ­containing ­10Q6PE15, gene:21301214literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
BC003965cDNA ­sequence ­BC003965Ccsmst1, Q6RUT7, gene:21448914APEX_IMS, targetP signal+, induction, coexpression, MS/MSIMSnonebrainstem, spinalcord, adipose, largeintestine, placenta, testis
Acot2acyl-CoA ­thioesterase ­2AA571646, MTE-, MTE-I, Mte1, Q9QYR9, gene:17121014literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolismall 14
Alas2aminolevulinic ­acid ­synthase ­2, ­erythroidA, ALAS, ALAS-E, ALASE, Al, Alas-2, P08680, gene:1165614literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpressionMatrixMetabolism > Metals and cofactors > Heme synthesis and processingnone
Acsm3acyl-CoA ­synthetase ­medium-chain ­family ­member ­3S, Sa, Sah, Q3UNX5, gene:2021614literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationkidney, liver, adipose, smallintestine, largeintestine, stomach
Romo1reactive ­oxygen ­species ­modulator ­12010100O12Rik, AI853864, P60603, gene:6706714literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway;
Small molecule transport		cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
Mrpl39mitochondrial ­ribosomal ­protein ­L39C21orf8, MRP, MRP-L5, ORF22, Rp, Rpml5, Q9JKF7, gene:2739314literature, APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Rhot2ras ­homolog ­family ­member ­T2Arh, Arht2, Mi, Miro2, Q8JZN7, gene:21495214literature, yeast mito homolog, mito protein domain+, induction, coexpressionMOMSignaling > Calcium homeostasis > EF hand proteins;
Mitochondrial dynamics and surveillance > Trafficking		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Higd1aHIG1 ­domain ­family, ­member ­1A2210020B17Rik, 7420700H20Rik, AI303276, AW049839, HIM, HIMP1, Hig, Hig1, Q9JLR9, gene:5629514literature, APEX_IMS, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly		all 14
Tbrg4transforming ­growth ­factor ­beta ­regulated ­gene ­42310042P22Rik, AA120735, AA408001, AI527316, Cp, Cpr2, R74877, Tb-12, Q91YM4, gene:2137914literature, APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		all 14
Apooapolipoprotein ­O0610008C08Rik, 1110019O03Rik, Mico, Micos26, Q9DCZ4, gene:6831614literature, APEX_IMS, targetP signal, mito protein domain+, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Pdp1pyruvate ­dehyrogenase ­phosphatase ­catalytic ­subunit ­1Gm1024, Ppm, Ppm2c, Q3UV70, gene:38151114literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dnajc15DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C151110003P16Rik, Dnaj, Dnajd1, Q78YY6, gene:6614814GFP, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorcerebrum, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Bcat2branched ­chain ­aminotransferase ­2, ­mitochondrialBcat(m), Bcat-, Bcat-2, Eca4, Eca40, O35855, gene:1203614literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismcerebrum, cerebellum, brainstem, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Abcd3ATP-binding ­cassette, ­sub-family ­D ­(ALD), ­member ­3AI313901, AU018866, AW146054, PMP, PMP68, PMP70, Pxm, Pxmp1, P55096, gene:1929914GFP, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpressionMembraneSmall molecule transport > ABC transporterskidney, liver, adipose, placenta, testis
Cps1carbamoyl-phosphate ­synthetase ­14732433M03Rik, C, CPS, D1Ucl, D1Ucla3, Q8C196, gene:22723114literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Urea cyclecerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Atp5mplATP ­synthase ­membrane ­subunit ­6.8PL2010107E04Rik, 9430003J03Rik, AU043134, AV124504, MLQ, Mp68, P56379, gene:7025714induction, coexpression++, MS/MS+MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
Oatornithine ­aminotransferaseAI194874, rh, rhg, P29758, gene:1824214literature, APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolismall 14
Hao2hydroxyacid ­oxidase ­2AI325478, Ha, Hao-2, Hao3, Haox3, Q9NYQ2, gene:5618514yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSunknownMetabolism > Lipid metabolismkidney, largeintestine, testis
Tha1threonine ­aldolase ­11300017K07Rik, GLY, GLY1, Q6XPS7, gene:7177614targetP signal+, mito protein domain+, MS/MS+Matrixnonekidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
Hadhbhydroxyacyl-CoA ­dehydrogenase ­trifunctional ­multienzyme ­complex ­subunit ­beta4930479F15Rik, Mtp, Mtpb, TP-beta, Q99JY0, gene:23108614literature, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > Lysine metabolism		all 14
Rdh14retinol ­dehydrogenase ­14 ­(all-trans ­and ­9-cis)3110030G19Rik, AW215439, P, PAN2, Q9ERI6, gene:10501414yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMembraneMetabolism > Vitamin metabolism > Vitamin A metabolismcerebrum, cerebellum, brainstem, spinalcord, smallintestine, largeintestine, stomach, placenta, testis
Fastkd1FAST ­kinase ­domains ­15330408N05Rik, mKIAA1800, Q6DI86, gene:32072014APEX_matrix, targetP signal, induction, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		liver, largeintestine
Car5bcarbonic ­anhydrase ­5b, ­mitochondrial7330410H16Rik, CA, CAVB, Ca5b, CarVb, D730005F19Rik, Q9QZA0, gene:5607814literature, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Urea cyclecerebellum, spinalcord, kidney, adipose, stomach, placenta, testis
Grpel2GrpE-like ­2, ­mitochondrialmt-GrpE, mt-GrpE#2, mt-Grpel2, O88396, gene:1771414literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+MatrixProtein import, sorting and homeostasis > Protein import and sorting > Import motor;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis		placenta
Mrps17mitochondrial ­ribosomal ­protein ­S171810006P02Rik, Mprs17, Q9CQE3, gene:6625814literature, targetP signal, mito protein domain, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Lipt1lipoyltransferase ­1EG623661, Q8VCM4, gene:62366114GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Lipoate insertionadipose, placenta
Slc25a44solute ­carrier ­family ­25, ­member ­446720482A19, B430110G05Rik, Q8BGF9, gene:22951714yeast mito homolog+, mito protein domain+, induction, MS/MSMIMMetabolism > Amino acid metabolism > BCAA metabolism;
Small molecule transport > SLC25A family		placenta
Dutdeoxyuridine ­triphosphatase5031412I06Rik, 5133400F09Rik, D2Bwg0749e, Dutp, dUTPase, Q8VCG1, gene:11007414literature, targetP signal+, Rickettsial homolog, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, spinalcord, liver, heart, adipose, largeintestine, stomach, placenta
Immp2lIMP2 ­inner ­mitochondrial ­membrane ­peptidase-like ­(S. ­cerevisiae)AI853880, IM, IMP2, Tg(HLA-A/H2-D)2Enge, Q8BPT6, gene:9375714literature, yeast mito homolog++, mito protein domain, coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		cerebellum, brainstem, liver, skeletalmuscle, adipose, largeintestine, testis
Cox19cytochrome ­c ­oxidase ­assembly ­protein ­191810074D02Rik, 2810437L13Rik, Q8K0C8, gene:6803313yeast mito homolog, mito protein domain, induction, coexpression+, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors		liver, placenta
Aldh1l2aldehyde ­dehydrogenase ­1 ­family, ­member ­L2D330038I09Rik, mtFDH, Q8K009, gene:21618813literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismbrainstem, spinalcord, liver, skeletalmuscle, smallintestine, largeintestine, stomach, placenta
Chchd2coiled-coil-helix-coiled-coil-helix ­domain ­containing ­2AL033347, Etoh, Etohi6, Q9D1L0, gene:1400413APEX_IMS, targetP signal+, yeast mito homolog+, mito protein domain, coexpressionIMSMitochondrial dynamics and surveillance > Apoptosisnone
Pisdphosphatidylserine ­decarboxylase9030221M09Rik, Q8BSF4, gene:32095113targetP signal, yeast mito homolog++, mito protein domain, MS/MSMIMMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Crotcarnitine ­O-octanoyltransferase1200003H03Rik, Q9DC50, gene:7411413yeast mito homolog+, mito protein domain, induction, coexpression, MS/MSunknownMetabolism > Lipid metabolism > Fatty acid oxidationkidney, liver
Noa1nitric ­oxide ­associated ­12610024G14Rik, AU022345, AtNOS1, mAt, mAtNOS1, Q9JJG9, gene:5641213literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		adipose, largeintestine
Ndufaf8NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­81810043H04Rik, A2AMZ4, gene:20850113targetP signal, induction, coexpression+, MS/MSIMSOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		adipose, stomach
Acaa1bacetyl-Coenzyme ­A ­acyltransferase ­1BQ8VCH0, gene:23567413targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Lipid metabolismkidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtrf1lmitochondrial ­translational ­release ­factor ­1-like9130004K12Rik, Q8BJU9, gene:10885313literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Translation factorstestis
Atp23ATP23 ­metallopeptidase ­and ­ATP ­synthase ­assembly ­factor ­homolog1110068E08Rik, 2410012H02Rik, Xrcc6b, Xrcc6bp1, Q9CWQ3, gene:6887613yeast mito homolog++, mito protein domain+, coexpressionIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebellum
Yme1l1YME1-like ­1 ­(S. ­cerevisiae)Fts, FtsH1, Ftsh, O88967, gene:2737713literature, APEX_IMS, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hdhd5haloacid ­dehalogenase ­like ­hydrolase ­domain ­containing ­5A930002G03Rik, Cecr, Cecr5, Q91WM2, gene:21493213APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++Matrixnonecerebellum, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Aldh7a1aldehyde ­dehydrogenase ­family ­7, ­member ­A1Atq, Atq1, D18Wsu181, D18Wsu181e, Q9DBF1, gene:11069513literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Chchd7coiled-coil-helix-coiled-coil-helix ­domain ­containing ­71810049H20Rik, Q8K2Q5, gene:6643313yeast mito homolog, induction, coexpression, MS/MS+IMSMetabolism > Metals and cofactors > Copper metabolismcerebrum, smallintestine, placenta, testis
Pdprpyruvate ­dehydrogenase ­phosphatase ­regulatory ­subunit4930402E16Rik, AU018056, mKIAA1990, Q7TSQ8, gene:31951813APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Nlnneurolysin ­(metallopeptidase ­M3 ­family)4930472G13Rik, C79345, Q91YP2, gene:7580513literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufaf2NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­21810058I14Rik, C86051, Ndufa, Ndufa12l, mim, mimitin, Q59J78, gene:7559713literature, APEX_matrix, targetP signal, induction, coexpression, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Fastkd2FAST ­kinase ­domains ­22810421I24Rik, Q922E6, gene:7561913literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Dcakddephospho-CoA ­kinase ­domain ­containing3010024O21Rik, 6720485C15Rik, AI849483, Q8BHC4, gene:6808713GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMembranenoneall 14
Sdr39u1short ­chain ­dehydrogenase/reductase ­family ­39U, ­member ­12310014G06Rik, Q5M8N4, gene:65479513targetP signal, mito protein domain, coexpression, MS/MS++unknownnonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Garsglycyl-tRNA ­synthetaseGENA202, Gars1, Gena2, Gena201, Nmf249, Sgr, Sgrp23, Q9CZD3, gene:35317213targetP signal+, yeast mito homolog, mito protein domain, inductionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Uqcr11ubiquinol-cytochrome ­c ­reductase, ­complex ­III ­subunit ­XI0710008D09Rik, AL022707, Uqc, Uqcr, Q9CPX8, gene:6659413literature, targetP signal, mito protein domain+, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, stomach, placenta, testis
Ears2glutamyl-tRNA ­synthetase ­2, ­mitochondrial3230401I01Rik, mKIAA1970, Q9CXJ1, gene:6741713literature, APEX_matrix, GFP, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesadipose, largeintestine, placenta
Cox6b2cytochrome ­c ­oxidase ­subunit ­6B21700067P11Rik, BC048670, COXV, COXVIB2, Q80ZN9, gene:33318213literature, yeast mito homolog+, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		testis
Timm10btranslocase ­of ­inner ­mitochondrial ­membrane ­10BFxc1, Tim10, Tim10b, Tim9, Tim9b, Q9WV96, gene:1435613literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, largeintestine, stomach, placenta, testis
Atpaf1ATP ­synthase ­mitochondrial ­F1 ­complex ­assembly ­factor ­16330547J17Rik, AI593252, ATP, ATP11, ATP11p, H3BLL2, gene:23064913literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MSMatrixOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, brainstem, spinalcord, adipose, smallintestine, largeintestine, placenta, testis
Sfxn3sideroflexin ­3Q91V61, gene:9428013yeast mito homolog, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > Sideroflexins		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Abcd2ATP-binding ­cassette, ­sub-family ­D ­(ALD), ­member ­2A, ABC3, ABC39, AL, ALDL1, ALDR, ALDRP, Q61285, gene:2687413targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MembraneSmall molecule transport > ABC transportersadipose
Sqorsulfide ­quinone ­oxidoreductase0610039J17Rik, 4930557M22Rik, Sq, Sqrdl, Q9R112, gene:5901013literature, targetP signal+, mito protein domain, MS/MS++MIMMetabolism > Electron carriers > Q-linked reactions, other;
Metabolism > Sulfur metabolism		spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sirt5sirtuin ­50610012J09Rik, 1500032M05Rik, AV001953, Q8K2C6, gene:6834613literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, brainstem, spinalcord, liver, heart, adipose, largeintestine, stomach
Nudt13nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­134933433B15Rik, Q8JZU0, gene:6772513GFP, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebellum, brainstem, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Acad11acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­115730439E10Rik, AI987948, Q80XL6, gene:10263213mito protein domain+, induction, coexpressionMIMMetabolism > Lipid metabolism > Fatty acid oxidationspinalcord, kidney, liver, adipose
Ppoxprotoporphyrinogen ­oxidasePpo, P51175, gene:1904413literature, APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Heme synthesis and processingcerebrum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
D2hgdhD-2-hydroxyglutarate ­dehydrogenaseAA408776, AA408778, AI325464, Q8CIM3, gene:9831413literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domainMatrixMetabolism > Carbohydrate metabolism > TCA-associatedadipose, largeintestine
Diablodiablo, ­IAP-binding ­mitochondrial ­protein0610041G12Rik, 1700006L01Rik, AU040403, Sm, Smac, Q9JIQ3, gene:6659313literature, APEX_IMS, targetP signal+, mito protein domain+, MS/MSIMSMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a45solute ­carrier ­family ­25, ­member ­45AW491445, Q8CFJ7, gene:10737513yeast mito homolog, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A familyliver, adipose, smallintestine, stomach, placenta, testis
Ttc19tetratricopeptide ­repeat ­domain ­192010204O13Rik, 2810460C24Rik, AI505442, Q8CC21, gene:7279512literature, APEX_IMS, targetP signal+, mito protein domain, induction, MS/MS+MIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, spinalcord, adipose, largeintestine, stomach, testis
Agxtalanine-glyoxylate ­aminotransferaseAGT, Agt1, Agxt1, SPT, O35423, gene:1161112literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Amino acid metabolism > Glyoxylate metabolism		liver
DglucyD-glutamate ­cyclase9030617O03Rik, Q8BH86, gene:21783012literature, APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolismall 14
Mtfmtmitochondrial ­methionyl-tRNA ­formyltransferase2310020P08Rik, Q9D799, gene:6960612literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > fMet processing;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		none
mt-Co1cytochrome ­c ­oxidase ­subunit ­ICoxI, P00397, gene:1770812literature, APEX_IMS, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV subunits;
Metabolism > Metals and cofactors > Heme-containing proteins;
OXPHOS > OXPHOS subunits		all 14
Endogendonuclease ­GO08600, gene:1380412literature, APEX_IMS, yeast mito homolog, mito protein domain, coexpression++, MS/MSIMSMitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial dynamics and surveillance > Apoptosis		all 14
Fam162afamily ­with ­sequence ­similarity ­162, ­member ­A2310056P07Rik, HGTD-P, Q9D6U8, gene:7018612APEX_IMS, APEX_matrix, targetP signal, induction, coexpression, MS/MS++MIMnoneall 14
Atp5j2ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­F21110019H14Rik, Atp5mf, P56135, gene:5742312literature, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Gls2glutaminase ­2 ­(liver, ­mitochondrial)A330074B06Rik, AI195532, GA, GLS, L, Lga, Q571F8, gene:21645612targetP signal, mito protein domain+, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, smallintestine, largeintestine
Timmdc1translocase ­of ­inner ­mitochondrial ­membrane ­domain ­containing ­12810021C21Rik, 4930455C21Rik, AV135763, Q8BUY5, gene:7691612literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps33mitochondrial ­ribosomal ­protein ­S33AI841153, CGI-13, CGI-139, Gda, Gdap3, MRP-, MRP-S33, PTD00, PTD003, Q9D2R8, gene:1454812literature, targetP signal, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tfamtranscription ­factor ­A, ­mitochondrialAI661103, Hmgt, Hmgts, mtTF, mtTFA, tsHM, tsHMG, P40630, gene:2178012literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription		all 14
EcsitECSIT ­signalling ­integratorSit, Sitpec, Q9QZH6, gene:2694012literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrs2MRS2 ­magnesium ­transporterGm902, HPT, Mr, Mrs2l, RPT, Q5NCE8, gene:38083612APEX_matrix, GFP, targetP signal, yeast mito homolog++, coexpressionMIMSmall molecule transport;
Signaling		cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, smallintestine, largeintestine, stomach, placenta, testis
Abcb6ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­61200005B17Rik, Q9DC29, gene:7410412literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMOMMetabolism > Metals and cofactors > Heme synthesis and processing;
Small molecule transport > ABC transporters		cerebrum, brainstem, liver, largeintestine, stomach, placenta, testis
Mtfr1lmitochondrial ­fission ­regulator ­1-like2410166I05Rik, AI480750, Fam54, Fam54b, Q9CWE0, gene:7682412mito protein domain+, induction, coexpression, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, placenta, testis
Lap3leucine ­aminopeptidase ­32410015L10Rik, AA410100, LAP-3, Lap, Lapep, Pe, Pep, Pep-7, Pep-S, Pep7, Peps, Q9CPY7, gene:6698812APEX_matrix, targetP signal, Rickettsial homolog, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Acsf2acyl-CoA ­synthetase ­family ­member ­2Q8VCW8, gene:26489512APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Gpt2glutamic ­pyruvate ­transaminase ­(alanine ­aminotransferase) ­24631422C05Rik, AL, ALT2, AU014768, AU041193, C87201, Q8BGT5, gene:10868212APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolismcerebrum, brainstem, liver, skeletalmuscle, adipose, stomach, placenta, testis
Grhprglyoxylate ­reductase/hydroxypyruvate ­reductase1110059D05Rik, 6430629L09Rik, Glxr, Q91Z53, gene:7623812APEX_matrix, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glyoxylate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
StomstomatinEpb7., Epb7.2, sto, P54116, gene:1383012yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSMembranenoneadipose, placenta, testis
Glod4glyoxalase ­domain ­containing ­41700082G03Rik, 2700085E05Rik, C81254, Q9CPV4, gene:6720112APEX_matrix, targetP signal, coexpression, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm6translocase ­of ­outer ­mitochondrial ­membrane ­61110002E23Rik, AI663970, Q9CQN3, gene:6611912GFP, mito protein domain+, coexpression, MS/MS+MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps36mitochondrial ­ribosomal ­protein ­S361110018B13Rik, S36mt, Q9CQX8, gene:6612812literature, APEX_matrix, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome;
Metabolism > Carbohydrate metabolism > TCA cycle		all 14
Tmem65transmembrane ­protein ­652610029O13Rik, 4930438D12Rik, Q4VAE3, gene:7486812literature, APEX_matrix, targetP signal, coexpression, MS/MS++MIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm70atranslocase ­of ­outer ­mitochondrial ­membrane ­70A2610044B22Rik, D16Ium2, D16Ium22, D16Ium22e, D16Wsu109, D16Wsu109e, Tom7, Tom70, Tomm7, Tomm70, mKIAA0719, Q9CZW5, gene:2818512literature, yeast mito homolog+, mito protein domain, induction, coexpressionMOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Fhitfragile ­histidine ­triad ­geneAW045638, Fra1, Fra14A2, O89106, gene:1419812targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Osgepl1O-sialoglycoprotein ­endopeptidase-like ­12610001M19Rik, AA416452, Q6PEB4, gene:7208512APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Crls1cardiolipin ­synthase ­10610009I22Rik, 4930557M15Rik, 5730490M08Rik, Q80ZM8, gene:6658612literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cardiolipin synthesisnone
Mocs1molybdenum ­cofactor ­synthesis ­13110045D15Rik, AI043170, AW536397, Q5RKZ7, gene:5673812APEX_matrix, targetP signal, mito protein domain+, MS/MS+MatrixMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteinscerebrum, liver, adipose, smallintestine, largeintestine, stomach, placenta
Aldh1l1aldehyde ­dehydrogenase ­1 ­family, ­member ­L11810048F20Rik, FDH, Fthfd, Neut2, Q8R0Y6, gene:10774712APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, liver, smallintestine, largeintestine, stomach, placenta, testis
Rfkriboflavin ­kinase0610038L10Rik, AF031381, KOI-4, fla, Q8CFV9, gene:5439112targetP signal, yeast mito homolog++, MS/MSMatrixMetabolism > Vitamin metabolism > Vitamin B2 metabolismbrainstem, spinalcord, kidney, adipose, smallintestine, largeintestine
Dhrs1dehydrogenase/reductase ­(SDR ­family) ­member ­11110029G07Rik, AW112170, D14Ertd484e, Q99L04, gene:5258512targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Polgpolymerase ­(DNA ­directed), ­gammaAA409516, P, PolgA, Q3UG70, gene:1897512literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair		cerebrum, cerebellum, spinalcord, liver, adipose, largeintestine, placenta, testis
Prelid3aPRELI ­domain ­containing ­3AA230074A19Rik, BC019561, Sl, Slmo1, Q8VE85, gene:22565511yeast mito homolog+, mito protein domain+, MS/MSIMSMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebrum, cerebellum, spinalcord
Timm8a2translocase ­of ­inner ­mitochondrial ­membrane ­8A2Q4FZG7, gene:22326211literature, yeast mito homolog+, mito protein domain+, MS/MSIMSProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		all 14
Slc25a14solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­brain), ­member ­14BMCP, BMCP1, UCP, UCP5, UCP5L, UCP5S, Q9Z2B2, gene:2052311literature, yeast mito homolog+, mito protein domain+, MS/MSMIMMetabolism > Sulfur metabolism;
Small molecule transport > SLC25A family		cerebrum, cerebellum, brainstem, placenta, testis
Rhot1ras ­homolog ­family ­member ­T12210403N23Rik, AA415293, AF244542, AI834919, Arh, Arht1, C430039G08Rik, Mi, Miro1, Q8BG51, gene:5904011literature, targetP signal, yeast mito homolog, mito protein domain+, MS/MS+MOMSignaling > Calcium homeostasis > EF hand proteins;
Mitochondrial dynamics and surveillance > Trafficking		all 14
Gpx1glutathione ­peroxidase ­1AI195024, AL033363, CGP, CGPx, GPx-, GPx-1, GSHPx, GSHPx-1, Gp, Gpx, P11352, gene:1477511literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a46solute ­carrier ­family ­25, ­member ­461200007B05Rik, AI325987, Q9CQS4, gene:6745311yeast mito homolog+, mito protein domain+, inductionMOMSmall molecule transport > SLC25A family;
Mitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions		cerebrum, spinalcord, adipose, placenta
mt-Nd5NADH ­dehydrogenase ­subunit ­5P03921, gene:1772111literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
mt-Nd4NADH ­dehydrogenase ­subunit ­4P03911, gene:1771911literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
mt-Nd2NADH ­dehydrogenase ­subunit ­2P03893, gene:1771711literature, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Prelid1PRELI ­domain ­containing ­12610524G07Rik, Preli, Q8R107, gene:6649411literature, APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+IMSMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		none
Tstd3thiosulfate ­sulfurtransferase ­(rhodanese)-like ­domain ­containing ­32610029I01Rik, Q9D0B5, gene:7703211targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a32solute ­carrier ­family ­25, ­member ­322610043O12Rik, Mftc, Q8BMG8, gene:6990611literature, targetP signal, yeast mito homolog+, mito protein domain+MIMMetabolism > Vitamin metabolism > Vitamin B2 metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > SLC25A family		adipose, placenta
Mcumitochondrial ­calcium ­uniporter2010012O16Rik, AV064928, C10orf42, Ccdc109, Ccdc109a, D130073L02Rik, Gm64, Q3UMR5, gene:21599911literature, GFP, targetP signal, mito protein domain+, MS/MS++MIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > Calcium uniporter		cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Nipsnap1nipsnap ­homolog ­1O55125, gene:1808211APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		all 14
Pus1pseudouridine ­synthase ­1A730013B20Rik, MPU, MPUS1, mPus1p, Q9WU56, gene:5636111APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications		none
Pdp2pyruvate ­dehyrogenase ­phosphatase ­catalytic ­subunit ­24833426J09Rik, Gm1705, mKIAA1348, Q504M2, gene:38205111APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpressionMatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismadipose
Lypla1lysophospholipase ­1APT-1, Gm39587, LPL-I, P, Pla1a, P97823, gene:1877711Rickettsial homolog, mito protein domain, coexpression, MS/MS++unknownMetabolism > Lipid metabolism;
Signaling		all 14
Mthfd2lmethylenetetrahydrofolate ­dehydrogenase ­(NADP+ ­dependent) ­2-like1110019K23Rik, C630010D07Rik, D3YZG8, gene:66556311literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismspinalcord, placenta
Mtrf1mitochondrial ­translational ­release ­factor ­1A830062K05Rik, MtRF-1, Q8K126, gene:21125311literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Translation factorsadipose
Coq8bcoenzyme ­Q8B0610012P18Rik, Adck, Adck4, E9QLB8, gene:7688911APEX_matrix, GFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMMetabolism > Metals and cofactors > Coenzyme Q metabolismadipose, smallintestine, largeintestine, placenta
Hemk1HemK ­methyltransferase ­family ­member ­12310008M14Rik, AW049265, Q921L7, gene:6953611GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+MatrixMitochondrial central dogma > Translation > Translation factorsnone
Akr7a5aldo-keto ­reductase ­family ­7, ­member ­A5 ­(aflatoxin ­aldehyde ­reductase)0610025K21Rik, A, Afar, Afar1, Akr7a2, Q8CG76, gene:11019811APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism;
Metabolism > Detoxification > Xenobiotic metabolism		all 14
Cyp27a1cytochrome ­P450, ­family ­27, ­subfamily ­a, ­polypeptide ­11300013A03Rik, Cyp2, Cyp27, Q9DBG1, gene:10408611literature, targetP signal+, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme-containing proteins		kidney, liver, skeletalmuscle, adipose, smallintestine, placenta, testis
Oxct2a3-oxoacid ­CoA ­transferase ­2AOxct, Oxct2, Scot, Scot-, Scot-t1, Q9JJN4, gene:6405911targetP signal+, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolismtestis
Mrpl52mitochondrial ­ribosomal ­protein ­L521110047B07Rik, Q9D0Y8, gene:6883611literature, APEX_matrix, targetP signal+, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Fis1fission, ­mitochondrial ­12010003O14Rik, Ttc11, Q9CQ92, gene:6643711literature, yeast mito homolog++, mito protein domain+MOMMitochondrial dynamics and surveillance > Fissionall 14
AmtaminomethyltransferaseEG434437, GCVT, Q8CFA2, gene:43443711targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		cerebrum, brainstem, spinalcord, kidney, liver, largeintestine, stomach, placenta
Exogendo/exonuclease ­(5'-3'), ­endonuclease ­G-likeAW557704, ENDO, ENG, ENGL-B, ENGL-a, Endogl1, Endogl2, Engl, Engla, Englb, Q8C163, gene:20819411APEX_IMS, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MIMMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair;
Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay		cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta
Mpstmercaptopyruvate ­sulfurtransferaseMst, Q3UW66, gene:24622111APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MIMMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Sulfur metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pnpopyridoxine ­5'-phosphate ­oxidaseAI415282, Q91XF0, gene:10371111APEX_matrix, targetP signal, yeast mito homolog++, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Vitamin B6 metabolismbrainstem, liver
Mpv17l2MPV17 ­mitochondrial ­membrane ­protein-like ­2Fksg2, Fksg24, Q8VIK2, gene:23438411GFP, targetP signal, yeast mito homolog+, mito protein domain, coexpressionMIMMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, placenta
Fundc2FUN14 ­domain ­containing ­24833415N24Rik, DC44, HCBP, HCBP6, Q9D6K8, gene:6739111mito protein domain+, MS/MS++MOMMitochondrial dynamics and surveillance > Organelle contact sites;
Signaling		cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl18mitochondrial ­ribosomal ­protein ­L181010001C05Rik, C79879, HSPC0, HSPC071, MRP-, MRP-L18, Q9CQL5, gene:6768111literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Atp5g2ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­C2 ­(subunit ­9)1810041M08Rik, Atp5mc2, P56383, gene:6794211literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		none
Mettl5methyltransferase ­like ­52810410A08Rik, Q8K1A0, gene:7542211Rickettsial homolog, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modificationsnone
Slc25a38solute ­carrier ­family ­25, ­member ­38AV019094, BC010801, a, appoptosin, Q91XD8, gene:20863811yeast mito homolog++, mito protein domain+, coexpressionMIMMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > SLC25A family		none
Slc25a36solute ­carrier ­family ­25, ­member ­36C330005L02Rik, Q922G0, gene:19228711GFP, yeast mito homolog+, mito protein domain+, coexpressionMIMMetabolism > Nucleotide metabolism > Nucleotide import;
Small molecule transport > SLC25A family		brainstem, spinalcord, placenta, testis
Trmt2bTRM2 ­tRNA ­methyltransferase ­2B4732479N06Rik, Q8BQJ6, gene:21520111GFP, targetP signal, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications		none
Abat4-aminobutyrate ­aminotransferase9630038C02Rik, AI255750, GABA, Gabaat, Gabat, Gm9851, I54, Laibat, X61497, P61922, gene:26886011literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism;
Metabolism > Metals and cofactors > Fe-S-containing proteins		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aldh5a1aldhehyde ­dehydrogenase ­family ­5, ­subfamily ­A16330403E24Rik, Ahd-1, Ahd1, D630032B01Rik, SS, SSADH, Ssdh1, Q8BWF0, gene:21457911APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolismall 14
Got2glutamatic-oxaloacetic ­transaminase ­2, ­mitochondrialAL022787, FABP, FABP-pm, Got-2, Kyat, Kyat4, mA, mAspAT, P05202, gene:1471911literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Amino acid metabolism > Glutamate metabolism;
Metabolism > Amino acid metabolism > Glyoxylate metabolism;
Metabolism > Amino acid metabolism > Kynurenine metabolism;
Metabolism > Sulfur metabolism		all 14
Ckmt1creatine ­kinase, ­mitochondrial ­1, ­ubiquitousMt-CK, ScCKmit, U-MtCK, UbCKmi, UbCKmit, mi-C, mi-CK, mia-CK, P30275, gene:1271611literature, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Nucleotide metabolism > Creatine metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Gtpbp3GTP ­binding ­protein ­32410009F13Rik, AI607903, Gtpb, Q923K4, gene:7035911literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		largeintestine
Sirt3sirtuin ­32310003L23Rik, AI848213, Si, Sir2l3, Q8R104, gene:6438411literature, APEX_matrix, mito protein domain, induction, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism;
Signaling		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
C330018D20RikRIKEN ­cDNA ­C330018D20 ­geneAU018666, Q9CWB7, gene:7742211targetP signal, coexpression+, MS/MSMatrixnonecerebrum, cerebellum, spinalcord, liver, heart, skeletalmuscle, adipose, placenta, testis
Parlpresenilin ­associated, ­rhomboid-likeD16Ertd607, D16Ertd607e, P, PRO2, PRO2207, PS, PSARL1, PSENIP2, Psarl, Q5XJY4, gene:38103811literature, targetP signal, yeast mito homolog++, mito protein domain, MS/MSMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bloc1s1biogenesis ­of ­lysosomal ­organelles ­complex-1, ­subunit ­1AI839753, BL, BLOS1, Gcn5, Gcn5l1, O55102, gene:1453310mito protein domain, coexpression++, MS/MSunknownSignalingplacenta, testis
Cox8ccytochrome ­c ­oxidase ­subunit ­8C1700007F21Rik, COX8-, COX8-3, COXV, COXVIII-3, A6H666, gene:7548310literature, targetP signal, mito protein domain+, MS/MSMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		testis
AclyATP ­citrate ­lyaseA730098H14Rik, AW538652, Q91V92, gene:10411210APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Sfxn5sideroflexin ­5C230001H08Rik, Q925N0, gene:9428210literature, yeast mito homolog, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport > Sideroflexins		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine
Slc25a40solute ­carrier ­family ­25, ­member ­40B230315F11Rik, Q8BGP6, gene:31965310literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Slc25a27solute ­carrier ­family ­25, ­member ­273632410G24Rik, 9430092A03Rik, D530043E16Rik, Ucp, Ucp4, Q9D6D0, gene:7401110literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord
Slc25a23solute ­carrier ­family ­25 ­(mitochondrial ­carrier; ­phosphate ­carrier), ­member ­232310067G05Rik, SCaMC, SCaMC-3, Q6GQS1, gene:6697210literature, yeast mito homolog+, mito protein domain+, MS/MSMIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family		cerebrum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta
Ucp3uncoupling ­protein ­3 ­(mitochondrial, ­proton ­carrier)AI645527, Slc2, Slc25a9, UCP-, UCP-3, P56501, gene:2222910literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A familyspinalcord, heart, skeletalmuscle, adipose
Htra2HtrA ­serine ­peptidase ­2AI481710, Htr, O, Omi, Pr, Prss25, mnd, mnd2, Q9JIY5, gene:6470410literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Apoptosis		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nadk2NAD ­kinase ­2, ­mitochondrialMNA, MNADK, Nadk, Nadkd1, Q8C5H8, gene:6864610APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
mt-Cytbcytochrome ­bP00158, gene:1771110literature, yeast mito homolog++, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex III > CIII subunits;
Metabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits		all 14
Chchd5coiled-coil-helix-coiled-coil-helix ­domain ­containing ­51110027L01Rik, AW045710, Q9CQP3, gene:6617010APEX_IMS, yeast mito homolog++, coexpression, MS/MSIMSnoneadipose, placenta, testis
Mrps31mitochondrial ­ribosomal ­protein ­S311500002D03Rik, AA960481, Imoge, Imogen38, Imogen44, Q61733, gene:5731210literature, APEX_matrix, targetP signal, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufa1NADH:ubiquinone ­oxidoreductase ­subunit ­A11810049F12Rik, MWFE, O35683, gene:5440510literature, coexpression+, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Hoga14-hydroxy-2-oxoglutarate ­aldolase ­10610010D20Rik, Dhd, Dhdpsl, N, Npl2, Q9DCU9, gene:6743210GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Amino acid metabolism > Glyoxylate metabolismkidney, liver, adipose, largeintestine, placenta, testis
Aldh3a2aldehyde ­dehydrogenase ­family ­3, ­subfamily ­A2AI194803, Ahd, Ahd-, Ahd-3, Ahd-3r, Ahd3, Ahd3-r, Ald, Aldh, Aldh4, Aldh4-r, FAL, FALDH, P47740, gene:1167110targetP signal+, yeast mito homolog, mito protein domain, coexpressionMembraneMetabolism > Detoxification > ROS and glutathione metabolismspinalcord, kidney, liver, smallintestine, largeintestine, stomach, placenta, testis
Pam16presequence ­translocase-asssociated ­motor ­16 ­homolog ­(S. ­cerevisiae)2010110I09Rik, AV006767, CGI-13, CGI-136, Mag, Magmas, Tim1, Tim16, Timm16, Q9CQV1, gene:6644910literature, APEX_matrix, targetP signal, yeast mito homolog, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorall 14
Tomm5translocase ­of ­outer ­mitochondrial ­membrane ­51110019J04Rik, Tom5, B1AXP6, gene:6851210literature, mito protein domain+, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufb4NADH:ubiquinone ­oxidoreductase ­subunit ­B40610006N12Rik, 1300010H20Rik, Q9CQC7, gene:6819410literature, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Fam136afamily ­with ­sequence ­similarity ­136, ­member ­A2010309E21Rik, AW124904, Hyccin, Q9CR98, gene:6648810APEX_IMS, mito protein domain+, MS/MS++IMSnoneall 14
Mpv17lMpv17 ­transgene, ­kidney ­disease ­mutant-likeM-, M-LP, Q99MS3, gene:9373410yeast mito homolog+, mito protein domain, MS/MS++MIMSmall molecule transportcerebrum, cerebellum, brainstem, spinalcord, kidney, liver
Gykl1glycerol ­kinase-like ­1AI449806, Gk-r, Gk-rs1, Q8C635, gene:1462510yeast mito homolog+, mito protein domain, MS/MS++Membranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, smallintestine, testis
Cpt1bcarnitine ­palmitoyltransferase ­1b, ­muscleCpt, Cpt1, Cpt1-m, Cpti, Cpti-m, M-CP, M-cpti, Q924X2, gene:1289510literature, yeast mito homolog+, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle		cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Akr1b10aldo-keto ­reductase ­family ­1, ­member ­B10 ­(aldose ­reductase)2310005E10Rik, Akr1b16, G5E895, gene:6786110induction, coexpression, MS/MS++unknownMetabolism > Vitamin metabolism > Vitamin A metabolism;
Metabolism > Detoxification > Xenobiotic metabolism		cerebrum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a2solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­ornithine ­transporter) ­member ­2Or, Ornt2, Q99ML6, gene:8388510literature, yeast mito homolog++, mito protein domain+MIMMetabolism > Amino acid metabolism > Urea cycle;
Small molecule transport > SLC25A family		testis
Slc25a53solute ­carrier ­family ­25, ­member ­532310046F18Rik, 2810402A17Rik, AI448995, AI841128, Mcar, Mcart6, A2AF28, gene:6706210yeast mito homolog++, mito protein domain+MIMSmall molecule transport > SLC25A familytestis
Opa3optic ­atrophy ­3D630048P19Rik, Gm1425, Gm472, Q505D7, gene:40318710literature, targetP signal, coexpression, MS/MS++MOMnoneall 14
Fahd1fumarylacetoacetate ­hydrolase ­domain ­containing ­11110025H10Rik, AV002085, Q8R0F8, gene:6863610literature, APEX_matrix, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedall 14
Pxmp4peroxisomal ­membrane ­protein ­43010018P03Rik, Pmp24, Q9JJW0, gene:5903810targetP signal, mito protein domain+, coexpressionunknownnonekidney, liver, adipose
Nif3l1Ngg1 ­interacting ­factor ­3-like ­1 ­(S. ­pombe)1110030G24Rik, Q9EQ80, gene:6510210APEX_matrix, targetP signal, yeast mito homolog, coexpression, MS/MS+Matrixnonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
Grsf1G-rich ­RNA ­sequence ­binding ­factor ­1BB232551, C80280, D5Wsu31, D5Wsu31e, Q8C5Q4, gene:23141310APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		adipose, smallintestine, largeintestine, stomach, placenta, testis
Macrod1mono-ADP ­ribosylhydrolase ­1AI604841, AW743046, D930010J01Rik, Lrp16, Q922B1, gene:10722710APEX_matrix, targetP signal, coexpression, MS/MS++MatrixSignalingcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cisd3CDGSH ­iron ­sulfur ­domain ­3Mel-13, Mel1, Mel13, B1AR13, gene:21714910APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		all 14
Nmnat3nicotinamide ­nucleotide ­adenylyltransferase ­34933408N02Rik, PN, PNAT3, Q99JR6, gene:7408010literature, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Nudt8nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­82310039H17Rik, Q9CR24, gene:6638710APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Coenzyme A metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Catcatalase2210418N07, Ca, Cas, Cas-1, Cas1, Cs-, Cs-1, P24270, gene:1235910yeast mito homolog++, mito protein domain, coexpressionIMSMetabolism > Detoxification > ROS and glutathione metabolismspinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dnajc19DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C191810055D05Rik, AA959924, Tim14, Q9CQV7, gene:6771310literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorall 14
Elac2elaC ­ribonuclease ­Z ­21110017O07Rik, D11Wsu80, D11Wsu80e, Hpc2, Q80Y81, gene:6862610APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processingcerebellum, skeletalmuscle, adipose, largeintestine, stomach
Sugctsuccinyl-CoA ­glutarate-CoA ­transferase5033411D12Rik, D17907, Q7TNE1, gene:19213610APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Amino acid metabolismkidney, liver, testis
Hint3histidine ­triad ­nucleotide ­binding ­protein ­30610010I17Rik, AV009015, HIN, HINT-3, HINT-4, HINT4, Q9CPS6, gene:6684710Rickettsial homolog, mito protein domain, induction, coexpression+unknownnonebrainstem, heart, skeletalmuscle
Karslysyl-tRNA ­synthetaseAA589550, AL024334, AL033315, AL033367, D8Ertd698, D8Ertd698e, D8Wsu108, D8Wsu108e, Kars1, L, LysRS, mKIAA0070, Q99MN1, gene:8530510literature, GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Dnajc28DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C28BC020175, ORF28, Q8VCE1, gene:24673810targetP signal, Rickettsial homolog, mito protein domain, coexpression+unknownnonestomach
Cyb5bcytochrome ­b5 ­type ­B1810044O22Rik, AU015618, Cyb5m, Q9CQX2, gene:6642710literature, mito protein domain, coexpression, MS/MS++MOMMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex;
Metabolism > Electron carriers > Cytochromes		all 14
Nudt2nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­22310051L06Rik, AA939917, AP, APAH1, P56380, gene:6640110mito protein domain, coexpression, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
Phyhphytanoyl-CoA ­hydroxylaseAI256161, AI265699, L, Lnap1, PAHX, O35386, gene:1692210targetP signal, induction, MS/MS++MatrixMetabolism > Lipid metabolismkidney, liver, smallintestine
Guk1guanylate ­kinase ­1AA409738, AL033299, AL033300, AV026611, Gmk, Guk-1, Q64520, gene:149239APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach
Nudt19nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­19D7R, D7Rp, D7Rp2, D7Rp2-r, D7Rp2-s, D7Rp2e, RP, RP2-r, RP2-s, P11930, gene:1109599APEX_matrix, targetP signal+, mito protein domain, inductionMatrixMetabolism > Metals and cofactors > Coenzyme A metabolismkidney, liver, largeintestine, placenta
mt-Co3cytochrome ­c ­oxidase ­subunit ­IIIP00416, gene:177109literature, yeast mito homolog++, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits		all 14
Mrpl42mitochondrial ­ribosomal ­protein ­L422700009F22Rik, 2900055D03Rik, D10Ertd322, D10Ertd322e, HSPC2, HSPC204, L31mt, L42mt, MRP-, MRP-L31, MRP-L42, MRP-S32, PTD00, PTD007, Rpm, Rpml31, S32mt, Q9CPV3, gene:672709APEX_matrix, GFP, mito protein domain+, induction, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeliver, adipose, largeintestine, testis
Dhrs7bdehydrogenase/reductase ­(SDR ­family) ­member ­7BBC003479, C79874, C80074, PexRAP, Q99J47, gene:2168209Rickettsial homolog, mito protein domain, induction, coexpressionMembranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nt5m5',3'-nucleotidase, ­mitochondrial2010013E09Rik, AI846937, dNT-, dNT-2, Q8VCE6, gene:1038509literature, targetP signal, mito protein domain, induction, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, testis
Mthfsl5, ­10-methenyltetrahydrofolate ­synthetase-likeGm2382, L7N466, gene:1000397079targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta
Mthfs5, ­10-methenyltetrahydrofolate ­synthetase1110034I12Rik, 2310020H23Rik, AI119695, Q9D110, gene:1078859targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta
Nme4NME/NM23 ­nucleoside ­diphosphate ­kinase ­42610027N22Rik, 2810024O08Rik, 5730493H09Rik, NM23-M, NM23-M4, Nm23M4, Q9WV84, gene:565209APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMIMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingadipose, largeintestine, placenta, testis
Oma1OMA1 ­zinc ­metallopeptidase2010001O09Rik, MPRP-1, ZMPOMA1, Q9D8H7, gene:670139APEX_IMS, GFP, targetP signal, yeast mito homolog++, coexpressionMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Fission		skeletalmuscle, adipose, largeintestine
Acsl6acyl-CoA ­synthetase ­long-chain ­family ­member ­6A330035H04Rik, AW050338, Fac, Facl6, L, LACS, Lacsl, mKIAA0837, Q91WC3, gene:2167399yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, testis
Rpusd3RNA ­pseudouridylate ­synthase ­domain ­containing ­3AI527266, Q14AI6, gene:1011229APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications		largeintestine
Acss1acyl-CoA ­synthetase ­short-chain ­family ­member ­11110032O15Rik, AI788978, Ac, Acas2, Acas2l, AceC, AceCS2, Q99NB1, gene:687389literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dguokdeoxyguanosine ­kinasedGK, dGK1, dGK2, dGK3, Q9QX60, gene:273699literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pars2prolyl-tRNA ­synthetase ­(mitochondrial)(putative)BC027073, Q8CFI5, gene:2305779APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasessmallintestine, largeintestine, stomach
Htatip2HIV-1 ­Tat ­interactive ­protein ­2AW111545, Cc3, TIP, Tip30, Q9Z2G9, gene:534159yeast mito homolog, mito protein domain+, MS/MSMembranenonecerebrum, cerebellum, brainstem, liver, adipose, placenta, testis
Qrsl1glutaminyl-tRNA ­synthase ­(glutamine-hydrolyzing)-like ­12700038P16Rik, C80053, Ga, GatA, Q9CZN8, gene:765639literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesbrainstem, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
NaxdNAD(P)HX ­dehydratase0710008K08Rik, 2810407E01Rik, Car, Carkd, Q9CZ42, gene:692259GFP, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolismall 14
Chchd6coiled-coil-helix-coiled-coil-helix ­domain ­containing ­60710001P09Rik, 1700021B03Rik, Mico, Micos25, Q91VN4, gene:660989literature, APEX_IMS, APEX_matrix, yeast mito homolog, coexpression, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pcbd2pterin ­4 ­alpha ­carbinolamine ­dehydratase/dimerization ­cofactor ­of ­hepatocyte ­nuclear ­factor ­1 ­alpha ­(TCF1) ­22700061N24Rik, Dcoh, Dcoh2, Dcohm, Q9CZL5, gene:725629targetP signal+, yeast mito homolog, induction, MS/MSunknownMetabolism > Metals and cofactors > Tetrahydrobiopterin synthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Agmatagmatine ­ureohydrolase ­(agmatinase)5033405N08Rik, A2AS89, gene:759869literature, targetP signal+, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolismliver, smallintestine
Micu2mitochondrial ­calcium ­uptake ­21110008L20Rik, 4833427E09Rik, AU041871, Efha, Efha1, Smhs2, Q8CD10, gene:685149literature, APEX_IMS, GFP, targetP signal+, mito protein domain, MS/MS+MIMSignaling > Calcium homeostasis > Calcium cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > Calcium uniporter		smallintestine, largeintestine, placenta, testis
Akr1b7aldo-keto ­reductase ­family ­1, ­member ­B7A, AR, Avdp, MV, MVDP, P21300, gene:119979induction, coexpression, MS/MS++unknownMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Scp2sterol ­carrier ­protein ­2, ­liverAA409774, AA409893, C76618, C79031, NSL-TP, SC, SCP, SCP-2, SCP-X, SCPX, ns, ns-LTP, P32020, gene:202809targetP signal, Rickettsial homolog, mito protein domain+MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisbrainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, placenta, testis
Rab24RAB24, ­member ­RAS ­oncogene ­family6530406O07Rik, P35290, gene:193369yeast mito homolog, mito protein domain, induction, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, stomach, testis
Mcubmitochondrial ­calcium ­uniporter ­dominant ­negative ­beta ­subunit9030408N13Rik, Ccdc109b, Q810S1, gene:668159literature, targetP signal+, mito protein domain+MIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > Calcium uniporter		placenta
Lyplal1lysophospholipase-like ­1BC027340, Q96, Q96AVO, Q3UFF7, gene:2267918targetP signal, mito protein domain, MS/MS++unknownMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, placenta, testis
Spata19spermatogenesis ­associated ­191700001L23Rik, AV047838, spergen-1, Q9DAQ9, gene:754698mito protein domain+, MS/MS++unknownnonetestis
mt-Atp8ATP ­synthase ­F0 ­subunit ­8P03930, gene:177068literature, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		all 14
Ldhal6blactate ­dehydrogenase ­A-like ­6B4933402O15Rik, AI326310, LD, LDHL, Ldhal, Q8BVP2, gene:1065578targetP signal, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Carbohydrate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aldh1a7aldehyde ­dehydrogenase ­family ­1, ­subfamily ­A7AI987940, Ahd2-l, Ahd2-like, Aldh, Aldh-pb, Aldh1a4, Aldhpb, O35945, gene:263588yeast mito homolog+, mito protein domain, coexpression, MS/MSunknownnonecerebrum, cerebellum, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Kyat3kynurenine ­aminotransferase ­3Ccbl, Ccbl2, KA, KATIII, Kat, Kat3, Q71RI9, gene:2299058APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Kynurenine metabolism;
Metabolism > Metals and cofactors > NAD biosynthesis and metabolism		spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Oxsm3-oxoacyl-ACP ­synthase, ­mitochondrial4933425A18Rik, C80494, Q9D404, gene:711478literature, APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisliver, heart, adipose, smallintestine, largeintestine, placenta, testis
mt-Nd3NADH ­dehydrogenase ­subunit ­3P03899, gene:177188literature, Rickettsial homolog, mito protein domain+, MS/MSMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Adck1aarF ­domain ­containing ­kinase ­12610005A10Rik, Q9D0L4, gene:721138yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSunknownnonecerebrum, spinalcord, kidney, heart, skeletalmuscle, adipose, stomach, placenta
Slc25a33solute ­carrier ­family ­25, ­member ­335730438N18Rik, Pn, Pnc1, Q3TZX3, gene:705568literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Small molecule transport > SLC25A family		brainstem, spinalcord, placenta, testis
Mgst1microsomal ­glutathione ­S-transferase ­11500002K10Rik, Gst, Q91VS7, gene:566158mito protein domain, coexpression, MS/MS++MembraneMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism		cerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Unguracil ­DNA ­glycosylaseUNG1, UNG2, P97931, gene:222568literature, targetP signal, yeast mito homolog, mito protein domain, inductionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Nsun4NOL1/NOP2/Sun ­domain ­family, ­member ­42310010O12Rik, 2810405F18Rik, AI507900, Shtap, Q9CZ57, gene:721818APEX_matrix, targetP signal, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		placenta
Tmem205transmembrane ­protein ­205Q91XE8, gene:2350438yeast mito homolog, mito protein domain+, coexpressionMembranenoneliver, adipose
Dbidiazepam ­binding ­inhibitorACBD1, Ac, Acbp, E, EP, endoz, endozepine, P31786, gene:131678targetP signal, mito protein domain, induction, coexpressionunknownMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
CoasyCoenzyme ­A ­synthase1300003G02Rik, Dpc, Dpck, P, Ppat, Ukr, Ukr1, Q9DBL7, gene:717438APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Coenzyme A metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Stard7START ­domain ­containing ­7AI852671, AL022671, AW544915, Q8R1R3, gene:991388APEX_IMS, targetP signal, mito protein domain, induction, coexpression+IMSMetabolism > Lipid metabolism > Phospholipid metabolism;
Small molecule transport		none
Letm2leucine ­zipper-EF-hand ­containing ­transmembrane ­protein ­26030453H13, D030041N04Rik, Q7TNU7, gene:2700358targetP signal, yeast mito homolog+, mito protein domain+MIMnonenone
Ptcd1pentatricopeptide ­repeat ­domain ­11110069M14Rik, Q8C2E4, gene:717998targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granulescerebellum, largeintestine, placenta
Mtfp1mitochondrial ­fission ­process ­11700020C11Rik, 2610507A21Rik, AV005788, Mtp1, Mtp18, Q9CRB8, gene:679008literature, induction, coexpression, MS/MS+MembraneMitochondrial dynamics and surveillance > Fissionall 14
Coa4cytochrome ­c ­oxidase ­assembly ­factor ­45330414O08Rik, AI115477, AW047259, Chchd8, E2ig2, Q8BT51, gene:681858yeast mito homolog++, mito protein domain, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		placenta
Ephx2epoxide ­hydrolase ­2, ­cytoplasmicCEH, Eph, Eph2, SEH, s, sE, sEP, P34914, gene:138508Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Lipid metabolism		kidney, liver, heart, skeletalmuscle, adipose, smallintestine, stomach
Nrd1nardilysin, ­N-arginine ­dibasic ­convertase, ­NRD ­convertase ­12600011I06Rik, AI875733, NRD, NRD-C, Nrdc, Q8BHG1, gene:2305988targetP signal, Rickettsial homolog, mito protein domain+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting		testis
Acacbacetyl-Coenzyme ­A ­carboxylase ­betaAI597064, AW743042, Acc, Acc2, Accb, E9Q4Z2, gene:1007058yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+MOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Vitamin metabolism > Biotin utilizing proteins		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Mavsmitochondrial ­antiviral ­signaling ­proteinD430028G21Rik, IP, IPS-1, Visa, cardif, Q8VCF0, gene:2286078literature, induction, coexpression+, MS/MSMOMSignaling > Immune responsebrainstem, skeletalmuscle, adipose, placenta, testis
Tmem143transmembrane ­protein ­1432310076O21Rik, AI481604, Q8VD26, gene:702098targetP signal, coexpression+, MS/MSMIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
Mtpapmitochondrial ­poly(A) ­polymerase0610027A18Rik, AW551379, Pa, Papd1, Tent, Tent6, Q9D0D3, gene:674408literature, APEX_matrix, targetP signal+, mito protein domain, inductionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		cerebrum, cerebellum, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sdslserine ­dehydratase-like4432411H13Rik, AI504310, SDH1, SDS, SDS-RS1, TDH, Q8R238, gene:2576358yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Amino acid metabolism > Serine metabolismnone
Cmpk2cytidine ­monophosphate ­(UMP-CMP) ­kinase ­2, ­mitochondrial1200004E04Rik, TDK, TDKI, Tyk, Tyki, Q3U5Q7, gene:221698literature, targetP signal+, Rickettsial homolog, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingspinalcord, smallintestine
Glyctkglycerate ­kinase6230410P16Rik, C430006L12, Q8QZY2, gene:2355828targetP signal, coexpression, MS/MS+MatrixMetabolism > Carbohydrate metabolismkidney, liver, placenta
Rpusd4RNA ­pseudouridylate ­synthase ­domain ­containing ­42410001E19Rik, Q9CWX4, gene:719898APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications		placenta
Smim20small ­integral ­membrane ­protein ­201110067B18Rik, 1810013D10Rik, MITRAC7, N28078, D3Z7Q2, gene:662787literature,targetP signal, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, placenta, testis
Mterf4mitochondrial ­transcription ­termination ­factor ­41810059A23Rik, 4933412H03Rik, Mterfd, Mterfd2, Q8BVN4, gene:698217APEX_matrix, targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblynone
Top1mtDNA ­topoisomerase ­1, ­mitochondrial2900052H09Rik, Q8R4U6, gene:729607literature, APEX_matrix, targetP signal+, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtRNA metabolism > Transcription		none
Arg2arginase ­type ­IIAII, AU022422, O08691, gene:118477literature, APEX_matrix, targetP signal+, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolismkidney, adipose, smallintestine, largeintestine, placenta
Ptrh2peptidyl-tRNA ­hydrolase ­2A230072I16Rik, Bit, Bit1, CGI-147, PTH 2, Q8R2Y8, gene:2170577literature, yeast mito homolog, mito protein domain, MS/MS++MOMnoneall 14
Lyrm1LYR ­motif ­containing ­11110065L10Rik, 2310004B22Rik, 4930404J24Rik, Q9CQB7, gene:739197GFP, yeast mito homolog, mito protein domain+, MS/MSunknownnonebrainstem, testis
Aars2alanyl-tRNA ­synthetase ­2, ­mitochondrialAarsl, AlaRS, Gm89, Q14CH7, gene:2248057literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acsl1acyl-CoA ­synthetase ­long-chain ­family ­member ­1Ac, Acas, Acas1, Acs, FACS, Fac, Facl2, LACS 1, LACS1, P41216, gene:140817yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMOMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Dnajc30DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C301300007M11Rik, Wbscr, Wbscr18, P59041, gene:661147APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, MS/MSMIMnonecerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach
Tmlhetrimethyllysine ­hydroxylase, ­epsilonBbox, Bbox2, D430017M14Rik, TML, TMLD, TMLH, Q91ZE0, gene:1922897literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Carnitine synthesis and transportkidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
BaxBCL2-associated ­X ­proteinQ07813, gene:120287literature, mito protein domain, coexpression, MS/MS++MOMMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, brainstem, adipose, largeintestine, placenta, testis
Cryzl2crystallin ­zeta ­like ­2Q3UNZ8, gene:2265277targetP signal, mito protein domain, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Dnm1ldynamin ­1-like6330417M19Rik, AI450666, Dlp1, Dnm, Dnmlp1, Dr, Drp1, pyt, python, Q8K1M6, gene:740067literature, yeast mito homolog+, mito protein domain, inductionMOMMitochondrial dynamics and surveillance > Fissioncerebrum, cerebellum, brainstem, spinalcord
Pxmp2peroxisomal ­membrane ­protein ­222kD, 22kDa, PMP, PMP22, P42925, gene:193017GFP, yeast mito homolog+, mito protein domain, inductionMIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Cox20cytochrome ­c ­oxidase ­assembly ­protein ­202310005N03Rik, Fam3, Fam36a, Q9D7J4, gene:663597literature, APEX_IMS, GFP, yeast mito homolog++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Tmem177transmembrane ­protein ­1772300008B03Rik, Q8BPE4, gene:663437targetP signal, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, adipose, stomach, placenta, testis
Tk2thymidine ­kinase ­2, ­mitochondrialAU024611, mt-TK, Q8BN51, gene:578137literature, targetP signal+, mito protein domain, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, adipose
Fundc1FUN14 ­domain ­containing ­11500005J14Rik, 1810033P05Rik, Q9DB70, gene:720187yeast mito homolog, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, testis
Pgs1phosphatidylglycerophosphate ­synthase ­12610019F11Rik, 4933424M23Rik, SAF, Q8BHF7, gene:744517targetP signal, yeast mito homolog++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebrum, spinalcord, placenta
Fasnfatty ­acid ­synthaseA630082H08Rik, F, FAS, P19096, gene:141047yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionIMSMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
Cbr2carbonyl ­reductase ­2ML, MLCR, P08074, gene:124097targetP signal, Rickettsial homolog, mito protein domain, MS/MS+MatrixMetabolismcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Chpt1choline ­phosphotransferase ­1Q8C025, gene:2128627targetP signal, mito protein domain, induction, coexpression+MIMMetabolism > Lipid metabolism > Phospholipid metabolismnone
Atp5g1ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­C1 ­(subunit ­9)Atp5mc1, Q9CR84, gene:119517literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		none
Fam210bfamily ­with ­sequence ­similarity ­210, ­member ­B2010011I20Rik, AI430961, AV108736, Q9D8B6, gene:670177targetP signal, yeast mito homolog, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Iron homeostasiscerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sfxn2sideroflexin ­2C79732, F630107H02Rik, Q925N2, gene:942797yeast mito homolog, mito protein domain+, coexpressionMIMSmall molecule transport > Sideroflexinskidney, liver, adipose, largeintestine, stomach, placenta, testis
Mmadhcmethylmalonic ­aciduria ­(cobalamin ­deficiency) ­cblD ­type, ­with ­homocystinuria2010311D03Rik, AI314967, CblD, Q99LS1, gene:1091297APEX_matrix, targetP signal, induction, coexpressionMatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolismnone
Otcornithine ­transcarbamylaseAI265390, Sf, spf, P11725, gene:184167literature, targetP signal, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism > Urea cyclecerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Txnrd1thioredoxin ­reductase ­1T, TR, TR1, Trx, TrxR1, Q9JMH6, gene:504937GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSunknownMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins		skeletalmuscle, smallintestine, placenta, testis
Arf5ADP-ribosylation ­factor ­5P84084, gene:118447targetP signal, mito protein domain, coexpression, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Fpgsfolylpolyglutamyl ­synthetaseAA408187, P48760, gene:142876APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homologMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismnone
Trmt10ctRNA ­methyltransferase ­10C, ­mitochondrial ­RNase ­P ­subunit1300018J16Rik, D16Ertd454, D16Ertd454e, Rg9mtd, Rg9mtd1, Rnmtd1, Q3UFY8, gene:525756literature, APEX_matrix, GFP, targetP signal+, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications		largeintestine, placenta
Them7thioesterase ­superfamily ­member ­70610012H03Rik, Q9DCP4, gene:740886targetP signal, mito protein domain, MS/MS+Matrixnonekidney
Lactb2lactamase, ­beta ­2Cgi-8, Cgi-83, E430032H21Rik, Q99KR3, gene:2124426mito protein domain, induction, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decaykidney, liver, largeintestine, stomach
Smim26small ­integral ­membrane ­protein ­26Gm561, Q3V460, gene:2287156induction, coexpression, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, placenta, testis
Pgam5phosphoglycerate ­mutase ­family ­member ­52610528A17Rik, Q8BX10, gene:725426APEX_IMS, mito protein domain, coexpression, MS/MS++MOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
Ptpmt1protein ­tyrosine ­phosphatase, ­mitochondrial ­11110001D10Rik, 2810004N20Rik, PLIP, Q66GT5, gene:664616literature, APEX_matrix, mito protein domain, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		all 14
Hebp1heme ­binding ­protein ­1Hebp, p22HBP, Q9R257, gene:151996APEX_IMS, mito protein domain, coexpression, MS/MS++IMSnonecerebrum, cerebellum, liver, adipose, placenta
Abcd1ATP-binding ­cassette, ­sub-family ­D ­(ALD), ­member ­1A, ALDP, Ald, Aldgh, P48410, gene:116666targetP signal, Rickettsial homolog, mito protein domain, inductionMembraneSmall molecule transport > ABC transportersadipose
Hsdl1hydroxysteroid ­dehydrogenase ­like ­12700067E09Rik, Q8BTX9, gene:725526GFP, Rickettsial homolog, mito protein domain, MS/MS++unknownnonecerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cbr3carbonyl ­reductase ­31110001J05Rik, C81353, Q8K354, gene:1098576targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Detoxification > Xenobiotic metabolismcerebrum, spinalcord, adipose, smallintestine, largeintestine, stomach
Prdx6peroxiredoxin ­61-Cys Prx, 1-cys, 1-cysPrx, 9430088D19Rik, AA690119, Aop2, Brp-, Brp-12, CP-, CP-3, GP, GPx, Ltw, Ltw-, Ltw-4, Ltw4, Lvtw, Lvtw-4, N, NSGPx, ORF06, Prdx5, a, aiPLA2, O08709, gene:117586yeast mito homolog+, Rickettsial homolog, mito protein domainunknownMetabolism > Lipid metabolism > Phospholipid metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism		cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Dnajc4DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C4Hsp, Hspf2, Mcg18, Q9D844, gene:574316GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMembraneProtein import, sorting and homeostasis > Protein homeostasislargeintestine
CebpzosCCAAT/enhancer ­binding ­protein ­(C/EBP), ­zeta, ­opposite ­strand1110001A16Rik, Q8BTE5, gene:685546coexpression+, MS/MS+unknownnonecerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, placenta, testis
Foxred1FAD-dependent ­oxidoreductase ­domain ­containing ­1BC024806, TEG-23, Tex23, Q3TQB2, gene:2351696literature, targetP signal, mito protein domain, coexpression+MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		adipose, largeintestine, placenta, testis
Eri3exoribonuclease ­3P, PI, PINT1, Prnpip1, Q8C460, gene:1405466targetP signal+, mito protein domain, MS/MSMatrixnonecerebrum, cerebellum
Dhx30DEAH ­(Asp-Glu-Ala-His) ­box ­polypeptide ­302810477H02Rik, C130058C04Rik, Ddx30, HELG, Ret-CoR, hel, Q99PU8, gene:728316literature, targetP signal+, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Bcl2l13BCL2-like ­13 ­(apoptosis ­facilitator)BCL-R, BCL-RAMBO, E430016C20Rik, Mi, Mil, Mil-1, Mil1, P59017, gene:940446literature, mito protein domain, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy;
Mitochondrial dynamics and surveillance > Apoptosis		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Acp6acid ­phosphatase ­6, ­lysophosphatidic5730559A09Rik, AC, ACPL1, AU022842, mPA, mPACPL1, Q8BP40, gene:666596literature, APEX_IMS, targetP signal, mito protein domain, MS/MS++IMSMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox7a2lcytochrome ­c ­oxidase ­subunit ­7A2 ­likeCOX, COX7AR, COX7RP, EB1, SIG, SIG-, SIG-81, SIG81, Silg81, Q61387, gene:204636literature, APEX_IMS, APEX_matrix, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits;
OXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly		all 14
Tstd1thiosulfate ­sulfurtransferase ­(rhodanese)-like ­domain ­containing ­1AV065366, EG226654, Gm4848, KAT, E9PY03, gene:2266546targetP signal, yeast mito homolog, mito protein domain, MS/MSunknownMetabolism > Sulfur metabolismkidney, smallintestine, largeintestine
Qdprquinoid ­dihydropteridine ­reductase2610008L04Rik, D5Ertd371e, Dhpr, PKU2, Q8BVI4, gene:1103916APEX_matrix, targetP signal, mito protein domain, inductionMatrixMetabolism > Metals and cofactors > Tetrahydrobiopterin synthesis;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, stomach, placenta, testis
Acsm2acyl-CoA ­synthetase ­medium-chain ­family ­member ­2AI315615, BC031140, Q8K0L3, gene:2337996yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Detoxification > Xenobiotic metabolism		kidney, liver, heart
Adck2aarF ­domain ­containing ­kinase ­2AA408112, BB006057, Q6NSR3, gene:578696GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMIMnonenone
Osbpl1aoxysterol ­binding ­protein-like ­1AG430090F17Rik, Gm753, ORP-1, Osbpl1b, Q91XL9, gene:642916Rickettsial homolog, mito protein domain, induction, MS/MSunknownMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebrum, liver, largeintestine, placenta
Trmt1tRNA ­methyltransferase ­16720406L13Rik, 6720477L24, D8Ertd812, D8Ertd812e, Q3TX08, gene:2125286targetP signal+, yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Mtif3mitochondrial ­translational ­initiation ­factor ­32810012L14Rik, AI414549, Q9CZD5, gene:763666literature, APEX_matrix, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > Translation factorslargeintestine
Pet100PET100 ­homolog2900053A13Rik, P0DJE0, gene:1005038906literature, yeast mito homolog++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, spinalcord, kidney, liver, heart, smallintestine, largeintestine, placenta
Mtfr1mitochondrial ­fission ­regulator ­11300002C08Rik, 1700080D04Rik, 2810026O10Rik, 4930579E05Rik, Chppr, Fam54, Fam54a2, Q99MB2, gene:674726literature, targetP signal, mito protein domain+, coexpressionMembraneMitochondrial dynamics and surveillance > Fissionnone
Tfb1mtranscription ­factor ­B1, ­mitochondrialAI429207, mtTFB1, Q8JZM0, gene:2244816literature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		brainstem, largeintestine, placenta, testis
Fth1ferritin ­heavy ­polypeptide ­1FHC, Fth, H-fer, HFt, MFH, P09528, gene:143196mito protein domain, MS/MS++unknownMetabolism > Metals and cofactors > Iron homeostasiscerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta
Tspotranslocator ­proteinBz, Bzrp, IBP, P, PBR, Ts, Tspo1, P50637, gene:122576literature, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisspinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Glyatglycine-N-acyltransferaseA330009E03Rik, ACGNAT, AI195249, AI315345, CAT, GAT, Q91XE0, gene:1071466literature, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Detoxification > Xenobiotic metabolism		spinalcord, kidney, liver, placenta
Rbfaribosome ­binding ­factor ­A1110032A13Rik, AI595940, Q6P3B9, gene:687316APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblynone
Rnaseh1ribonuclease ­H1E9QLN8, gene:198196literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		none
Tmem186transmembrane ­protein ­1862810440M13Rik, 4432406C05Rik, AI648175, AW210586, Q9CR76, gene:666905targetP signal, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pex11bperoxisomal ­biogenesis ­factor ­11 ­betaPEX11beta, Pex11pbeta, Q9Z210, gene:186325targetP signal, coexpression, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Nudt5nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­5Q9JKX6, gene:538935yeast mito homolog++, mito protein domain, coexpressionunknownMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingnone
Sod1superoxide ­dismutase ­1, ­solubleB430204E11Rik, Cu/Zn-, Cu/Zn-SOD, CuZn, CuZnSOD, I, Ip, Ipo-1, Ipo1, SO, SODC, Sod, Sod-1, P08228, gene:206555literature, yeast mito homolog, mito protein domain, induction, coexpressionIMSMetabolism > Detoxification > ROS and glutathione metabolismall 14
Starsteroidogenic ­acute ­regulatory ­proteinAV363654, D8Ertd419, D8Ertd419e, stARD1, P51557, gene:208455literature, targetP signal, mito protein domain, coexpression, MS/MSMOM , IMSMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesistestis
Gtpbp10GTP-binding ­protein ­10 ­(putative)4930545J22Rik, BC034507, Q8K013, gene:2077045APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, placenta
Acss3acyl-CoA ­synthetase ­short-chain ­family ­member ­38430416H19Rik, Gm874, Q14DH7, gene:3806605targetP signal, yeast mito homolog, mito protein domain, MS/MSMatrixMetabolism > Lipid metabolismkidney, liver, adipose, placenta, testis
Ccdc51coiled-coil ­domain ­containing ­515730568A12Rik, AI551049, Mit, Mitok, Q3URS9, gene:666585APEX_matrix, targetP signal, MS/MS++MIMSmall molecule transportall 14
Acot9acyl-CoA ­thioesterase ­90610041P13Rik, Acat, Acate2, C76421, MT-ACT4, MT-ACT48, MTE-2, U8, p4, p48, Q9R0X4, gene:563605literature, targetP signal, MS/MS++MIMMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufaf3NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­34733401H18Rik, Q9JKL4, gene:667065literature, targetP signal, mito protein domain, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Flad1flavin ­adenine ­dinucleotide ­synthetase ­1A930017E24Rik, Pp5, Pp591, Q8R123, gene:3199455APEX_matrix, mito protein domain, induction, coexpressionMatrixMetabolism > Vitamin metabolism > Vitamin B2 metabolismspinalcord, adipose, stomach
Acacaacetyl-Coenzyme ­A ­carboxylase ­alphaA530025K05Rik, Ac, Acac, Acc, Acc1, Gm738, Q5SWU9, gene:1074765yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis;
Metabolism > Vitamin metabolism > Biotin utilizing proteins		brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Kmokynurenine ­3-monooxygenase ­(kynurenine ­3-hydroxylase)AI046660, Q91WN4, gene:982565yeast mito homolog, mito protein domain, MS/MS++MOMMetabolism > Amino acid metabolism > Kynurenine metabolism;
Metabolism > Metals and cofactors > NAD biosynthesis and metabolism		kidney, liver
Mterf3mitochondrial ­transcription ­termination ­factor ­32410017I18Rik, Mterfd, Mterfd1, Q8R3J4, gene:664105literature, APEX_matrix, GFP, targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblynone
Oxr1oxidation ­resistance ­12210416C20Rik, C7, C7B, Q4KMM3, gene:1707195literature, yeast mito homolog+, mito protein domain, MS/MSMOMMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem
Nudt9nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­91190002C07Rik, ADPR-PPase, AI462474, Q8BVU5, gene:741675APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, placenta, testis
Thnsl1threonine ­synthase-like ­1 ­(bacterial)AW413632, Q8BH55, gene:2089675APEX_matrix, mito protein domain, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, testis
Pycr2pyrroline-5-carboxylate ­reductase ­family, ­member ­21810018M05Rik, P5c, P5cr2, Q922Q4, gene:690515APEX_matrix, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Hint1histidine ­triad ­nucleotide ­binding ­protein ­1AA673479, Hint, Ip, Ipk1, PKCI, PKCI-1, PRKC, PRKCNH1, P70349, gene:152545Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, kidney, smallintestine, placenta, testis
Slc25a34solute ­carrier ­family ­25, ­member ­34Gm1369, A2ADF7, gene:3840715yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a48solute ­carrier ­family ­25, ­member ­48AU042651, E230025K15, Q8BW66, gene:3282585yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a28solute ­carrier ­family ­25, ­member ­28Mfr, Mfrn2, Mrs3, Mrs3/4, Q8R0Z5, gene:2466965literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Metals and cofactors > Iron homeostasis;
Small molecule transport > SLC25A family		none
Slc25a43solute ­carrier ­family ­25, ­member ­43Gm8, A2A3V2, gene:1947445yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a47solute ­carrier ­family ­25, ­member ­47AI132487, AI876593, HDMCP, Q6IS41, gene:1049105literature, yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a41solute ­carrier ­family ­25, ­member ­414933406J04Rik, AI507137, Q8BVN7, gene:1037755yeast mito homolog+, mito protein domain+MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Small molecule transport > SLC25A family		none
Slc25a54solute ­carrier ­family ­25, ­member ­544930443G12Rik, SCaMC-1, SCaMC-1like, B1AUS6, gene:746865yeast mito homolog+, mito protein domain+MembraneSmall molecule transport > SLC25A familynone
Slc25a37solute ­carrier ­family ­25, ­member ­371700020E22Rik, 4930513O14Rik, 4930526G11Rik, AI848481, C330015G08Rik, Fra, Mf, Mfr, Mfrn, Mfrn1, Ms, Mscp, frascati, mito, mitoferrin, Q920G8, gene:677125literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Metals and cofactors > Iron homeostasis;
Small molecule transport > SLC25A family		none
Ucp2uncoupling ­protein ­2 ­(mitochondrial, ­proton ­carrier)Slc25a8, UCP 2, UCPH, P70406, gene:222285literature, yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
YbeyybeY ­metallopeptidase1110068N23Rik, A130042E20Rik, C21orf57, ORF57, ORF66, Q8CAV0, gene:2161195APEX_matrix, targetP signal, Rickettsial homolog, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		largeintestine, placenta, testis
Ogg18-oxoguanine ­DNA-glycosylase ­1Mmh, O08760, gene:182945literature, targetP signal+, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Gm4952predicted ­gene ­4952EG240549, Q5FW57, gene:2405495mito protein domain, MS/MS++unknownMetabolismkidney, liver
Fabp1fatty ­acid ­binding ­protein ­1, ­liverFa, Fabpl, L-F, L-FABP, P12710, gene:140805mito protein domain, MS/MS++unknownMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Lipid metabolism		liver, smallintestine
Mettl15methyltransferase ­like ­150610027B03Rik, AI303697, AW049952, Mett5d1, Q9DCL4, gene:768945APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modificationslargeintestine, placenta
Metap1dmethionyl ­aminopeptidase ­type ­1D ­(mitochondrial)2310066F24Rik, 3110033D18Rik, AV117938, MAP 1D, Map1d, MetAP 1D, Meta, Metapl1, Q9CPW9, gene:665595literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > fMet processing;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases		none
Ldhblactate ­dehydrogenase ­BAI790582, H-Ld, H-Ldh, LDH-B, LDH-H, Ldh-, Ldh-2, Ldh2, P16125, gene:168325Rickettsial homolog, mito protein domain, inductionunknownMetabolism > Amino acid metabolism > Glyoxylate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Lyrm9LYR ­motif ­containing ­91810012P15Rik, Q3UN90, gene:662745mito protein domain+, MS/MSunknownnonecerebellum, heart, adipose, testis
Mtarc1mitochondrial ­amidoxime ­reducing ­component ­11300013F15Rik, Mar, Marc1, Mos, Mosc1, Q9CW42, gene:661125mito protein domain+, MS/MSMOMMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Metabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Recql4RecQ ­protein-like ­4RecQ4, Q75NR7, gene:794565targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Plpbppyridoxal ­phosphate ­binding ­protein1700024N20Rik, 2200002F22Rik, P, Prosc, Q9Z2Y8, gene:1148635APEX_matrix, targetP signal, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin B6 metabolismall 14
Mul1mitochondrial ­ubiquitin ­ligase ­activator ­of ­NFKB ­10610009K11Rik, AV000801, Gide, Q8VCM5, gene:683505literature, mito protein domain+, inductionMOMProtein import, sorting and homeostasis > Protein homeostasis;
Mitochondrial dynamics and surveillance > Fission;
Signaling		skeletalmuscle, largeintestine
Nudt6nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­6Asfgf2b, Q8CH40, gene:2292285APEX_matrix, targetP signal, mito protein domain, coexpressionMatrixnonenone
Pink1PTEN ­induced ­putative ­kinase ­11190006F07Rik, AU042772, AW557854, BRPK, br, mFLJ00387, Q99MQ3, gene:689435literature, targetP signal, mito protein domain, coexpressionMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy;
Signaling		none
Vps13dvacuolar ­protein ­sorting ­13DB1ART2, gene:2308955manual, yeast mito homolog, mito protein domain, induction, coexpressionMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle
Dmac2distal ­membrane ­arm ­assembly ­complex ­22310004L02Rik, At, Atp5sl, C030044E10Rik, Q9D7K5, gene:663494APEX_matrix, GFP, targetP signal, induction, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, stomach
Micu1mitochondrial ­calcium ­uptake ­1C730016L05Rik, Calc, Cba, Cbara1, Q8VCX5, gene:2160014literature, APEX_IMS, GFP, targetP signal, mito protein domain, MS/MS+MIMSignaling > Calcium homeostasis > Calcium cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > Calcium uniporter		cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nt5dc35'-nucleotidase ­domain ­containing ­3AU040402, AW540062, C630002B14Rik, G, TU12B1-TY, Q3UHB1, gene:1034664APEX_matrix, targetP signal, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, stomach, placenta, testis
Nipsnap3anipsnap ­homolog ­3A1700054F22Rik, AI429120, G3X8S9, gene:733984APEX_matrix, targetP signal, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Top3atopoisomerase ­(DNA) ­III ­alphaO70157, gene:219754APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replicationtestis
Amacralpha-methylacyl-CoA ­racemaseMac, Macr1, O09174, gene:171174literature, mito protein domain, coexpression, MS/MSMatrixMetabolism > Lipid metabolism > Fatty acid oxidationkidney, liver, adipose, smallintestine, testis
Trmt5TRM5 ­tRNA ­methyltransferase ­52610027O18Rik, mKIAA1393, Q9D0C4, gene:763574literature,targetP signal, yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Micu3mitochondrial ­calcium ­uptake ­family, ­member ­32900075B16Rik, Efha, Efha2, Q9CTY5, gene:785064manual, targetP signal, mito protein domain, MS/MSMIMSignaling > Calcium homeostasis > Calcium cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > Calcium uniporter		cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, stomach
Pnkdparoxysmal ­nonkinesiogenic ­dyskinesia2210013N15Rik, 2810403H05Rik, AI854243, Brp, Brp17, MNCb-5687, MR-1, Tahccp2, Q69ZP3, gene:566954literature,targetP signal, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Car5acarbonic ­anhydrase ­5a, ­mitochondrialCAV, Ca, Ca5a, Car5, P23589, gene:123524literature, targetP signal, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Urea cycleliver
Nthl1nth ­(endonuclease ­III)-like ­1 ­(E.coli)Nth, Nth1, Octs3, O35980, gene:182074literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainunknownMetabolism > Metals and cofactors > Fe-S-containing proteinsnone
Arl2ADP-ribosylation ­factor-like ­22610009M23Rik, AI115441, AW553335, Q9D0J4, gene:563274literature, mito protein domain, coexpression, MS/MS+IMSMitochondrial dynamics and surveillance > Fusioncerebrum, brainstem, spinalcord, adipose, largeintestine
Synj2bpsynaptojanin ­2 ­binding ­proteinA, AA409442, ARIP2, ActRIP4, D12Wsu118, D12Wsu118e, OMP, OMP25, Q9D6K5, gene:240714APEX_IMS, mito protein domain, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Organelle contact sitescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mettl8methyltransferase ­like ­8BC004636, T, Tip, A2AUU0, gene:2280194APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtRNA metabolismnone
Mterf1bmitochondrial ­transcription ­termination ­factor ­1bGm9897, B9EJ57, gene:2085954literature, APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription		none
Rsad1radical ­S-adenosyl ­methionine ­domain ­containing ­1B430319G23, BC056485, Q5SUV1, gene:2379264APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Metals and cofactors > Fe-S-containing proteinsnone
Fdpsfarnesyl ­diphosphate ­synthetase6030492I17Rik, AI256750, Fdp, Fdpsl1, mKIAA1293, Q920E5, gene:1101964Rickettsial homolog, mito protein domain, MS/MS+MIMMetabolism > Lipid metabolism > Cholesterol-associatedliver, adipose, smallintestine, largeintestine, placenta
Ociad1OCIA ­domain ­containing ­16030432N09Rik, A, AI481327, AW557942, Asrij, B230209J16Rik, BB021357, Emi, Emi2, Im, Imi2, OCIA, TPA0, TPA018, Q9CRD0, gene:680954APEX_IMS, GFP, MS/MS++MOMnoneall 14
FastkFas-activated ­serine/threonine ­kinase0610011K02Rik, 610011K02Rik, Q8C725, gene:665874GFP, targetP signal, induction, coexpressionMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		none
Acsm4acyl-CoA ­synthetase ­medium-chain ­family ­member ­4O-M, O-MACS, OM, OMACS, Q80W40, gene:2338014manual, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMetabolism > Lipid metabolism > Fatty acid oxidationnone
Nme6NME/NM23 ­nucleoside ­diphosphate ­kinase ­6nm23-M, nm23-M6, O88425, gene:543694literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processinglargeintestine
Ahcyl1S-adenosylhomocysteine ­hydrolase-like ­11110034F20Rik, AA409031, AA414901, Ahcy-, Ahcy-rs3, DC, DCAL, IR, Irbit, Q80SW1, gene:2297094mito protein domain+, inductionMOMMitochondrial dynamics and surveillance > Organelle contact sitesbrainstem, spinalcord, smallintestine, stomach
Smim8small ­integral ­membrane ­protein ­81810030N24Rik, 2810406B13Rik, Q9CQQ0, gene:662914manual, induction, coexpression, MS/MSMOMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, adipose, placenta, testis
Idi1isopentenyl-diphosphate ­delta ­isomerase4832416K17Rik, IPPI1, P58044, gene:3195544targetP signal, mito protein domain, MS/MS+MatrixMetabolism > Lipid metabolism > Cholesterol-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtx3metaxin ­34930470O13Rik, AA409304, AI853833, AU067765, EG624619, Gm1194, Gm6514, D3YTP3, gene:3827934manual, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Intramitochondrial membrane interactionscerebrum, cerebellum, brainstem, spinalcord
Tmem126btransmembrane ­protein ­126B1110001A23Rik, Q9D1R1, gene:684724mito protein domain+, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bnip3BCL2/adenovirus ­E1B ­interacting ­protein ­3N, Nip3, O55003, gene:121764literature, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, brainstem, heart, skeletalmuscle, adipose
Fkbp8FK506 ­binding ­protein ­838kD, 38kDa, FKBP-38, FKBP-8, FKBPR38, Fkbp3, Fkbp38, mFKBP38, O35465, gene:142324literature, yeast mito homolog, mito protein domain, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Organelle contact sites;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, brainstem, spinalcord, largeintestine, placenta, testis
Mcrip2MAPK ­regulated ­corepressor ­interacting ­protein ­29530058B02Rik, Fam19, Fam195a, Q9CQB2, gene:682413induction, coexpression+unknownSignalingnone
Bola3bolA-like ­3 ­(E. ­coli)1810056O20Rik, Q8CEI1, gene:786533targetP signal, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins		cerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pnpt1polyribonucleotide ­nucleotidyltransferase ­11200003F12Rik, Old35, P, PNPase, Pnptl1, Q8K1R3, gene:717013literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrix, IMSMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decayall 14
Pde12phosphodiesterase ­122'-PDE, E430028B21Rik, Q3TIU4, gene:2119483APEX_matrix, targetP signal+, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		brainstem, smallintestine, largeintestine, testis
Usp30ubiquitin ­specific ­peptidase ­306330590F17Rik, AI851327, D5Ertd483, D5Ertd483e, Q3UN04, gene:1007563literature,targetP signal+, mito protein domainMOMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		adipose, placenta, testis
Tfb2mtranscription ­factor ­B2, ­mitochondrialHkp, Hkp1, Q3TL26, gene:152783literature, APEX_matrix, targetP signal+, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtRNA metabolism > Transcription		placenta
Mrps18bmitochondrial ­ribosomal ­protein ­S18B2400002C15Rik, MRP-S18-2, S18mt-b, Q99N84, gene:669733literature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
Maobmonoamine ­oxidase ­B6330414K01Rik, MAO, MAO-B, Q8BW75, gene:1097313literature, mito protein domain, MS/MS++MOMMetabolism > Amino acid metabolism > Catechol metabolism;
Metabolism > Detoxification > Xenobiotic metabolism		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Prxl2aperoxiredoxin ­like ­2A5730469M10Rik, AU040822, Ad, Adrx, Fam21, Fam213a, Pamm, Q9CYH2, gene:705643GFP, mito protein domain, MS/MS++MembraneMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, placenta, testis
Mgst3microsomal ­glutathione ­S-transferase ­32010012L10Rik, 2010306B17Rik, 2700004G04Rik, AA516734, GST, GST-III, Q9CPU4, gene:664473APEX_IMS, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Eicosanoid metabolismall 14
Dhodhdihydroorotate ­dehydrogenase2810417D19Rik, AI834883, O35435, gene:567493literature, mito protein domain, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing;
Metabolism > Electron carriers > Q-linked reactions, other		cerebrum, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl48mitochondrial ­ribosomal ­protein ­L481810030E20Rik, 2610028L11Rik, CGI-11, CGI-118, D4Ertd786, D4Ertd786e, L48mt, MRP-L48, Q8JZS9, gene:524433literature, APEX_matrix, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Gdap1ganglioside-induced ­differentiation-associated-protein ­1O88741, gene:145453APEX_IMS, mito protein domain, MS/MS++MOMnonecerebrum, cerebellum, brainstem, spinalcord
Bak1BCL2-antagonist/killer ­1Ba, Bak, N-B, N-BAK1, N-Bak, O08734, gene:120183literature, mito protein domain, MS/MS++MOMMitochondrial dynamics and surveillance > Apoptosisbrainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
mt-Nd1NADH ­dehydrogenase ­subunit ­1P03888, gene:177163literature, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		all 14
Ociad2OCIA ­domain ­containing ­21810027I20Rik, Q9D8W7, gene:4339043MS/MS++unknownSignalingall 14
Taztafazzin5031411C02Rik, 9130012G04Rik, AW107266, AW552613, G4.5, I7HJS2, gene:668263literature,yeast mito homolog++, mito protein domainIMSMetabolism > Lipid metabolism > Cardiolipin synthesisnone
Dcxrdicarbonyl ­L-xylulose ­reductase0610038K04Rik, 1810027P18Rik, XR, Q91X52, gene:678803APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMetabolism > Carbohydrate metabolismcerebrum, cerebellum, spinalcord, heart, adipose, largeintestine, stomach, placenta, testis
Pmaip1phorbol-12-myristate-13-acetate-induced ­protein ­1N, Noxa, Q9JM54, gene:588013literature, targetP signal, mito protein domain+MOMMitochondrial dynamics and surveillance > Apoptosisnone
Nipsnap3bnipsnap ­homolog ­3B2700063N13Rik, Nipsnap3a, Q9CQE1, gene:665363GFP, targetP signal, MS/MS+Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mmaamethylmalonic ­aciduria ­(cobalamin ­deficiency) ­type ­A2810018E08Rik, AI840684, Q8C7H1, gene:1091363manual, targetP signal, coexpression+MatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolismcerebrum, cerebellum, brainstem, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cyp11a1cytochrome ­P450, ­family ­11, ­subfamily ­a, ­polypeptide ­1Cyp1, Cyp11a, Cypxia1, D9Ertd411, D9Ertd411e, P450s, P450scc, Sc, Scc, csc, cscc, Q9QZ82, gene:130703literature, mito protein domain, MS/MS+MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme-containing proteins		adipose, placenta, testis
Aifm2apoptosis-inducing ­factor, ­mitochondrion-associated ­25430437E11Rik, Am, Amid, D730001I10Rik, FSP1, PR, PRG3, Q8BUE4, gene:713613literature, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMembraneMetabolism > Detoxification > ROS and glutathione metabolism;
Mitochondrial dynamics and surveillance > Apoptosis		none
Marchf5membrane ­associated ­ring-CH-type ­finger ­51810015H18Rik, 2310008I22Rik, 2700055A20Rik, 5730499H23Rik, E130202O05Rik, MARC, MARCH-V, MI, MITOL, March5, Marchv, Rnf1, Rnf153, Q3KNM2, gene:691043literature, mito protein domain, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Prdx2peroxiredoxin ­2AL022839, Band-8, NkefB, P, PRP, PrxII, T, TDX1, TP, TPx, TPx-B, TR, TSA, Tdpx, Tdpx1, Torin, Q61171, gene:216723GFP, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, stomach, placenta, testis
Sfxn4sideroflexin ­4Q925N1, gene:942813literature, yeast mito homolog, mito protein domain+MIMSmall molecule transport > Sideroflexinscerebellum, spinalcord
Ifi27interferon, ­alpha-inducible ­protein ­271110013J02Rik, 2900026P10Rik, D12Ertd647, D12Ertd647e, ISG12a, Ifi2, Ifi27l1, Q8C6G0, gene:526683literature, targetP signal, induction, coexpressionMembraneSignaling > Immune response;
Mitochondrial dynamics and surveillance > Apoptosis		none
Abca9ATP-binding ­cassette, ­sub-family ­A ­(ABC1), ­member ­9D630040K07Rik, Q8K449, gene:2172623GFP, targetP signal, Rickettsial homolog, mito protein domainMembraneSmall molecule transport > ABC transporterscerebrum, placenta
Ddx28DEAD ­box ­helicase ­282410004K13Rik, AI449652, Mddx28, Q9CWT6, gene:719863literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		spinalcord, adipose
Acot7acyl-CoA ­thioesterase ­72410041A17Rik, AU01471, Ach1, Act, Bac, Bach, CTE-IIa, Cte-II, Lach1, Q91V12, gene:700252targetP signal, mito protein domain, inductionMatrixMetabolism > Lipid metabolismbrainstem, spinalcord, adipose, largeintestine
Msrb3methionine ­sulfoxide ­reductase ­B3D430026P16Rik, I-8-23, MsrB2, Q8BU85, gene:3201832yeast mito homolog+, mito protein domainunknownMetabolism > Detoxification > ROS and glutathione metabolismnone
2300009A05RikRIKEN ­cDNA ­2300009A05 ­geneQ0VG49, gene:694782APEX_matrix, targetP signal, MS/MSMatrixnonebrainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, testis
Agpat51-acylglycerol-3-phosphate ­O-acyltransferase ­5 ­(lysophosphatidic ­acid ­acyltransferase, ­epsilon)1110013A05Rik, D8Ertd319, D8Ertd319e, Q9D1E8, gene:521232literature, mito protein domain, induction, MS/MSMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, placenta, testis
Acod1aconitate ­decarboxylase ­1AI323667, CAD, Ir, Irg1, P54987, gene:163652literature,yeast mito homolog, mito protein domain+MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism;
Signaling > Immune response		none
Fbxl4F-box ­and ­leucine-rich ­repeat ­protein ­4AI836810, FBL, FBL4, FBL5, Q8BH70, gene:2695142literature, mito protein domain, coexpressionIMSnoneadipose
Ftmtferritin ­mitochondrial4930447C24Rik, FerH, Fth3, MtF, Q9D5H4, gene:676342literature, targetP signal, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Iron homeostasistestis
Gpamglycerol-3-phosphate ­acyltransferase, ­mitochondrialGPA, GPAT, GPAT-1, GPAT1, P90, Q61586, gene:147322literature, mito protein domain, coexpressionMembraneMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Qtrt1queuine ­tRNA-ribosyltransferase ­catalytic ­subunit ­12610028E17Rik, Tgt, Q9JMA2, gene:605072APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Hpdl4-hydroxyphenylpyruvate ­dioxygenase-likeA830048M07Rik, BC034099, Glox, Gloxd1, Q8K248, gene:2426422manual, targetP signal, inductionunknownnonenone
Isoc2aisochorismatase ­domain ­containing ­2aIs, Isoc2, P85094, gene:6649942APEX_matrix, MS/MS++Matrixnoneall 14
Cyp11b1cytochrome ­P450, ­family ­11, ­subfamily ­b, ­polypeptide ­1AA389061, CPN1, Cyp11, Cyp11b, Cyp11b-, Cyp11b-1, FHI, Q3TG86, gene:1101152literature, targetP signal, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisnone
Cyp11b2cytochrome ­P450, ­family ­11, ­subfamily ­b, ­polypeptide ­2ALDOS, Cpn2, Cyp11, Cyp11b, Cyp11b-, Cyp11b-2, P15539, gene:130722literature, targetP signal, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme-containing proteins		none
Pet117PET117 ­homologGm20571, P0DJF2, gene:1000486442literature, yeast mito homolog, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, liver, adipose, largeintestine, stomach, placenta
Dhrs2dehydrogenase/reductase ­member ­25430405K24Rik, Hep27, Q149L0, gene:714122literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMetabolism > Detoxification > Xenobiotic metabolismnone
Cdk5rap1CDK5 ­regulatory ­subunit ­associated ­protein ­12310066P17Rik, Q8BTW8, gene:669712literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Snd1staphylococcal ­nuclease ­and ­tudor ­domain ­containing ­1AL033314, Tudo, Tudor-SN, Q78PY7, gene:564632GFP, yeast mito homolog, mito protein domainunknownnonecerebrum, cerebellum, brainstem, liver, smallintestine, placenta, testis
Cyb5r3cytochrome ­b5 ­reductase ­30610016L08Rik, 2500002N19Rik, B5R, C85115, Di, Dia, Dia-1, Dia1, WU:Cyb5r3, Q9DCN2, gene:1097542literature, mito protein domain, MS/MS+MOMMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex;
Metabolism > Lipid metabolism		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Maoamonoamine ­oxidase ­A1110061B18Rik, AA407771, MA, Q64133, gene:171612literature, mito protein domain, MS/MS+MOMMetabolism > Amino acid metabolism > Catechol metabolism;
Metabolism > Detoxification > Xenobiotic metabolism		all 14
Mffmitochondrial ­fission ­factor5230400G24Rik, AI314724, Q6PCP5, gene:757342literature, induction, MS/MSMOMMitochondrial dynamics and surveillance > Fissioncerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta, testis
Nlrx1NLR ­family ­member ­X1BC034204, NOD9, Q3TL44, gene:2701512APEX_matrix, targetP signal, MS/MSMatrixSignaling > Immune responseall 14
Fam185afamily ­with ­sequence ­similarity ­185, ­member ­A4631428I10, AI847670, Q7TPD2, gene:3300502APEX_matrix, targetP signal, coexpressionMatrixnonenone
Mief1mitochondrial ­elongation ­factor ­1A230016E22, AI452372, Smc, Smcr7l, Q8BGV8, gene:2395552literature, mito protein domain, induction, coexpressionMOM , MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly;
Mitochondrial dynamics and surveillance > Fission		none
Coa7cytochrome ­c ­oxidase ­assembly ­factor ­72010305A19Rik, AI451324, D4Ertd796, D4Ertd796e, Sel, Selrc1, Q921H9, gene:698932literature, APEX_IMS, mito protein domain, coexpression, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acot11acyl-CoA ­thioesterase ­111110020M10Rik, 2010309H15Rik, AW060409, BFIT, BFIT1, The, Thea, Them1, mKIAA0707, Q8VHQ9, gene:3299102literature,targetP signal, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Fatty acid oxidationnone
Pusl1pseudouridylate ­synthase-like ­12810021I11Rik, AI853843, D18346, A2ADA5, gene:4338131APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translationcerebrum, spinalcord, largeintestine, placenta
Polqpolymerase ­(DNA ­directed), ­thetaA430110D14Rik, Q8CGS6, gene:777821literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenancebrainstem, testis
Dmac2ldistal ­membrane ­arm ­assembly ­complex ­2 ­like1110015E18Rik, ATPW, At, Atp5s, Q9CRA7, gene:680551literature, APEX_matrix, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Rmdn3regulator ­of ­microtubule ­dynamics ­31200015F23Rik, AI131757, Fam82, Fam82a2, Ptpip51, RMD-3, Rmd3, Q3UJU9, gene:678091literature, APEX_IMS, GFP, MS/MS++MOMMitochondrial dynamics and surveillance > Organelle contact sitescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Atp5mdATP ­synthase ­membrane ­subunit ­DAPIT2010301L15Rik, Usmg, Usmg5, Q78IK2, gene:664771GFP, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits;
Mitochondrial dynamics and surveillance > Cristae formation		all 14
Tomm20translocase ­of ­outer ­mitochondrial ­membrane ­201810060K07Rik, BB284719, Gm19268, MAS20, MOM19, TOM2, TOM20, mKIAA0016, Q9DCC8, gene:679521literature, yeast mito homolog+MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM;
Mitochondrial dynamics and surveillance		cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Bnip3lBCL2/adenovirus ­E1B ­interacting ­protein ­3-likeC86132, D14Ertd719, D14Ertd719e, N, Nip3L, Nix, Q9Z2F7, gene:121771literature, mito protein domain+, coexpressionMOMMitochondrial dynamics and surveillance > Apoptosisnone
Aifm3apoptosis-inducing ­factor, ­mitochondrion-associated ­32810401C16Rik, AI840249, Aifl, Q3TY86, gene:721681literature, Rickettsial homolog, mito protein domain+MIMMetabolism > Metals and cofactors > Fe-S-containing proteins;
Mitochondrial dynamics and surveillance > Apoptosis		none
Timm29translocase ­of ­inner ­mitochondrial ­membrane ­291810026J23Rik, TIM29, Q8BGX2, gene:697731coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathwaycerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, largeintestine, placenta, testis
Ppm1kprotein ­phosphatase ­1K ­(PP2C ­domain ­containing)2900063A19Rik, A930026L03Rik, PP2, PP2C-kappa, PP2Cm, Q8BXN7, gene:2433821literature, targetP signal, mito protein domainMatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex		cerebellum, liver, heart, adipose
Sirt4sirtuin ­44930596O17Rik, Q8R216, gene:753871literature, targetP signal, mito protein domainMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismlargeintestine
Park7Parkinson ­disease ­(autosomal ­recessive, ­early ­onset) ­7DJ-1, Dj1, Q99LX0, gene:573201literature, mito protein domain, coexpressionMOMProtein import, sorting and homeostasis > Protein homeostasis;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		all 14
Mterf1amitochondrial ­transcription ­termination ­factor ­1a4931431L11Rik, 9230106K09Rik, Mter, Mterf, Mterf1, mTERF1b, Q8CHZ9, gene:5457251literature, APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly		none
mt-Nd4lNADH ­dehydrogenase ­subunit ­4LP03903, gene:177201literature, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		heart, skeletalmuscle
AA467197expressed ­sequence ­AA467197NME, Nmes1, mir-147, Q810Q5, gene:4334701GFP, mito protein domain, MS/MS+Membranenonesmallintestine, largeintestine, stomach, placenta, testis
Uqcc2ubiquinol-cytochrome ­c ­reductase ­complex ­assembly ­factor ­22900010M23Rik, Cbp, Cbp6, M19, Mnf, Mnf1, Q9CQY6, gene:672671APEX_matrix, GFP, coexpression, MS/MSMIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors		all 14
Nme3NME/NM23 ­nucleoside ­diphosphate ­kinase ­31810009F08Rik, AI413736, DR-nm, DR-nm23, Ndk, Ndk3, Nm23-DR, Nm23-M, Nm23-M3, Q9WV85, gene:790591GFP, yeast mito homolog, Rickettsial homolog, mito protein domainMOMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, kidney, adipose, placenta, testis
Gtpbp6GTP ­binding ­protein ­6 ­(putative)AV119224, Pg, Pgbpll, p, pgpl, Q3U6U5, gene:1079991APEX_matrix, targetP signal+, mito protein domainMatrixnonenone
Them5thioesterase ­superfamily ­member ­51110007B02Rik, 1110038F21Rik, Q9CQJ0, gene:661981literature,targetP signal+, mito protein domainMatrixMetabolism > Lipid metabolismnone
Prkacaprotein ­kinase, ­cAMP ­dependent, ­catalytic, ­alphaC, P, PKCD, Pk, Pkaca, P05132, gene:187471literature,mito protein domain, coexpressionMIMSignaling > cAMP-PKA signalingcerebrum, brainstem, spinalcord, adipose, testis
Miga2mitoguardin ­25730472N09Rik, AA408683, AI790341, C9orf54, Fam73, Fam73b, R7476, R74766, Q8BK03, gene:1089580literature,coexpressionMOMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Organelle contact sites		cerebrum, cerebellum, brainstem, spinalcord, liver, testis
Mgarpmitochondria ­localized ­glutamic ­acid ­rich ­protein4930583H14Rik, AI195347, CESP-1, HUMMR, Osap, Qsap, Q8VI64, gene:677490literature, APEX_IMS, targetP signal, yeast mito homolog, coexpressionMembraneMitochondrial dynamics and surveillance > Traffickingnone
Mcl1myeloid ­cell ­leukemia ­sequence ­1AW556805, Mcl-, Mcl-1, P97287, gene:172100manual, targetP signal, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisadipose, largeintestine, placenta, testis
Myg1melanocyte ­proliferating ­gene ­10610023A07Rik, 2810433J21Rik, 5830429P19Rik, AI325965, Gamm, Gamm1, Q9JK81, gene:603150literature, targetP signal, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications		none
Etfbkmtelectron ­transfer ­flavoprotein ­beta ­subunit ­lysine ­methyltransferase4833442J19Rik, AI256744, ETFB-KMT, Mettl2, Mettl20, Q80ZM3, gene:3202040literature,mito protein domain+MatrixMetabolism > Electron carriers > Q-linked reactions, othernone
MutyhmutY ­DNA ­glycosylase5730495A01Rik, Mutyha, Mutyhalpha, Mutyhb, Mutyhbet, Mutyhbeta, Mutyhc, Myh, Q99P21, gene:706030GFP, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenancenone
Fastkd5FAST ­kinase ­domains ­5C78212, mKIAA1792, Q7TMV3, gene:3806010APEX_matrix, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		skeletalmuscle, largeintestine, placenta
Paicsphosphoribosylaminoimidazole ­carboxylase, ­phosphoribosylaminoribosylaminoimidazole, ­succinocarboxamide ­synthetase2610511I09Rik, A, ADE2H, ADE2H1, AIRC, PAIS, Q9DCL9, gene:670540APEX_matrix, Rickettsial homolog, coexpressionMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingnone
Cpt1ccarnitine ­palmitoyltransferase ­1c6530437J22Rik, 9630004I06Rik, CPT I-C, CPT IC, CPT1-B, CPTI-B, Q8BGD5, gene:780700literature, yeast mito homolog+, mito protein domainMOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle		none
Rcc1lreculator ­of ­chromosome ­condensation ­1 ­like5730496C04Rik, AU019812, Wbscr, Wbscr16, Q9CYF5, gene:942540literature, APEX_matrix, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modificationsplacenta
Antkmtadenine ­nucleotide ­translocase ­lysine ­methyltransferaseANT-KMT, Fam17, Fam173a, Q501J2, gene:2149170literature,coexpression, MS/MSMIMMetabolism > Nucleotide metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta
Uqcc3ubiquinol-cytochrome ­c ­reductase ­complex ­assembly ­factor ­3AI4624, AI462493, Cbp, Cbp4, Q8K2T4, gene:1071970literature,coexpression, MS/MSMIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors		liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Prdx4peroxiredoxin ­4AOE3, AOE372, Pr, Prx-iv, Prx4, TRANK, O08807, gene:533810APEX_IMS, Rickettsial homolog, mito protein domainIMSMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pycr1pyrroline-5-carboxylate ­reductase ­1P5CR 1, P5CR1, Q922W5, gene:2090270literature, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Proline metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Cryzcrystallin, ­zetaSEZ, Sez9, P47199, gene:129720APEX_matrix, mito protein domain, MS/MSMatrixnonespinalcord, kidney, liver, adipose, placenta, testis
Angel2angel ­homolog ­22610307I21Rik, 5730410O10Rik, AI845692, D1Ertd396, D1Ertd396e, D1Ertd654, D1Ertd654e, Q8K1C0, gene:52477-0APEX_matrix, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mt-mRNA modificationsadipose, smallintestine, placenta, testis
Mgme1mitochondrial ­genome ­maintenance ­exonuclease ­18430406I07Rik, AI426476, Q9CXC3, gene:74528-0literature, APEX_matrix, GFP, targetP signalMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay		largeintestine, placenta
Agpat41-acylglycerol-3-phosphate ­O-acyltransferase ­4 ­(lysophosphatidic ­acid ­acyltransferase, ­delta)1500003P24Rik, Q8K4X7, gene:68262-0literature,mito protein domain, inductionMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		testis
Comtd1catechol-O-methyltransferase ­domain ­containing ­11810030M08Rik, MT773, Q8BIG7, gene:69156-0GFP, MS/MS++Membranenoneall 14
Neu4sialidase ­49330166I04, Q8BZL1, gene:241159-0GFP, targetP signal+MOMMetabolism > Carbohydrate metabolismnone
Cyp27b1cytochrome ­P450, ­family ­27, ­subfamily ­b, ­polypeptide ­1Cp2, Cp2b, Cyp, Cyp1, Cyp27, Cyp27b, Cyp4, Cyp40, P450c, P450c1, Pd, Pddr, Vd, Vdd, Vdd1, Vddr, VddrI, Vdr, O35084, gene:13115-0literature, targetP signal, mito protein domainMIMMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Vitamin metabolism > Vitamin D metabolism		none
NoctnocturninAU043840, Ccr, Ccr4, Ccrn4l, O35710, gene:12457-0literature,targetP signal, mito protein domainMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismnone
Hdhd3haloacid ­dehalogenase-like ­hydrolase ­domain ­containing ­32810435D12Rik, Q9CYW4, gene:72748-0APEX_matrix, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc8b1solute ­carrier ­family ­8 ­(sodium/lithium/calcium ­exchanger), ­member ­B1AF261233, NC, NCKX, NCKX6, NCLX, Slc2, Slc24a6, Q925Q3, gene:170756-0literature,mito protein domain, inductionMIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport		placenta
mt-Nd6NADH ­dehydrogenase ­subunit ­6P03925, gene:17722-1literature, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits		none
Dmac1distal ­membrane ­arm ­assembly ­complex ­11700027K24Rik, 3110001D03Rik, Tmem261, Q9CQ00, gene:66928-1literature,MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors		cerebrum, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bco2beta-carotene ­oxygenase ­2B-dio, B-diox-II, Bcdo, Bcdo2, Bcmo, Bcmo2, CMO, CMO2, Q99NF1, gene:170752-1literature,mito protein domain, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin A metabolismsmallintestine
Tdrkhtudor ­and ­KH ­domain ­containing ­protein2700091C21Rik, Tdrd, Tdrd2, Q80VL1, gene:72634-1GFP, mito protein domain, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, adipose, testis
Gpx4glutathione ­peroxidase ­4GPx-4, GSHPx-4, PHG, PHGPx, mtPHG, mtPHGPx, sn, snGPx, Q91XR9, gene:625249-1literature, yeast mito homolog, mito protein domainMIMMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins		all 14
Comtcatechol-O-methyltransferaseComt1, D16Wsu103, D16Wsu103e, D330014B15Rik, O88587, gene:12846-1GFP, induction, coexpressionMembraneMetabolism > Amino acid metabolism > Catechol metabolismliver
Mtfr2mitochondrial ­fission ­regulator ­22610016C23Rik, 4933412C16Rik, Dufd1, Fam5, Fam54a, Q8VED8, gene:71804-1manual, mito protein domain+MembraneMitochondrial dynamics and surveillance > Fissionnone
BikBCL2-interacting ­killerBiklk, Bl, Blk, Nb, Nbk, O70337, gene:12124-1manual, mito protein domain+MOMMitochondrial dynamics and surveillance > Apoptosisnone
Lig3ligase ­III, ­DNA, ­ATP-dependentD11Wsu78, D11Wsu78e, Q80ZH7, gene:16882-1literature,yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair		none
Cry1cryptochrome ­1 ­(photolyase-like)AU020726, AU021000, Ph, Phll1, P97784, gene:12952-1literature, yeast mito homolog, mito protein domain, coexpressionunknownnonenone
Trub2TruB ­pseudouridine ­(psi) ­synthase ­family ­member ­2G430055L02Rik, Q91WG3, gene:227682-1APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications		none
Tomm20ltranslocase ­of ­outer ­mitochondrial ­membrane ­20-like4930553D19Rik, Q9D4V6, gene:75266-1manual, yeast mito homolog+MOMProtein import, sorting and homeostasis > Protein import and sortingnone
Ccdc127coiled-coil ­domain ­containing ­1270610011N22Rik, 5430420E17Rik, A430066A18, AI256405, AW050060, C130002N06, Q3TC33, gene:67433-1APEX_IMS, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
YrdcyrdC ­domain ­containing ­(E.coli)AV303379, BC023823, IRIP, ITIP, Q3U5F4, gene:230734-1manual, targetP signal, Rickettsial homologMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Preplprolyl ­endopeptidase-like2810457N15Rik, 9530014L06Rik, D030028O16Rik, mKIAA0436, Q8C167, gene:213760-1APEX_matrix, targetP signal, Rickettsial homologMatrixnonespinalcord, largeintestine
Myo19myosin ­XIX1110055A02Rik, Myohd, Myohd1, Q5SV80, gene:66196-2literature,yeast mito homolog, mito protein domainMOMMitochondrial dynamics and surveillance > Traffickingadipose
Thg1ltRNA-histidine ­guanylyltransferase ­1-like ­(S. ­cerevisiae)Q9CY52, gene:66628-2literature, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pif1PIF1 ­5'-to-3' ­DNA ­helicase4631410M14, AI4494, AI449441, Q80SX8, gene:208084-2literature, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenancenone
Rab5ifRAB5 ­interacting ­factor1110008F13Rik, AI316789, RCAF1, RIP5, Q9CQT9, gene:67388-2GFP, induction, coexpressionMIMOXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly		none
Cep89centrosomal ­protein ­892610507L03Rik, Ccdc123, Q9CZX2, gene:72140-2literature, targetP signalIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors		none
Acot10acyl-CoA ­thioesterase ­10Acat, Acate3, MT-ACT4, MT-ACT48, p4, p48, Q32MW3, gene:64833-2literature, targetP signalMatrixMetabolism > Lipid metabolismnone
Efhd1EF ­hand ­domain ­containing ­14931430I01Rik, AI452351, PP30, PP3051, mito, mitocalcin, Q9D4J1, gene:98363-2literature, mito protein domain, inductionMIMSignaling > Calcium homeostasis > EF hand proteinsnone
BidBH3 ­interacting ­domain ­death ­agonist2700049M22Rik, AI875481, AU022477, P70444, gene:12122-2literature, mito protein domain, coexpressionMOMMitochondrial dynamics and surveillance > Apoptosisnone
AtpsckmtATP ­synthase ­C ­subunit ­lysine ­N-methyltransferaseA930016P21Rik, AA987072, Fam173, Fam173b, mFam173b, Q9D1Z3, gene:68073-2literature,coexpressionMIMOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors		placenta
Cyp24a1cytochrome ­P450, ­family ­24, ­subfamily ­a, ­polypeptide ­124-OH, 24-OHase, CP2, CP24, Cyp2, Cyp24, Q64441, gene:13081-2literature, targetP signal, mito protein domainMIMMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Vitamin metabolism > Vitamin D metabolism		none
Sptlc2serine ­palmitoyltransferase, ­long ­chain ­base ­subunit ­2LCB, LCB2, LCB2a, Sp, Spt2, P97363, gene:20773-2GFP, Rickettsial homolog, mito protein domainMembraneMetabolism > Lipid metabolism > Phospholipid metabolismnone
Apex1apurinic/apyrimidinic ­endonuclease ­1APE, Apex, HA, HAP1, Ref-, Ref-1, P28352, gene:11792-2literature,Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
E130311K13RikRIKEN ­cDNA ­E130311K13 ­geneQ8BN57, gene:329659-2APEX_matrix, MS/MSMatrixnoneadipose, testis
Agkacylglycerol ­kinase2610037M15Rik, 6720408I04Rik, AI465370, MuL, Mulk, Q9ESW4, gene:69923-3literature, APEX_IMS, mito protein domainMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathway;
Metabolism > Lipid metabolism > Phospholipid metabolism		cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dus2dihydrouridine ­synthase ­22310016K04Rik, Dus, Dus2l, Q9D7B1, gene:66369-3GFP, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pank2pantothenate ­kinase ­24933409I19Rik, AI642621, Q3U4S0, gene:74450-3literature, targetP signal, mito protein domainIMSMetabolism > Metals and cofactors > Coenzyme A metabolismnone
Polg2polymerase ­(DNA ­directed), ­gamma ­2, ­accessory ­subunitmtPolB, p55, polG-beta, Q9QZM2, gene:50776-3literature, APEX_matrix, targetP signal, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid		none
Gpat2glycerol-3-phosphate ­acyltransferase ­2, ­mitochondrialA530057A03Rik, Gm116, Gpa, xGPAT1, Q14DK4, gene:215456-3manual, mito protein domainMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism		testis
Tomm34translocase ­of ­outer ­mitochondrial ­membrane ­342610100K07Rik, TOM3, TOM34, Q9CYG7, gene:67145-3literature, mito protein domainMOMProtein import, sorting and homeostasis > Protein import and sorting > TOMtestis
Plscr3phospholipid ­scramblase ­32210403O21Rik, 2610037N06Rik, ESTM3, X83310, Q9JIZ9, gene:70310-3literature,yeast mito homolog, mito protein domainMIMMetabolism > Lipid metabolism > Cardiolipin synthesisnone
Fkbp10FK506 ­binding ­protein ­1065kD, AI325255, FKBP-10, FKBP-65, FKBP65, Fkbp, Fkbp-, Fkbp-rs1, Fkbp1, Fkbp1-rs, Fkbp6, Fkbprp, Q61576, gene:14230-3APEX_IMS, mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesnone
Exd2exonuclease ­3'-5' ­domain ­containing ­24930539P14Rik, C85658, Exdl, Exdl2, Q8VEG4, gene:97827-3literature,mito protein domainMatrixMitochondrial central dogma > Translationcerebrum, cerebellum, testis
Bcl2l1BCL2-like ­1Bcl, Bcl(X, Bcl(X)L, Bcl-XL, Bcl2l, BclX, bcl-, bcl-x, bcl2-L-1, Q64373, gene:12048-3literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, placenta
Golph3golgi ­phosphoprotein ­34733401N08Rik, 5730410D03Rik, AW413496, Q9CRA5, gene:66629-4literature, targetP signal, inductionIMSnonenone
Nt5dc25'-nucleotidase ­domain ­containing ­22510015F01Rik, Q91X76, gene:70021-4APEX_matrix, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingspinalcord, largeintestine, placenta
Armc10armadillo ­repeat ­containing ­102810037C14Rik, Svh, Q9D0L7, gene:67211-4GFP, MS/MSMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Trafficking		cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Alkbh1alkB ­homolog ­1, ­histone ­H2A ­dioxygenase2700073G19Rik, Abh, Alk, Alkbh, al, alkB, hABH, P0CB42, gene:211064-4literature, APEX_matrix, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications		none
Akap10A ­kinase ­(PRKA) ­anchor ­protein ­101500031L16Rik, B130049N18Rik, D-AK, D-AKAP-2, D-AKAP2, PRKA10, O88845, gene:56697-4literature, mito protein domainMOMSignaling > cAMP-PKA signalingnone
Serac1serine ­active ­site ­containing ­14930511N22Rik, D17Ertd141, D17Ertd141e, Q3U213, gene:321007-4literature, APEX_IMS, targetP signalMOMMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, cerebellum, skeletalmuscle, stomach, testis
Septin4septin ­4A, ARTS, Bh5, Pnu, Pnutl2, Sep, Sept4, P28661, gene:18952-4literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisbrainstem, spinalcord
Fastkd3FAST ­kinase ­domains ­32310010B21Rik, AW048587, Q8BSN9, gene:69577-5APEX_matrix, targetP signalMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay		none
Bcl2l11BCL2-like ­11 ­(apoptosis ­facilitator)1500006F24Rik, Bi, Bim, Bo, Bod, bcl2-L-11, O54918, gene:12125-5manual, targetP signalMOMMitochondrial dynamics and surveillance > Apoptosisnone
Nbr1NBR1, ­autophagy ­cargo ­receptormKIAA0049, P97432, gene:17966-5APEX_IMS, coexpressionIMSMitochondrial dynamics and surveillance > Autophagycerebellum, liver
Rpiaribose ­5-phosphate ­isomerase ­ARPI, P47968, gene:19895-5APEX_matrix, targetP signalMatrixMetabolism > Carbohydrate metabolismplacenta
BokBCL2-related ­ovarian ­killermat, matador, mtd, O35425, gene:51800-5manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Miga1mitoguardin ­1A930038D06, AI852168, C030011O14Rik, Fam7, Fam73a, Mit, Mita1, Q4QQM5, gene:215708-5literatureMOMMitochondrial dynamics and surveillance > Fusioncerebrum, cerebellum, brainstem, spinalcord, smallintestine, testis
Prorpprotein ­only ­RNase ­P ­catalytic ­subunit1110008L16Rik, Mr, Mrpp3, mKIAA0391, Q8JZY4, gene:66132-5APEX_matrixMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing		spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Stx17syntaxin ­174833418L03Rik, 6330411F21Rik, 9030425C21Rik, AW048351, Q9D0I4, gene:67727-6APEX_IMS, coexpressionMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Organelle contact sites;
Mitochondrial dynamics and surveillance > Autophagy		testis
Primpolprimase ­and ­polymerase ­(DNA-directed)BC065112, Ccdc111, Q6P1E7, gene:408022-6literature,mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Dna2DNA ­replication ­helicase/nuclease ­2Dn, Dna2l, E130315B21Rik, Q6ZQJ5, gene:327762-6literature, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Metabolism > Metals and cofactors > Fe-S-containing proteins		none
Adcy10adenylate ­cyclase ­104930431D04Rik, 4931412F17, Sa, Sacy, s, sAC, Q8C0T9, gene:271639-6literature,mito protein domainMembraneSignaling > cAMP-PKA signalingnone
Prss35protease, ­serine ­356030424L22Rik, P3D9, Q8C0F9, gene:244954-6GFP, mito protein domainunknownProtein import, sorting and homeostasis > Protein homeostasisnone
Mief2mitochondrial ­elongation ­factor ­2AI482195, Gm11, Smc, Smcr7, Q5NCS9, gene:237781-6literature,mito protein domainMOMMitochondrial dynamics and surveillance > Fissionnone
Nsun3NOL1/NOP2/Sun ­domain ­family ­member ­36720484A09Rik, AU022521, Q8CCT7, gene:106338-6APEX_matrix, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pabpc5poly(A) ­binding ­protein, ­cytoplasmic ­5C820015E17, Q8C7D3, gene:93728-6literature, mito protein domainMatrixnonenone
Styxl1serine/threonine/tyrosine ­interacting-like ­11700011C14Rik, Dusp, Dusp24, Mkstyx, Q9DAR2, gene:76571-6literature,mito protein domainMatrixMitochondrial dynamics and surveillance > Apoptosisnone
Sphk2sphingosine ­kinase ­2C76851, Sk2, Spk2, Q9JIA7, gene:56632-6literature,mito protein domainMIMMetabolism > Lipid metabolism > Phospholipid metabolism;
Mitochondrial dynamics and surveillance > Apoptosis		none
Prknparkin ­RBR ­E3 ­ubiquitin ­protein ­ligaseP, Pa, Park2, Q9WVS6, gene:50873-6manual, mito protein domainMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy		none
Nsun2NOL1/NOP2/Sun ­domain ­family ­member ­2D13Wsu123e, Mi, Misu, Q1HFZ0, gene:28114-6literature,mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pick1protein ­interacting ­with ­C ­kinase ­1Prk, Prkcabp, Q8C1W2, gene:18693-6literature, mito protein domainunknownnonenone
Dmpkdystrophia ­myotonica-protein ­kinaseDM, DMK, Dm15, MDPK, MT-PK, P54265, gene:13400-6literature, mito protein domainMOMnonenone
Casp9caspase ­9AI115399, APAF-3, AW493809, CASP-9, Casp, Caspase-9, ICE-, ICE-LAP6, Mch6, Q8C3Q9, gene:12371-6literature,mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Apoptosis		none
Casp8caspase ­8CASP-8, Casp, FLI, FLICE, MAC, MACH, Mch5, O89110, gene:12370-6literature, mito protein domainMOMProtein import, sorting and homeostasis > Protein homeostasis;
Mitochondrial dynamics and surveillance > Apoptosis		none
Casp3caspase ­3A830040C14Rik, AC-, AC-3, CASP-3, CC3, CPP, CPP-32, CPP32, Casp, Caspase-3, Lice, SCA-1, Ya, Yama, mld, mldy, P70677, gene:12367-6literature,mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Apoptosis		none
Bcl2l2BCL2-like ­2AW048834, Bcl-, Bcl-w, Gtrg, Gtrgal2, Gtro, Gtrosa41, bcl, bclw, c98, P70345, gene:12050-6literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Bcl2l10Bcl2-like ­10AA420380, AU023065, B, Boo, C85687, D, Diva, Q9Z0F3, gene:12049-6manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Bcl2a1dB ­cell ­leukemia/lymphoma ­2 ­related ­protein ­A1dA1-, A1-d, O55179, gene:12047-6manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Bcl2B ­cell ­leukemia/lymphoma ­2AW986256, Bcl-, Bcl-2, C430015F12Rik, D630044D05Rik, D830018M01Rik, P10417, gene:12043-6literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
BadBCL2-associated ­agonist ­of ­cell ­deathAI325008, Bbc2, Q61337, gene:12015-6literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Pde2aphosphodiesterase ­2A, ­cGMP-stimulatedCGS-PDE, cGSPDE, Q3TYK5, gene:207728-6literature,targetP signalMIMSignaling > cAMP-PKA signalingcerebrum, cerebellum, brainstem, largeintestine
Spata20spermatogenesis ­associated ­20Tis, Tisp78, Q80YT5, gene:217116-6APEX_matrixMatrixnonetestis
Plgrktplasminogen ­receptor, ­C-terminal ­lysine ­transmembrane ­protein1110007H22Rik, 5033414D02Rik, AI852040, Plg-, Plg-R(KT), Plg-RKT, Q9D3P8, gene:67759-7GFPMembranenonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pld6phospholipase ­D ­family, ­member ­64933433K01Rik, Gm10, Zuc, mZuc, mit, mitoPLD, Q5SWZ9, gene:194908-8literatureMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Mitochondrial dynamics and surveillance > Fusion		none
Bbc3BCL2 ­binding ­component ­3PU, PUMA, PUMA/JFY1, Q99ML1, gene:170770-8manualMOMMitochondrial dynamics and surveillance > Apoptosisnone
CstadCSA-conditional, ­T ­cell ­activation-dependent ­protein9530039B02Rik, Q9D245, gene:78617-8literatureMOMSignaling > Immune responsenone
1700066M21RikRIKEN ­cDNA ­1700066M21 ­geneAI428479, Q9D9H8, gene:73467-8APEX_matrixMatrixnonenone
Spire1spire ­type ­actin ­nucleation ­factor ­16030430B19Rik, AI415299, AU022898, AW550622, Sp, Spir-1, D3YTL8, gene:68166-8literatureMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Organelle contact sites		none
Armcx1armadillo ­repeat ­containing, ­X-linked ­13010033I09Rik, ALEX1, Q9CX83, gene:78248-10literatureMOMMitochondrial dynamics and surveillance > Traffickingnone
Armcx2armadillo ­repeat ­containing, ­X-linked ­23230401N03Rik, AI043003, ALEX2, Q6A058, gene:67416-10literatureMembranenonenone
Armcx6armadillo ­repeat ­containing, ­X-linked ­6AW060994, Q8K3A6, gene:278097-11literatureMembranenonenone
Nat8lN-acetyltransferase ­8-like1110038O08Rik, Sh, Shati, Q3UGX3, gene:269642-11literatureMembraneMetabolism > Amino acid metabolism > Glutamate metabolismnone
SphkapSPHK1 ­interactor, ­AKAP ­domain ­containing4930544G21Rik, A930009L15Rik, AI852220, S, SKIP, mKIAA1678, Q6NSW3, gene:77629-11manualMIMSignaling > cAMP-PKA signalingnone
Mettl4methyltransferase ­like ­42410198H06Rik, A730091E08Rik, AV296509, HsT66, HsT661, Q3U034, gene:76781-11literatureMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA modificationsnone
Armcx3armadillo ­repeat ­containing, ­X-linked ­31200004E24Rik, AI450003, ALEX3, Q8BHS6, gene:71703-11literatureMOMMitochondrial dynamics and surveillance > Traffickingnone
Snap29synaptosomal-associated ­protein ­291300018G05Rik, AI891940, AU020222, BB131856, Gs32, Q9ERB0, gene:67474-11APEX_IMSIMSMitochondrial dynamics and surveillance > Autophagynone
Polbpolymerase ­(DNA ­directed), ­betaA430088C08Rik, Q8K409, gene:18970-11literatureMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Htd2hydroxyacyl-thioester ­dehydratase ­type ­2, gene:109729085 literatureMatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisnone
Pigbos1Pigb ­opposite ­strand ­12310009A05Rik, 5031420N21Rik, A0A5F8MPY0, gene:66364 literatureMOMMitochondrial dynamics and surveillance > Organelle contact sitesnone